[Congenital stenosis of the anus and rectum (Problems of nosology and pathogenesis)].
The work deals with the differential analysis of two forms of congenital rectal stenosis--"membranous" which is consequent upon incomplete obliteration of the anal membrane and "tubular" with involvement of the rectum along its length. It is pointed out that in most cases tubular rectal stenosis is a component of the complex of anomalies of the caudal region described for the first time by G. Currarino (1981) and called the ASP-triad. From analysis of 12 cases of the ASP syndrome a new scheme of the pathogenesis of the complex of anomalies constituting the syndrome is suggested. The authors identified a component of the syndrome which was not described earlier, namely, specific dysplasia of the pelvic floor and the external sphincter muscles of the anus, which provided the basis for naming the complex the PFASP syndrome (PF--Pelvic Floor Dysplasia). Problems of surgical correction of the PFASP complex of anomalies are discussed. A pathogenetically substantiated analysis of postoperative complications is made.
Pankevich
T L
TL
Lëniushkin
A I
AI
Alekseevskikh
Iu G
IuG
D001004:Anus Diseases / Q000145:classification / Q000151:congenital / Q000175:diagnosis / Q000601:surgery; D002648:Child; D002675:Child, Preschool; D003251:Constriction, Pathologic; D005260:Female; D006801:Humans; D007223:Infant; D017773:Pelvic Floor / Q000002:abnormalities* / Q000601:surgery; D012002:Rectal Diseases / Q000145:classification / Q000151:congenital* / Q000175:diagnosis / Q000601:surgery; D013577:Syndrome
Vrozhdënnyĭ stenoz zadneprokhodnogo kanala i priamoĭ kishki (voprosy nozologii i patogeneza).