[Caroli's syndrome: a variable entity].
We present the case of a 56 year old woman with Caroli's disease associated to congenital liver fibrosis, renal nephrocalcinosis and cutaneous vasculitis of the legs. Clinical signs of portal hypertension were treated by a shunt technique. After an asymptomatic period, the patient suffers now from crisis of angiocholitis.
Servicio de Aparato Digestivo, Ciudad Sanitaria Virgen de las Nieves, Granada.
M D
MD
Espinosa Aguilar
M
M
López de Hierro Ruiz
L M
LM
Pinel Julián
A
A
González Galilea
J F
JF
Suárez Crespo
M
M
Ruiz-Cabello
R
R
Martín-Vivaldi
D016767:Caroli Disease / Q000150:complications / Q000175:diagnosis / Q000628:therapy; D005260:Female; D006801:Humans; D008875:Middle Aged
Síndrome de Caroli: una entidad variable.