Urinary propionylcarnitine analysis for monitoring carnitine supplementation in inherited disorders of propionate metabolism.
Department of Pediatrics, Nagoya City University Medical School, Japan.
N
N
Sugiyama
I
I
Matsuda
Y
Y
Wada
K
K
Narisawa
M
M
Kobayashi
K
K
Kidouchi
D000293:Adolescent; D002331:Carnitine / Q000008:administration & dosage / Q000031:analogs & derivatives* / Q000627:therapeutic use* / Q000652:urine; D002648:Child; D002675:Child, Preschool; D005260:Female; D006801:Humans; D007223:Infant; D008297:Male; D008661:Metabolism, Inborn Errors / Q000188:drug therapy* / Q000652:urine; D011422:Propionates / Q000378:metabolism*
D011422:Propionates; C003223:propionylcarnitine; C029658:propionic acid; D002331:Carnitine