[Intestinal pseudo-obstruction secondary to systemic neuropathies and myopathies].
The term intestinal pseudo-obstruction, is applied to a group of clinical disorders in which there are obstructive symptoms, in the absence of a mechanical agent, secondary to a disorder of intestinal motility. In this report, we show manometric studies done in four patients, with acute intestinal pseudo-obstructions, secondary to von Recklinghausen's neurofibromatosis (VRNF), in two patients, and in one patient with Duchenne's muscular dystrophy (DMD) and in another with Werdnig-Hoffmann's disease (WHD). We studied 24 hours antroduodenal motility, specially during phase 3 of the migratory motor complex (CMM), which showed a neuropathic disorder in one case of von Recklinghausen's disease and a myopathic disorder in patients with Duchenne's muscular dystrophy and Werdnig-Hoffmann's disease. We analysed results and conclusions and specially the kinetic action of erythromycin.
García Aroca
J
J
Servicio de Cirugía Pediátrica, Hospital Niño Jesús, Madrid.
Sanz
N
N
Alonso
J L
JL
de Mingo
L
L
Rollán
V
V
D000293:Adolescent; D002648:Child; D005260:Female; D013271:Gastric Dilatation / Q000175:diagnosis / Q000209:etiology; D006801:Humans; D007077:Ileal Diseases / Q000175:diagnosis / Q000209:etiology*; D007418:Intestinal Pseudo-Obstruction / Q000175:diagnosis / Q000209:etiology*; D008297:Male; D009136:Muscular Dystrophies / Q000150:complications* / Q000175:diagnosis; D009456:Neurofibromatosis 1 / Q000150:complications* / Q000175:diagnosis; D014897:Spinal Muscular Atrophies of Childhood / Q000150:complications* / Q000175:diagnosis
Pseudoobstrucción intestinal secundaria a neuropatías y miopatías sistémicas.