[Congenital cutaneous aplasia. Apropos of 3 new cases located in the vertex].
Aplasia cutis congenita is a rare malformation characterized by absence of skin. We report three new cases, localized on the vertex with one appearing as a familial form and requiring an emergent surgical repair with a favorable outcome. After a review of the literature, the authors discuss nosological aspects and etiological problems which are still not resolved. It seems that vascular differentiation of the skin could play an associated role. As regards of treatment, different attitudes are possible and are exposed, with a preference for surgery which is the method of choice for the authors.
Guinard
D
D
Service de Chirurgie Plastique, Hôpital A. Michallon, CHRU, Grenoble.
Lebeau
J
J
Moutet
F
F
Raphael
B
B
D000015:Abnormalities, Multiple; D000505:Alopecia / Q000151:congenital; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D012535:Scalp / Q000002:abnormalities* / Q000601:surgery; D012868:Skin Abnormalities; D013518:Surgery, Plastic
L'aplasie cutanée congénitale. A propos de trois nouveaux cas localisés au vertex.