title: Infracardiac total anomalous pulmonary venous connection in tetralogy of Fallot with decreased pulmonary flow and masked pulmonary venous obstruction: report of one case.
abstract: We describe an 8-month-old male infant, who received a rerouting procedure for infracardiac total anomalous pulmonary venous connection and a 4-mm Gore-Tex central shunt for tetralogy of Fallot with pulmonary atresia. The masking effect of the pulmonary outflow in tetralogy of Fallot on the pulmonary venous obstruction in infracardiac total anomalous pulmonary venous connection is discussed. Preoperative recognition of this rare association is warranted, as palliative surgery alone may be disastrous. In addition, juxtaductal pulmonary artery coarctation in tetralogy of Fallot with pulmonary atresia may play a role in camouflaging the pulmonary venous obstruction in this case. Unmasking pulmonary venous obstruction by oral prostaglandin and augmenting pulmonary blood flow by a Gore-Tex shunt, pari passu, did harm this patient.
authors.affiliation: Department of Pediatrics, Changhua Christian Hospital, Taiwan, R.O.C.
authors.forename: M L
authors.initials: ML
authors.lastname: Lee
authors.forename: M H
authors.initials: MH
authors.lastname: Wu
authors.forename: H C
authors.initials: HC
authors.lastname: Lue
mesh_terms: D001166:Arteriovenous Shunt, Surgical; D002932:Cineangiography; D003330:Coronary Vessel Anomalies / Q000150:complications* / Q000601:surgery; D004374:Ductus Arteriosus, Patent / Q000150:complications* / Q000601:surgery; D004452:Echocardiography; D017809:Fatal Outcome; D006801:Humans; D007223:Infant; D008297:Male; D011667:Pulmonary Veins / Q000002:abnormalities*; D011668:Pulmonary Veno-Occlusive Disease / Q000175:diagnosis / Q000209:etiology*; D013771:Tetralogy of Fallot / Q000150:complications* / Q000601:surgery