[A case of ventricular septal defect and patent ductus arteriosus associated with absent right pulmonary artery, scimitar syndrome and severe pulmonary hypertension].
A 8 month-old female was diagnosed with ventricular septal defect and patent ductus arteriosus associated with absent right pulmonary artery and scimitar syndrome. Cardiac catheterization revealed severe pulmonary hypertension as follows; 72 mmHg of mean pulmonary artery pressure, 0.56 Qp/Qs and 1.73 Pp/Ps. Temporary closure of the ductus reduced the mean pulmonary artery pressure from 72 to 40 mmHg. PDA was ligated and VSD was closed successfully. However, 4 months after initial operation she was readmitted due to infection of the hypoplastic right lung. Removal of the hypoplastic right lung was performed and postoperative course was uneventful.
First Department of Surgery, Osaka University Medical School, Suita, Japan.
T
T
Nishimura
Y
Y
Shimazaki
T
T
Ohashi
S
S
Kamada
T
T
Sano
H
H
Matsuda
D004374:Ductus Arteriosus, Patent / Q000150:complications / Q000601:surgery*; D005260:Female; D006345:Heart Septal Defects, Ventricular / Q000150:complications / Q000601:surgery*; D006801:Humans; D006976:Hypertension, Pulmonary / Q000150:complications*; D007223:Infant; D011651:Pulmonary Artery / Q000002:abnormalities*; D012587:Scimitar Syndrome / Q000150:complications*