[Erythrohemophagocytic lymphohistiocytosis. A clinical report of 3 cases].
Three infants suffering from hepatosplenomegaly, pancytopenia, hyperlipidemia, low fibrinogen levels and fever are reported. Two patients died during the first year of life, the third one received allogenic bone transplantation and survives. Clinical and haematological features are consistent with diagnosis of hemophagocytic lymphohistiocytosis.
Dipartimento di Pediatria, Ospedale A. Cardarelli, Napoli, Italia.
P
P
Catera
V
V
Tammaro
S
S
Coletta
G
G
Esposito
S
S
Capasso
F
F
Antonelli
D016026:Bone Marrow Transplantation; D005260:Female; D015616:Histiocytosis, Non-Langerhans-Cell / Q000175:diagnosis / Q000628:therapy; D006801:Humans; D007223:Infant
Linfoistiocitosi eritroematofagica. Contributo clinico di 3 casi.