[Type IA glycogenosis with acute pancreatitis].
Type IA glycogenosis, or von Gierke disease, is the most common among the glycogenoses with enlarged liver. Acute pancreatitis is a rare manifestation of type IA glycogenosis and has been attributed to elevated serum fat levels. We report a case of type IA glycogenosis with acute pancreatitis. The radiologists should be familiar with the computed tomography findings in this rare complications of type IA glycogenosis.
Herman
T E
TE
Mallinckrodt Institute of Radiology, St. Louis Children's Hospital, Department of Radiology, Missouri 63110.
D000208:Acute Disease; D002648:Child; D005953:Glycogen Storage Disease Type I / Q000175:diagnosis* / Q000000981:diagnostic imaging; D006801:Humans; D008297:Male; D010195:Pancreatitis / Q000209:etiology*; D014057:Tomography, X-Ray Computed
Glycogénose type IA avec pancréatite aiguë.