title: Cerebral syrinx with Chiari I malformation.
abstract: A 13-year-old female presented with acute left gaze paralysis. MRI revealed hydrosyringomyelia (HSM) with syringobulbia in the left pons extending cephalad into the centrum semiovale. A suboccipital craniotomy was performed and the foramen of Magendie was imperforate. Ocular movements normalized in 2 months and postoperative MRI confirmed resolution of the cerebral syrinx and syringobulbia and diminished HSM. This case represents an extreme example of the altered spinal fluid dynamics with Chiari I malformation. Theories on HSM are reviewed.
authors.affiliation: Department of Neurosurgery, Temple University School of Medicine, Philadelphia, Pa.
authors.forename: P M
authors.initials: PM
authors.lastname: Kanev
authors.forename: C C
authors.initials: CC
authors.lastname: Getch
authors.forename: J
authors.initials: J
authors.lastname: Jallo
authors.forename: E N
authors.initials: EN
authors.lastname: Faerber
mesh_terms: D000328:Adult; D001139:Arnold-Chiari Malformation / Q000150:complications* / Q000175:diagnosis; D001479:Basal Ganglia / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D001921:Brain / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery; D003399:Craniotomy; D004172:Diplopia / Q000209:etiology; D005260:Female; D005539:Foramen Magnum / Q000473:pathology / Q000601:surgery; D006801:Humans; D008279:Magnetic Resonance Imaging; D011859:Radiography; D013595:Syringomyelia / Q000150:complications* / Q000601:surgery; D016896:Treatment Outcome