title: [Holter and sudden death: value in a case of arrhythmogenic right ventricular dysplasia].
abstract: The authors report the first case of arrhythmogenic right ventricular dysplasia presenting with a sudden death due to primary ventricular fibrillation (ventricular fibrillation not preceded by ventricular tachycardia) recorded by the Holter method. The patient was a 56 year old man whose only complaint was near syncopal case is the fact that it is the first documented case of ventricular fibrillation revealing arrhythmogenic right ventricular dysplasia, the diagnosis of which was made at autopsy. In addition, the Holter recording showed the factors which triggered the arrhythmia: the "trigger" of 4 monomorphic ventricular extrasystoles during the minute preceding the ventricular fibrillation; the arrhythmogenic substrate giving rise to late ventricular potentials and, finally, the analysis of the R-R intervals suggesting a role of the sympathetic and parasympathetic nervous systems. Holter recordings could help identify subjects at high risk of severe ventricular arrhythmias.
authors.affiliation: Centre médico-chirurgical, Villiers-Saint-Denis.
authors.forename: P
authors.initials: P
authors.lastname: Aouate
authors.forename: F
authors.initials: F
authors.lastname: Fontaliran
authors.forename: G
authors.initials: G
authors.lastname: Fontaine
authors.forename: R
authors.initials: R
authors.lastname: Frank
authors.forename: A
authors.initials: A
authors.lastname: Benassar
authors.forename: G
authors.initials: G
authors.lastname: Lascault
authors.forename: J
authors.initials: J
authors.lastname: Tonet
authors.forename: C
authors.initials: C
authors.lastname: Humbert
authors.forename: C
authors.initials: C
authors.lastname: Guérot
mesh_terms: D000273:Adipose Tissue / Q000473:pathology; D001145:Arrhythmias, Cardiac / Q000150:complications / Q000175:diagnosis; D009202:Cardiomyopathies / Q000150:complications* / Q000473:pathology; D016757:Death, Sudden, Cardiac / Q000209:etiology* / Q000473:pathology; D015716:Electrocardiography, Ambulatory; D006352:Heart Ventricles / Q000473:pathology*; D006801:Humans; D008297:Male; D008875:Middle Aged; D012307:Risk Factors; D014693:Ventricular Fibrillation / Q000150:complications* / Q000175:diagnosis; D016278:Ventricular Function, Right
vernacular_title: Holter et mort subite: intérêt dans un cas de dysplasie ventriculaire droite arythmogène.