[Kasabach-Merritt syndrome].
Kasabach Merritt syndrome, first recognized in 1940, is characterized by haemangiomatosis, thrombocytopenia and intravascular coagulation. It is most often seen in children, rarely in adults. The mortality rate is 20-30%. Treatment is by removing the haemangiomatosis and correcting the consumptive coagulopathy. The purpose of this paper is to present a patient with Kasabach Merritt syndrome with haemangiomatosis in the spleen and the liver. A review of the relevant literature is given.
Haahr
V
V
Medicinsk-haematologisk afdeling, Arhus Amtssygehus.
Jacobsen
E
E
Bendix
K
K
Nielsen
J L
JL
Peterslund
N A
NA
D000328:Adult; D004211:Disseminated Intravascular Coagulation / Q000175:diagnosis / Q000628:therapy; D005260:Female; D006391:Hemangioma / Q000097:blood / Q000175:diagnosis / Q000628:therapy; D006801:Humans; D008113:Liver Neoplasms / Q000097:blood / Q000175:diagnosis / Q000628:therapy; D013160:Splenic Neoplasms / Q000097:blood / Q000175:diagnosis / Q000628:therapy; D013577:Syndrome; D013921:Thrombocytopenia / Q000175:diagnosis / Q000628:therapy
Kasabach Merritt-syndrom.