Idiopathic infantile arterial calcification: a surviving patient with renal artery stenosis.
Idiopathic infantile arterial calcification (IIAC) is a rare hereditary, fatal disease. Death occurs usually within the first 28 months of life. IIAC is characterized by calcifications along the internal elastic membrane and proliferation of the intimal layer of muscular arteries. Specific therapy consists of administration of diphosphonates, but its effectiveness has been a matter of controversy. We report a case treated with diphosphonates which has had an unusual outcome.
Thiaville
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A
Department of Radiology, Hôpital Universitaire des Enfants Reine Fabiola, Brussels, Belgium.
Smets
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Clercx
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A
Perlmutter
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N
D001158:Arteries; D002114:Calcinosis / Q000150:complications* / Q000000981:diagnostic imaging / Q000188:drug therapy; D004164:Diphosphonates / Q000627:therapeutic use; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D011859:Radiography; D012078:Renal Artery Obstruction / Q000150:complications* / Q000000981:diagnostic imaging; D014652:Vascular Diseases / Q000150:complications* / Q000000981:diagnostic imaging / Q000188:drug therapy
D004164:Diphosphonates