title: Hypocomplementemic urticarial vasculitis syndrome with severe systemic manifestations.
abstract: We describe two children with clinical and laboratory features of hypocomplementemic urticarial vasculitis syndrome. Both patients had severe, life-threatening manifestations: rapidly progressive glomerulonephritis (patient 1) and pulmonary hemorrhage (patient 2). We conclude that this syndrome may be a potentially severe multisystem disease.
authors.affiliation: Clinica Pediatrica, Università di Pavia, Italy.
authors.forename: A
authors.initials: A
authors.lastname: Martini
authors.forename: A
authors.initials: A
authors.lastname: Ravelli
authors.forename: S
authors.initials: S
authors.lastname: Albani
authors.forename: F
authors.initials: F
authors.lastname: De Benedetti
authors.forename: M
authors.initials: M
authors.lastname: Massa
authors.forename: J J
authors.initials: JJ
authors.lastname: Wisnieski
mesh_terms: D000293:Adolescent; D002648:Child; D003165:Complement System Proteins / Q000172:deficiency*; D005921:Glomerulonephritis / Q000209:etiology*; D006470:Hemorrhage / Q000209:etiology*; D006801:Humans; D008171:Lung Diseases / Q000209:etiology*; D008297:Male; D013577:Syndrome; D014581:Urticaria / Q000150:complications*; D014657:Vasculitis / Q000150:complications*
chemical_list: D003165:Complement System Proteins