title: [Pulmonary lymphangioleiomyomatosis].
abstract: The authors present a clinical case of Lymphangioleiomyomatosis of the lung. They analyse the clinical, radiological and functional features and comment on the evolution and therapeutic approach of this rare disorder. To the authors, lung involvement as well as therapeutic decision are important features that affect the prognosis.
authors.affiliation: Departamento de Pneumologia, Hospital de Pulido Valente, Lisboa.
authors.forename: A C
authors.initials: AC
authors.lastname: Santos
authors.forename: C
authors.initials: C
authors.lastname: Bárbara
authors.forename: B
authors.initials: B
authors.lastname: Mendes
authors.forename: M J
authors.initials: MJ
authors.lastname: Gomes
authors.forename: R
authors.initials: R
authors.lastname: Amaral-Marques
mesh_terms: D000328:Adult; D001706:Biopsy; D003131:Combined Modality Therapy; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D008168:Lung / Q000000981:diagnostic imaging; D008175:Lung Neoplasms / Q000473:pathology* / Q000628:therapy; D018192:Lymphangioleiomyomatosis / Q000473:pathology* / Q000628:therapy; D014057:Tomography, X-Ray Computed
vernacular_title: Linfangioleiomiomatose pulmonar.