Sole pulmonary involvement by Langerhans' cell histiocytosis in a child.
The case of a boy aged 4 yrs and 7 months, with isolated pulmonary involvement by Langerhans' cell histiocytosis is reported. The presentation of the disease was a sudden pneumothorax, with no previous signs of respiratory disease. The case was confirmed by S-100 and MT1 antibody staining, and was treated with pulse steroids and several pleural drainages, until the boy died after a large bilateral pneumothorax.
Chatkin
J M
JM
Hospital São Lucas, School of Medicine, Pontificia Universidade Catolica do Rio Grande do Sul, Porto Alegre, Brazil.
Bastos
J C
JC
Stein
R T
RT
Gaiger
A M
AM
D002675:Child, Preschool; D006646:Histiocytosis, Langerhans-Cell / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D008168:Lung / Q000000981:diagnostic imaging / Q000473:pathology; D008171:Lung Diseases / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D008297:Male; D011030:Pneumothorax / Q000209:etiology; D011859:Radiography