[Hypertrophic osteoarthropathy disclosing hepatic and pulmonary multifocal epithelioid hemangioendothelioma].
Epithelioid hemangioendothelioma is a rare, low-grade vascular malignancy reported for the first time in 1982 by Weiss and Enzinger. It involves one or, more rarely, several organs. We report a case involving the lungs and liver, in which the first manifestation was symptomatic hypertrophic osteoarthropathy. Findings four years after the diagnosis included very slow tumor spread, resolution of symptoms, and stabilization of radiological changes.
Service de Rhumatologie, CHU Bichat, Paris.
P
P
Zufferey
M
M
Goycochea
M
M
Grossin
P
P
M'Bappe
O
O
Meyer
M F
MF
Kahn
D000293:Adolescent; D018323:Hemangioendothelioma, Epithelioid / Q000150:complications* / Q000503:physiopathology; D006801:Humans; D008113:Liver Neoplasms / Q000150:complications* / Q000503:physiopathology; D008175:Lung Neoplasms / Q000150:complications* / Q000503:physiopathology; D008297:Male; D009378:Neoplasms, Multiple Primary / Q000150:complications* / Q000503:physiopathology; D010005:Osteoarthropathy, Secondary Hypertrophic / Q000209:etiology*; D013997:Time Factors
Ostéo-arthropathie hypertrophiante révélatrice d'un hémangio-endothéliome épithélioïde multifocal hépatique et pulmonaire.