Cerebral syrinx with Chiari I malformation.
A 13-year-old female presented with acute left gaze paralysis. MRI revealed hydrosyringomyelia (HSM) with syringobulbia in the left pons extending cephalad into the centrum semiovale. A suboccipital craniotomy was performed and the foramen of Magendie was imperforate. Ocular movements normalized in 2 months and postoperative MRI confirmed resolution of the cerebral syrinx and syringobulbia and diminished HSM. This case represents an extreme example of the altered spinal fluid dynamics with Chiari I malformation. Theories on HSM are reviewed.
Kanev
P M
PM
Department of Neurosurgery, Temple University School of Medicine, Philadelphia, Pa.
Getch
C C
CC
Jallo
J
J
Faerber
E N
EN
D000328:Adult; D001139:Arnold-Chiari Malformation / Q000150:complications* / Q000175:diagnosis; D001479:Basal Ganglia / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D001921:Brain / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D003399:Craniotomy; D004172:Diplopia / Q000209:etiology; D005260:Female; D005539:Foramen Magnum / Q000473:pathology / Q000601:surgery; D006801:Humans; D008279:Magnetic Resonance Imaging; D011859:Radiography; D013595:Syringomyelia / Q000150:complications* / Q000601:surgery; D016896:Treatment Outcome