[Aorto-left ventricular tunnel with origin in the left sinus of Valsalva: a rare cause of congenital aortic insufficiency].
Aortico-left-ventricular tunnel is a rare congenital cardiac lesion that often results in severe aortic insufficiency in infancy. Normally, the defect appears immediately above the right coronary sinus of Valsalva and consists of a tunnel-like connection between the aortic root and the left ventricle. The differential diagnosis to coronary artery fistulae and ruptured aneurysms of the sinus of Valsalva is often difficult. We describe a patient with an aortico-left-ventricular tunnel originating from the left aortic sinus. Similar findings have been described in only three case reports. Additionally, in our case there was a stenosis in the midportion of the tunnel which was connected to an intraseptal aneurysm communicating with the left ventricular chamber via a "septal" defect. The infant underwent successful surgical correction of this malformation at 1 year and 5 months of age.
Ries
M
M
Kardiologische Abteilung, Universität Erlangen-Nürnberg.
Singer
H
H
Hofbeck
M
M
Buheitel
G
G
von der Emde
J
J
D000790:Angiocardiography; D001022:Aortic Valve Insufficiency / Q000151:congenital* / Q000503:physiopathology / Q000601:surgery; D006328:Cardiac Catheterization; D003330:Coronary Vessel Anomalies / Q000175:diagnosis* / Q000503:physiopathology / Q000601:surgery; D003937:Diagnosis, Differential; D004452:Echocardiography; D005500:Follow-Up Studies; D006439:Hemodynamics / Q000502:physiology; D006801:Humans; D007223:Infant; D008297:Male; D012850:Sinus of Valsalva / Q000002:abnormalities* / Q000503:physiopathology / Q000601:surgery
Aorto-linksventrikulärer Tunnel mit Ursprung im linken Sinus Valsalvae: Seltene Ursache einer kongenitalen Aorteninsuffizienz.