title: [Report of a case of malignant atrophic papulosis or Degos disease].
abstract: The Authors report an exceptional case of Atrophic Malignant Papulosis (P.A.M.) or Degos disease, presenting as acute abdomen with ileal and multiple colic perforations. The disease is due to an occlusive, progressive, thrombotic vascular pathology affecting different parts of the body and may bring to death. Usually this rare disease presents with typical multiple papulous skin lesions, followed by a systemic involvement of the digestive, nervous, and visive tracts. Peritonitis and cerebral infarction are the most frequent causes of death.
authors.affiliation: Istituto di Semeiotica Chirurgica, Università degli Studi di Bari.
authors.forename: G
authors.initials: G
authors.lastname: De Leo
authors.forename: T
authors.initials: T
authors.lastname: Losacco
authors.forename: C
authors.initials: C
authors.lastname: Punzo
authors.forename: M
authors.initials: M
authors.lastname: Lavacca
authors.forename: M V
authors.initials: MV
authors.lastname: Pitzalis
authors.forename: C
authors.initials: C
authors.lastname: De Tommaso
authors.forename: A
authors.initials: A
authors.lastname: Posca
mesh_terms: D000006:Abdomen, Acute / Q000175:diagnosis; D000328:Adult; D001284:Atrophy; D003108:Colonic Diseases / Q000175:diagnosis; D005260:Female; D006801:Humans; D007077:Ileal Diseases / Q000175:diagnosis; D007416:Intestinal Perforation / Q000175:diagnosis; D017444:Skin Diseases, Papulosquamous / Q000175:diagnosis; D013577:Syndrome; D014657:Vasculitis / Q000175:diagnosis
vernacular_title: Su un caso di papulosi atrofica maligna (P.A.M.) o malattia di Degos.