Pulmonary hypertension associated with portal hypertension in a child with Williams syndrome--a case report.
A 14-year-old white female with Williams syndrome and portal hypertension presented in shock; at autopsy she was found to have grade II to VI vascular changes of pulmonary hypertension. This case demonstrates the association of portal hypertension and pulmonary hypertension in a pediatric patient.
Land
S D
SD
Department of Pathology, Medical College of Virginia, Richmond 23298.
Shah
M D
MD
Berman
W F
WF
D000015:Abnormalities, Multiple / Q000503:physiopathology; D000293:Adolescent; D005260:Female; D006801:Humans; D006975:Hypertension, Portal / Q000150:complications*; D006976:Hypertension, Pulmonary / Q000150:complications*; D013577:Syndrome