[Primary ciliary dyskinesia. Electron microscopy study of ciliary ultrastructure].
A 75 year old patient with respiratory infections since childhood, bronchiectasis and situs inversus is presented. Fiberoptic bronchoscopy was performed obtaining samples of bronchial mucosa which allowed the observation of the existence of ultrastructural lesions such as ciliary fusion, changes in the form of the cilia, microtubular changes and changes of the dynein arms by electronic microscopic study. Diagnosis of Kartagener's syndrome was established. In the case presented moderate clinical involvement was present which allowed the survival of the patient despite his advanced age.
Royo
J A
JA
Servicio de Neumología, Hospital Clínico, Salamanca.
Barrueco
M
M
Ludeña
D
D
Gómez
F
F
González
J M
JM
Capurro
M
M
Riesco
J A
JA
D000368:Aged; D002923:Cilia / Q000648:ultrastructure; D006801:Humans; D007619:Kartagener Syndrome / Q000473:pathology*; D008297:Male; D008854:Microscopy, Electron
Discinesia ciliar primaria. Estudio por microscopia electrónica de la ultraestructura ciliar.