title: [Obstetrical management in maternal tuberous sclerosis (Pringle-Bourneville syndrome)--a case report].
abstract: The rupture of visceral hamartomas in tuberous sclerosis (Pringle-Bourneville) is more likely in pregnancy because of the increased blood volume and can be followed by lifethreatening retroperitoneal hemorrhage. To avoid complications during delivery the vacuum extraction in epidural anesthesia is recommended. Preconceptional genetic counseling in this autosomal dominant disorder is obligatory.
authors.affiliation: Geburtschilflich-gynäkologische Abteilung, Hanusch-Krankenhaus, Wien.
authors.forename: M
authors.initials: M
authors.lastname: Klein
authors.forename: M
authors.initials: M
authors.lastname: Matal
authors.forename: C
authors.initials: C
authors.lastname: Wagner
authors.forename: A
authors.initials: A
authors.lastname: Beck
mesh_terms: D000328:Adult; D018207:Angiomyolipoma / Q000175:diagnosis / Q000601:surgery*; D005260:Female; D005350:Fibroma / Q000175:diagnosis / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D007680:Kidney Neoplasms / Q000175:diagnosis / Q000601:surgery*; D008297:Male; D016609:Neoplasms, Second Primary / Q000175:diagnosis / Q000601:surgery; D011247:Pregnancy; D011252:Pregnancy Complications, Neoplastic / Q000175:diagnosis / Q000601:surgery*; D012878:Skin Neoplasms / Q000175:diagnosis / Q000601:surgery; D014402:Tuberous Sclerosis / Q000175:diagnosis / Q000601:surgery*
vernacular_title: Zum geburtshilflichen Management bei mütterlicher tuberöser Sklerose (Pringle-Bourneville-Syndrom)--ein Fallbericht.