[Arterial occlusion in cutis marmorata teleangiectatica congenita].
Cutis marmorata teleangiectatica congenita (CMTC) is a rare congenital vascular disorder of the venous system. In 50% of cases there are associated anomalies of other organ systems. Clinical improvement of the cutaneous manifestations is noted in most cases and usually occurs during the first year of life. We present a patient with CMTC with a band-like pattern following the L3 dermatome. At the age of 13 years, the skin manifestations worsened, with ulcerations and intermittent claudication. Angiographic imaging revealed stenosis of the deep femoral artery, and the circumflex femoral artery and the first perforating arteries were not visualized. To our knowledge, this is the first reported case of CMTC with anomalies of the large arteries.
Skaria
A M
AM
Klinik und Poliklinik für Dermatologie und Venerologie, Hôpital Cantonal Universitaire de Genève.
Hauser
C
C
D000293:Adolescent; D000792:Angiography; D001157:Arterial Occlusive Diseases / Q000175:diagnosis* / Q000188:drug therapy; D001165:Arteriovenous Malformations / Q000175:diagnosis* / Q000188:drug therapy; D001241:Aspirin / Q000008:administration & dosage; D004305:Dose-Response Relationship, Drug; D005260:Female; D006801:Humans; D007383:Intermittent Claudication / Q000175:diagnosis / Q000188:drug therapy; D007511:Ischemia / Q000175:diagnosis / Q000188:drug therapy; D007866:Leg / Q000098:blood supply; D012867:Skin / Q000098:blood supply*; D013684:Telangiectasis / Q000151:congenital* / Q000175:diagnosis / Q000188:drug therapy
D001241:Aspirin
Arterieller Verschluss bei Cutis marmorata teleangiectatica congenita.