[Sneddon's syndrome: an unusual cause of cerebral infarct at a relatively young age].
Sneddon's syndrome was diagnosed in a man of 56, and two women aged 48 and 22 years. It is a rare disease characterised by the combination of skin lesions (livedo racemosa) and cerebral infarctions at a relatively early age. Apart from the clinical presentation, the diagnosis can sometimes be confirmed by a typical microscopical image of a biopsy taken from a region adjacent to the livedo (endothelitis, perivascular lymphocyte infiltration and hypertrophy of the artery wall). The cause of the syndrome is unknown and a specific therapy is lacking. Early recognition of Sneddon's syndrome may protect patients against unnecessary ancillary investigations.
Canta
L R
LR
Afd. Neurologie, St. Elisabeth Ziekenhuis, Tilburg.
Koedijk
F H
FH
Tijssen
C C
CC
D000328:Adult; D002544:Cerebral Infarction / Q000000981:diagnostic imaging / Q000209:etiology*; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D012008:Recurrence; D017445:Skin Diseases, Vascular / Q000150:complications* / Q000175:diagnosis; D013577:Syndrome; D014057:Tomography, X-Ray Computed
Het syndroom van Sneddon: een zeldzame oorzaak van een herseninfarct op relatief jonge leeftijd.