Medullary renal dysplasia mimicking renal tumor in the Beckwith-Wiedemann syndrome.
The known association of Wilms' tumor with the Beckwith-Wiedemann syndrome has prompted a surveillance regimen for children with this problem. Herein we report a case of medullary renal dysplasia that was a new onset by documented ultrasound. The association of medullary renal dysplasia with Beckwith-Wiedemann syndrome is discussed as well as the management of this problem.
Brock
J W
JW
Division of Pediatric Urology, Children's Hospital of Vanderbilt University Medical Center, Nashville, Tennessee.
Johnson
J
J
D001506:Beckwith-Wiedemann Syndrome / Q000150:complications / Q000175:diagnosis*; D000013:Congenital Abnormalities / Q000175:diagnosis; D003937:Diagnosis, Differential; D006801:Humans; D007231:Infant, Newborn; D007674:Kidney Diseases / Q000150:complications / Q000175:diagnosis*; D007679:Kidney Medulla / Q000002:abnormalities* / Q000000981:diagnostic imaging; D007680:Kidney Neoplasms / Q000175:diagnosis*; D008297:Male; D009447:Neuroblastoma / Q000175:diagnosis*; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography