[Pulmonary fibro-xanthogranuloma associated with renal amyloidosis in a 5-year-old child].
BACKGROUND
Pulmonary fibroxanthogranuloma is a benign tumor that is rarely seen in children. Its association with renal amyloidosis is not known.


METHODS
A 5 year-old boy developed arthritis in his wrists and his hands became clubbed. X-rays showed a round mass in the left inferior pulmonary lobe. Sonography revealed that this mass contained fluid. Nephrotic syndrome appeared one month later. The pulmonary mass was then excised; histology indicated a fibroxanthogranuloma with no malignancy. Renal biopsy showed infiltration with amyloid substance. The nephrotic syndrome was improved one month after surgery, but contact with the child was then lost.


CONCLUSIONS
The association of this tumor with apparently secondary amyloidosis may indicate that fibroxanthogranuloma is a pseudotumor of inflammatory origin.
Mikou
N
N
Service de Pédiatrie II, Hôpital d'Enfants de Rabat, Maroc.
Balafrej
A
A
D000686:Amyloidosis / Q000209:etiology*; D002675:Child, Preschool; D006099:Granuloma / Q000150:complications*; D018219:Histiocytoma, Benign Fibrous / Q000150:complications*; D006801:Humans; D007674:Kidney Diseases / Q000209:etiology*; D008175:Lung Neoplasms / Q000150:complications*; D008297:Male; D010005:Osteoarthropathy, Secondary Hypertrophic / Q000209:etiology
Fibroxanthogranulome pulmonaire associé à une amylose rénale chez un enfant de 5 ans.