title: Anaesthesia and mucopolysaccharidoses. A review of airway problems in children.
abstract: The airway problems encountered during anaesthesia in all children with mucopolysaccharidoses presenting for a surgical procedure from 1988 to September 1991 are reviewed. Thirty-four patients underwent 89 anaesthetics for 110 procedures. The results reveal a high incidence of airway problems. The overall incidence of difficult intubation was 25% and failed intubation 8%. In those children with Hurler's syndrome, the difficult intubation incidence was 54% and failed intubation incidence 23%. Other potential anaesthetic problems such as cardiac anomalies and obstructive sleep apnoea are also reviewed.
authors.affiliation: Royal Manchester Children's Hospital, Pendlebury.
authors.forename: R W
authors.initials: RW
authors.lastname: Walker
authors.forename: M
authors.initials: M
authors.lastname: Darowski
authors.forename: P
authors.initials: P
authors.lastname: Morris
authors.forename: J E
authors.initials: JE
authors.lastname: Wraith
mesh_terms: D000293:Adolescent; D017677:Age Distribution; D000402:Airway Obstruction / Q000209:etiology*; D000758:Anesthesia / Q000379:methods*; D002648:Child; D002675:Child, Preschool; D006330:Heart Defects, Congenital / Q000209:etiology; D006801:Humans; D007223:Infant; D007442:Intubation, Intratracheal / Q000379:methods; D009083:Mucopolysaccharidoses / Q000150:complications / Q000601:surgery*; D012189:Retrospective Studies; D012891:Sleep Apnea Syndromes / Q000209:etiology; D017211:Treatment Failure