Idiopathic retroperitoneal fibrosis with systemic manifestations.
We describe a previously unreported association of idiopathic retroperitoneal fibrosis with mesenteric, pulmonary and perhaps periarticular fibrotic involvement, and panniculitis resembling Weber-Christian panniculitis. The onset of the disease was uncommon with arthritis. Then, several episodes of migratory panniculitis appeared; biopsy showed septal panniculitis without necrosis of adipose tissue. Considering the patient's anamnesis, it is tempting to speculate that these manifestations all originate from the same mechanism.
Bonnet
C
C
Department of Rheumatology, University of Limoges, France.
Arnaud
M
M
Bertin
P
P
Treves
R
R
Gotteron
R D
RD
D000328:Adult; D006801:Humans; D007596:Joints / Q000473:pathology; D008168:Lung / Q000473:pathology; D008279:Magnetic Resonance Imaging; D008297:Male; D008643:Mesentery / Q000473:pathology; D010201:Panniculitis, Nodular Nonsuppurative / Q000150:complications; D012185:Retroperitoneal Fibrosis / Q000150:complications / Q000473:pathology*; D012867:Skin / Q000473:pathology