title: [Kasabach-Merritt syndrome].
abstract: Kasabach Merritt syndrome, first recognized in 1940, is characterized by haemangiomatosis, thrombocytopenia and intravascular coagulation. It is most often seen in children, rarely in adults. The mortality rate is 20-30%. Treatment is by removing the haemangiomatosis and correcting the consumptive coagulopathy. The purpose of this paper is to present a patient with Kasabach Merritt syndrome with haemangiomatosis in the spleen and the liver. A review of the relevant literature is given.
authors.affiliation: Medicinsk-haematologisk afdeling, Arhus Amtssygehus.
authors.forename: V
authors.initials: V
authors.lastname: Haahr
authors.forename: E
authors.initials: E
authors.lastname: Jacobsen
authors.forename: K
authors.initials: K
authors.lastname: Bendix
authors.forename: J L
authors.initials: JL
authors.lastname: Nielsen
authors.forename: N A
authors.initials: NA
authors.lastname: Peterslund
mesh_terms: D000328:Adult; D004211:Disseminated Intravascular Coagulation / Q000175:diagnosis / Q000628:therapy; D005260:Female; D006391:Hemangioma / Q000097:blood / Q000175:diagnosis / Q000628:therapy; D006801:Humans; D008113:Liver Neoplasms / Q000097:blood / Q000175:diagnosis / Q000628:therapy; D013160:Splenic Neoplasms / Q000097:blood / Q000175:diagnosis / Q000628:therapy; D013577:Syndrome; D013921:Thrombocytopenia / Q000175:diagnosis / Q000628:therapy
vernacular_title: Kasabach Merritt-syndrom.