[Sustained monomorphic ventricular tachycardia in myotonic dystrophy].
Myotonic dystrophy is an hereditary multisystemic disease, characterized by slowly progressive myotonic atrophy of skeletic muscles. The heart is frequently affected with occurrence of arrhythmias and His-Purkinje system dysfunction and, less frequently, myocardial dysfunction. The surface ECG is the most sensible indicator of heart disease, and the most common electrophysiological finding is the prolongation of the H-V interval. Patients usually have few cardiovascular symptoms, but when present, the most frequent are: syncope, arrhythmias, atrioventricular block, congestive heart failure and sudden death. We present two patients with sustained monomorphic ventricular tachycardia as initial presentation of cardiac disease.
Kuzmicic Calderón
B
B
Unidad de Arritmias, Hospital Clínic i Provincial, Barcelona.
Valls Arara
V
V
Brugada Terradellas
J
J
Navarro Michel
X
X
Navarro López
F
F
D004562:Electrocardiography; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D009223:Myotonic Dystrophy / Q000150:complications*; D017180:Tachycardia, Ventricular / Q000209:etiology* / Q000503:physiopathology
Taquicardia ventricular monomórfica sostenida en la distrofia miotónica.