Unilateral pulmonary agenesis, esophageal atresia, and distal tracheoesophageal fistula.
A small-for-gestational-age, premature infant with the combination of unilateral pulmonary agenesis, esophageal atresia, and distal tracheoesophageal fistula was treated successfully by early gastrostomy and delayed fistula division with esophagoesophagostomy. Only 2 other successfully treated cases have been reported previously. Both were full-term infants treated with early division of the tracheoesophageal fistula and esophagoesophagostomy. Gestational age, size, and associated medical problems need to be considered when planning operative therapy for these babies.
Steadland
K M
KM
Department of Surgery, University of Florida College of Medicine, Gainesville 32610-0286.
Langham
M R
MR
Greene
M A
MA
Bagwell
C E
CE
Kays
D W
DW
Talbert
J L
JL
D000015:Abnormalities, Multiple; D004200:Diseases in Twins; D004933:Esophageal Atresia / Q000235:genetics / Q000601:surgery*; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D007234:Infant, Premature; D007236:Infant, Small for Gestational Age; D008168:Lung / Q000002:abnormalities*; D014138:Tracheoesophageal Fistula / Q000151:congenital* / Q000235:genetics / Q000601:surgery