Type I aortic dissection in a patient with osteogenesis imperfecta.
The previously undescribed association between aortic dissection and osteogenesis imperfecta is reported in a 39-year-old man with known osteogenesis imperfecta, who presented with a type I aortic dissection. His ascending aorta was repaired using a Dacron tube graft under hypothermic circulatory arrest but the patient died 12 h later, following re-dissection around the left coronary ostium resulting in massive myocardial infarction of the left ventricle.
Ashraf
S S
SS
Department of Cardiothoracic Surgery, Manchester Royal Infirmary, UK.
Shaukat
N
N
Masood
M
M
Lyons
T J
TJ
Keenan
D J
DJ
D000328:Adult; D000784:Aortic Dissection / Q000150:complications* / Q000601:surgery; D001014:Aortic Aneurysm / Q000150:complications* / Q000601:surgery; D002315:Cardiopulmonary Bypass; D017809:Fatal Outcome; D006324:Heart Arrest, Induced; D006801:Humans; D008297:Male; D009203:Myocardial Infarction / Q000209:etiology; D010013:Osteogenesis Imperfecta / Q000150:complications*; D011093:Polyethylene Terephthalates; D012086:Reoperation; D017211:Treatment Failure
D011093:Polyethylene Terephthalates