Arterial fibrodysplasia causing occlusive vascular disease simulating primary vasculitis.
We report a case of arterial fibrodysplasia causing vascular disease with ulceronecrotic lesions in lower extremities. The arteriography showed a beaded pattern in both arteries and veins; laboratory test findings were within normal value ranges; the biopsy reported medial hyperplasia involving the arterial and venous walls. Arterial fibrodysplasia should be considered as a differential diagnosis in patients complaining of recurrent occlusive vascular episodes without systemic manifestations, normal laboratory test results, and radiological patterns suggestive of fibrodysplasia. This is the first report of medial hyperplasia in digital arteries and venous wall involvement.
Guzmán
R
R
Internal Medicine Department, Hospital San Juan de Dois, Universidad Nacional de Colombia Santafé de Bogotá.
Restrepo
J F
JF
Lizarazo
H
H
Peña
M
M
Méndez
O
O
Iglesias
A
A
D000328:Adult; D000671:Amputation, Surgical; D003937:Diagnosis, Differential; D005352:Fibromuscular Dysplasia / Q000175:diagnosis* / Q000601:surgery; D005385:Fingers / Q000098:blood supply; D016523:Foot Ulcer / Q000209:etiology; D006801:Humans; D007866:Leg / Q000098:blood supply / Q000601:surgery; D008297:Male; D009336:Necrosis; D014034:Toes / Q000098:blood supply / Q000473:pathology / Q000601:surgery; D014657:Vasculitis / Q000175:diagnosis*