title: [Malignant rhabdoid tumor of the central nervous system. Apropos of a case with immunohistochemical and ultrastructural studies, and review of the literature].
abstract: The authors report a new case of cerebral malignant rhabdoid tumour in an eight year old girl. The diagnosis was confirmed on immunohistochemical and ultrastructural examinations showing cytoplasmic perinuclear inclusions composed of whorled filaments of vimentin. Base on a review of six cases reported in the literature, they analyse the clinical, histological, immunohistochemical and ultrastructural features of this exceptional central nervous system neoplasm. Different histogenetic hypotheses are discussed.
authors.affiliation: Service Central d'Anatomie et de Cytologie Pathologiques, Hôpital la Rabta, Tunis, Tunisie.
authors.forename: N
authors.initials: N
authors.lastname: Kchir
authors.forename: R
authors.initials: R
authors.lastname: Limam
authors.forename: S
authors.initials: S
authors.lastname: Haouet
authors.forename: S
authors.initials: S
authors.lastname: Chatti
authors.forename: A
authors.initials: A
authors.lastname: Chadly
authors.forename: M
authors.initials: M
authors.lastname: Khaldi
authors.forename: S
authors.initials: S
authors.lastname: Boubaker
authors.forename: M
authors.initials: M
authors.lastname: Zitouna
mesh_terms: D001932:Brain Neoplasms / Q000175:diagnosis / Q000473:pathology* / Q000648:ultrastructure; D002648:Child; D005260:Female; D006801:Humans; D007150:Immunohistochemistry; D012207:Rhabdomyoma / Q000175:diagnosis / Q000473:pathology* / Q000648:ultrastructure; D014057:Tomography, X-Ray Computed
vernacular_title: Tumeur rhabdoïde maligne du système nerveux central. A propos d'une observation avec études immunohistochimique et ultrastructurale, et revue de la littérature.