title: Definitive cure of hyperammonemia by liver transplantation in urea cycle defects: report of three cases.
authors.affiliation: Hopital des Enfants Malades, Paris, France.
authors.forename: D
authors.initials: D
authors.lastname: Jan
authors.forename: F
authors.initials: F
authors.lastname: Poggi
authors.forename: P
authors.initials: P
authors.lastname: Jouvet
authors.forename: D
authors.initials: D
authors.lastname: Rabier
authors.forename: J
authors.initials: J
authors.lastname: Laurent
authors.forename: A
authors.initials: A
authors.lastname: Beringer
authors.forename: P
authors.initials: P
authors.lastname: Hubert
authors.forename: J M
authors.initials: JM
authors.lastname: Saudubray
authors.forename: Y
authors.initials: Y
authors.lastname: Revillon
mesh_terms: D000592:Amino Acid Metabolism, Inborn Errors / Q000378:metabolism / Q000601:surgery*; D000641:Ammonia / Q000097:blood*; D001124:Argininosuccinate Synthase / Q000172:deficiency; D002648:Child; D002956:Citrulline / Q000097:blood; D006801:Humans; D016031:Liver Transplantation; D020163:Ornithine Carbamoyltransferase Deficiency Disease; D014508:Urea / Q000378:metabolism*
chemical_list: D002956:Citrulline; D000641:Ammonia; D014508:Urea; D001124:Argininosuccinate Synthase