title: [Studies on sexual development, sexual behavior and ability to experience sex of young women with Ullrich-Turner syndrome].
abstract: In this investigation 25 female patients were included with the Turner syndrome (TS). From the 25 patients 6 had spontaneous menstruations, 19 had menstruations only after a hormonal stimulation. In a semi-structured interview the patients were questioned about their sexual activities, behavior and orgastic capacity. The findings were related to a matched normal female population. Moreover an analysis of personality traits by means of the Freiburger Persönlichkeitsinventar [FPI], the Giessen Test [GT], and a questionnaire on education styles of parents [EMBU] has been undertaken. The endocrine profile of the patients with induced menarche showed an elevated value of LH and FSH in serum, and a low level of estradiol. The sexual development of all patients was normal during the prepubertal phase. However the biological puberty was delayed by three years in the study patients, in relation to a normal population. Each of these women had a normal female identity and was heterosexual oriented. In concordance with the literature, patients who were substituted too late, showed defined deficits in their psychic well being, as well as in their social and psychosexual functioning. These deficits only were significant in relation to delayed menarche, but not to chronological age, gynecological age, karyotype, body height or parental education style. Therefore, an early and adequately dosed hormonal intervention and a consequently and regularly performed substitution therapy with sexual steroids has to be undertaken beside the well known intervention with growth hormone.
authors.affiliation: Universitäts-Kinderklinik Leipzig.
authors.forename: E
authors.initials: E
authors.lastname: Hettmer
authors.forename: W
authors.initials: W
authors.lastname: Hoepffner
authors.forename: E
authors.initials: E
authors.lastname: Keller
authors.forename: E
authors.initials: E
authors.lastname: Brähler
mesh_terms: D000293:Adolescent; D000328:Adult; D005260:Female; D005783:Gender Identity; D006801:Humans; D007989:Libido; D011606:Psychosexual Development; D012725:Sexual Behavior; D014424:Turner Syndrome / Q000523:psychology*
vernacular_title: Untersuchungen zur sexuellen Entwicklung, zum Sexualverhalten und zur sexuellen Erlebnisfähigkeit junger Frauen mit Ullrich-Turner-Syndrom (UTS).