title: Primary intraventricular cardiac tumors in children: contemporary diagnostic and management options.
abstract: We reviewed the intraventricular cardiac tumors presenting at our institution between 1985-1991, studying the presentation, modes of investigation, and evidence of hemodynamic compromise. Thirteen patients presented with intraventricular tumors during the study period. Two of the tumors were rhabdomyosarcomas, one was a myxoma, and 10 were rhabdomyomas. All patients were evaluated with two-dimensional and pulsed Doppler echocardiography and B-color imaging was undertaken in three patients. Four patients presented for elective scans to complement investigations for tuberous sclerosis, seven patients had cardiac symptoms, and two patients presented prenatally. Obstruction to intracardiac flow was present in five patients. Two patients had the tumor excised and one had an open biopsy of the tumor. One patient had an transvascular biopsy at cardiac catheter. Early detection of cardiac tumors is increasing, particularly rhabdomyomas. With fetal echocardiography, more patients should come to attention prenatally. B-color may be useful addition in assessing cardiac tumors, aiding detection and definition of intramural lesions.
authors.affiliation: Adolph Basser Institute of Cardiology, Royal Alexandra Hospital for Children, Camperdown, Sydney, Australia.
authors.forename: J
authors.initials: J
authors.lastname: Hwa
authors.forename: C
authors.initials: C
authors.lastname: Ward
authors.forename: G
authors.initials: G
authors.lastname: Nunn
authors.forename: S
authors.initials: S
authors.lastname: Cooper
authors.forename: K C
authors.initials: KC
authors.lastname: Lau
authors.forename: G
authors.initials: G
authors.lastname: Sholler
mesh_terms: D002648:Child; D002675:Child, Preschool; D018618:Echocardiography, Doppler, Color; D005260:Female; D005315:Fetal Diseases / Q000000981:diagnostic imaging; D006338:Heart Neoplasms / Q000000981:diagnostic imaging* / Q000601:surgery; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D009232:Myxoma / Q000000981:diagnostic imaging / Q000601:surgery; D011247:Pregnancy; D012207:Rhabdomyoma / Q000000981:diagnostic imaging*; D012208:Rhabdomyosarcoma / Q000000981:diagnostic imaging / Q000601:surgery; D016216:Ultrasonography, Prenatal