Successful repair of the right atrial isomerism, double outlet right ventricle, common atrioventricular canal, pulmonary stenosis, and total anomalous pulmonary venous connection.
A 6-year-old boy was successfully operated on for double outlet ventricle, common atrioventricular canal with severe valvular regurgitation, right atrial isomerism, L-loop ventricles, total anomalous pulmonary venous connection, and pulmonary stenosis with hypoplastic left pulmonary artery. The interventricular rerouting from the left ventricle to the ascending aorta was performed with a spiral patch, the interatrial switching was performed by a Mustard patch, the common atrioventricular orifice was partitioned and valve repair was performed, and an 18-mm valved conduit was inserted between the right ventricle and the pulmonary artery. Although the patient had a small residual ventricular septal defect and pulmonary stenosis, the patient is alive and well.
Okita
Y
Y
Department of Cardiovascular Surgery, Tenri Hospital, Nara, Japan.
Miki
S
S
Ueda
Y
Y
Tahata
T
T
Sakai
T
T
Matsuyama
K
K
Matsumura
M
M
D000015:Abnormalities, Multiple / Q000601:surgery*; D006348:Cardiac Surgical Procedures / Q000379:methods; D002648:Child; D004310:Double Outlet Right Ventricle / Q000601:surgery; D006325:Heart Atria / Q000002:abnormalities; D006330:Heart Defects, Congenital / Q000601:surgery*; D006352:Heart Ventricles / Q000002:abnormalities; D006801:Humans; D008297:Male; D011666:Pulmonary Valve Stenosis / Q000601:surgery; D011667:Pulmonary Veins / Q000002:abnormalities