title: Congenital aural cholesteatoma: results of surgery in 60 cases.
abstract: From 1978 to 1993, 59 patients (60 ears) with congenital middle ear cholesteatoma were treated at the House Ear Clinic. The median patient age at presentation was 5 years, and the period of postoperative follow-up was 4.8 years. An intact canal wall was maintained in 58 of 60 cases and a closed middle ear space in all cases. In 12 operations, lateral graft tympanoplasty eradicated the cholesteatoma in one stage; 32 patients required a second-stage surgery to rule out recurrence, and the remaining 16 cases required three or more operations to eradicate disease and reconstruct the hearing mechanism. Thirty-five (63%) of 56 patients had a postoperative air-conduction threshold pure-tone average (PTA) within 10 dB of the best bone-conduction PTA; 91% were within 20 dB. Average speech reception threshold improved from 32 dB hearing level (HL) preoperatively to 20 dB HL postoperatively.
authors.affiliation: University of California Irvine, Orange.
authors.forename: K J
authors.initials: KJ
authors.lastname: Doyle
authors.forename: W M
authors.initials: WM
authors.lastname: Luxford
mesh_terms: D002648:Child; D018424:Cholesteatoma, Middle Ear / Q000151:congenital* / Q000503:physiopathology / Q000601:surgery*; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D008416:Mastoid / Q000601:surgery; D012086:Reoperation; D012189:Retrospective Studies; D013069:Speech Reception Threshold Test; D013997:Time Factors; D016896:Treatment Outcome; D014433:Tympanoplasty