title: [Aortic hypoplasia in a case of single ventricle with normally related vessels].
abstract: In cases with double inlet left ventricle when there exists a hypoplasia of one of the great arteries, the affected vessel arises from the accessory right ventricular chamber. This is due in general to the presence of a restrictive bulbo-ventricular foramen that results in hypoplasic vessel. The case we present in this paper has unusual anatomic morphology: the hypoplasic vessel (the aorta) arises from the main ventricular chamber. We analyse the electrocardiographic findings useful for the differential diagnosis from cases of isolated aortic coarctation of hypoplasia. We review also the intraventricular anatomic malformations that may cause the presence of a hypoplasic vessel. Even if, our patient died in the neonatal period, the adequate surgical procedure for this case is reviewed.
authors.affiliation: Departamento de Cardiología Pediátrica, Hospital Infantil, México, D.F.
authors.forename: A
authors.initials: A
authors.lastname: Arévalo Salas
authors.forename: M J
authors.initials: MJ
authors.lastname: Maitre Azcárate
authors.forename: M
authors.initials: M
authors.lastname: Quero Jiménez
mesh_terms: D000015:Abnormalities, Multiple / Q000175:diagnosis; D001011:Aorta / Q000002:abnormalities*; D005260:Female; D006330:Heart Defects, Congenital / Q000175:diagnosis; D006352:Heart Ventricles / Q000002:abnormalities*; D006801:Humans; D007231:Infant, Newborn
vernacular_title: Hipoplasia aórtica en un caso de ventrículo único con vasos normalmente relacionados.