Polysplenia syndrome: a case associated with transhepatic portal vein, short pancreas, and left inferior vena cava with hemiazygous continuation.
This paper presents a 57-year-old asymptomatic patient with the polysplenia syndrome with abdominal manifestations. In addition to multiple spleens, the abdominal findings included a left inferior vena cava with hemiazygous continuation, a striking portal anomaly with the portal vein following an "intraperitoneal-left transhepatic" route to reach the porta hepatis, and a congenitally short pancreas.
Sener
R N
RN
Department of Radiology, Ege University Hospital, Bornova, Izmir, Turkey.
Alper
H
H
D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging*; D001401:Azygos Vein / Q000002:abnormalities* / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D008875:Middle Aged; D010179:Pancreas / Q000002:abnormalities* / Q000000981:diagnostic imaging; D011169:Portal Vein / Q000002:abnormalities* / Q000000981:diagnostic imaging; D013154:Spleen / Q000002:abnormalities* / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed; D014682:Vena Cava, Inferior / Q000002:abnormalities* / Q000000981:diagnostic imaging