Idiopathic long q-t syndrome: brief case report and discussion.
Idiopathic long q-t syndrome (LQTS) is an infrequently occurring familial disorder in which affected family members have an abnormally prolonged q-tc interval with syncope, ventricular arrythmias and sudden death. In this article, we present the case of a 54-year-old female admitted for syncope, who was on no medications except for insulin. Her electrocardiogram on admission had prolonged q-tc interval (0.50 ms.). She had repeated episodes of torsades de pointes during her hospitalization, which were later controlled by beta-blockers. Electrocardiograms of her mother and daughter showed asymptomatic prolonged q-tc interval. This syndrome has an autosomal dominant pattern of transmission and it was first described by Romano and Ward in a patient with normal hearing. Our case is unusual because this condition presented so late in life.
Noble
W E
WE
Department of Medicine, Robert C. Byrd Health Sciences Center of WVU, Morgantown.
Chaudhuri
P
P
Qazi
M A
MA
D000465:Algorithms; D004562:Electrocardiography; D005260:Female; D006801:Humans; D008133:Long QT Syndrome / Q000175:diagnosis / Q000188:drug therapy / Q000235:genetics; D008875:Middle Aged; D011433:Propranolol / Q000627:therapeutic use; D013575:Syncope / Q000209:etiology; D016171:Torsades de Pointes / Q000188:drug therapy / Q000209:etiology
D011433:Propranolol