title: [Maffucci syndrome and ovarian tumor].
abstract: Maffucci's syndrome was first described in 1881 and results of a mesodermic dysembryoplasia, congenital but not hereditary. Pathogenic hypothesis are multiple. This syndrome is characterized by the occurrence of multiple haemangiomas in the soft tissue, and multiple enchondromas of the bones. The association of ovary tumor is however exceptional. Four cases are reported in the literature; we report the fifth case.
authors.affiliation: Service de gynécologie-obstétrique et de reproduction humaine, hôpital Aziza Othmana, Tunis, Tunisie.
authors.forename: L
authors.initials: L
authors.lastname: Hamdoun
authors.forename: C
authors.initials: C
authors.lastname: Mouelhi
authors.forename: F
authors.initials: F
authors.lastname: Zhioua
authors.forename: A
authors.initials: A
authors.lastname: Jedoui
authors.forename: S
authors.initials: S
authors.lastname: Meriah
authors.forename: S
authors.initials: S
authors.lastname: Houet
mesh_terms: D000293:Adolescent; D004687:Enchondromatosis / Q000150:complications*; D005260:Female; D006226:Hand Deformities / Q000209:etiology; D006801:Humans; D009364:Neoplasm Recurrence, Local; D010051:Ovarian Neoplasms / Q000150:complications* / Q000473:pathology; D013798:Thecoma / Q000150:complications* / Q000473:pathology
vernacular_title: Syndrome de Maffucci et tumeur ovarienne.