[Lethal hydrops fetalis secondary to an umbilical cord hemangioma].
We report an umbilical cord hemangioma associated with an hydrops fetalis and detected by ultrasonography at 21 week's gestation. Because of the fetal distress, a caesarean section was performed at 28 weeks'. The infant died soon after birth despite resuscitation. The post-mortem examination showed an extensive accumulation of serous fluid in the fetal tissues and the body cavities, and major pulmonary hypoplasia. The umbilical cord contained a grossly fusiform tumor which fulfilled the pathological criteria of an umbilical cord hemangioma. Umbilical cord hemangiomas are very unusual tumors and are rarely associated with a fetal hydrops. This tumor is a cause of increased maternal serum and amniotic fluid alpha-foetoprotein levels. Although it is usually isolated, it is imperative to search for associated malformations or angiomas that may clinically manifest later.
Carles
D
D
Département d'Anatomie Pathologique, Groupe Hospitalier Pellegrin, C.H.U. de Bordeaux.
Maugey-Laulom
B
B
Roux
D
D
Jimenez
M
M
Saudubray
F
F
Alberti
E M
EM
D017809:Fatal Outcome; D005260:Female; D018324:Hemangioma, Capillary / Q000150:complications*; D006801:Humans; D015160:Hydrops Fetalis / Q000209:etiology* / Q000473:pathology; D008297:Male; D010920:Placenta / Q000473:pathology; D011247:Pregnancy; D014470:Umbilical Cord
Anasarque foeto-placentaire létale secondaire à un hémangiome du cordon ombilical.