[Right ventricular arrhythmogenic dysplasia. The role of heart transplantation in its management].
Arrhythmogenic right ventricular dysplasia is a rare disease that usually presents with ventricular arrhythmias and sometimes with heart failure. Rarely symptoms become severe and refractory to conventional therapy. We present the case of a 36-year-old man with this disease who had sustained ventricular arrhythmias and severe right heart failure. Because these symptoms were poorly controlled with medical therapy, cardiac transplantation was finally chosen as definitive treatment. The patient had a favorable course and now leads near-normal life.
Servicio de Cardiología, Clínica Puerta de Hierro, Madrid.
J F
JF
Oteo
L
L
Alonso-Pulpón
M A
MA
Cavero
J A
JA
Rubio
C
C
Maicas
S
S
Serrano-Fiz
H Y
HY
Hotait
M
M
Artaza
I S
IS
Vegazo
J
J
Ugarte
D000328:Adult; D001145:Arrhythmias, Cardiac / Q000150:complications / Q000601:surgery*; D006333:Heart Failure / Q000150:complications / Q000601:surgery*; D016027:Heart Transplantation; D006352:Heart Ventricles / Q000002:abnormalities* / Q000601:surgery*; D006801:Humans; D008297:Male
Displasia arritmogénica ventricular derecha. El papel del trasplante cardíaco en su manejo.