title: [Anomalies of the genitalia and in sex differentiation].
abstract: Out of four biological sexes (male, female, bisexuality, asexuality) world legislation acknowledges only two. Therefore, hermaphrodites and eunuchs have either male or female documents. To determine human sexual anomaly, it is necessary to define genetic (chromosomal), gonadal (hormonal), phenotypic, psychological and legal sexes. True hermaphroditism must be distinguished from a false one: true hermaphrodites have both female and male gonads (or gonadal tissue), false hermaphrodites are unisexual, but their sex organs resemble those of the opposite sex. Five degrees of masculinization of the external genitalia in false female hermaphrodites are specified. In masculinization degree IV female sex organs look like genitalia of males suffering from perineoscrotal hypospadias with unaffected urogenital sinus and cryptorchidism. Feminization of male external genitalia comprises three anomalies: perineoscrotal hypospadias, unaffected urogenital sinus and cryptorchidism. Three cases are described: a girl with masculinization of the external sex organs of the 5th degree, a 7-year-old child with true hermaphroditism and gonadal tumor, a true hermaphrodite aged 22 surgically treated to correct the sex to be a male.
authors.forename: I M
authors.initials: IM
authors.lastname: Derevianko
authors.forename: T I
authors.initials: TI
authors.lastname: Derevianko
mesh_terms: D000328:Adult; D002648:Child; D003937:Diagnosis, Differential; D012734:Disorders of Sex Development / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D005260:Female; D005836:Genitalia, Female / Q000002:abnormalities* / Q000601:surgery; D005837:Genitalia, Male / Q000002:abnormalities* / Q000601:surgery; D006801:Humans; D008297:Male
vernacular_title: Anomalii polovykh organov i differentsiatsii pola.