title: [Proteus syndrome].
abstract: We report the case of a 4-year old boy presenting with a polymalformative syndrome made of cutaneous and subcutaneous lesions associated with visceral and skeletal lesions. The cutaneous lesions consisted of 3 verrucous hamartomas, one haemangioma and one lymphangioma. The subcutaneous lesions were melting of panniculus adiposus, plantar tumefaction and diffuse lipomatosis of the peritoneal and retroperitoneal cavities. The skeletal lesions were uneven lower limbs and dorsal scoliosis. Atrophy of the intestinal villi was also found. The diagnosis of Proteus syndrome was made.
authors.affiliation: Service de Dermatologie, CHU Rangueil, Toulouse.
authors.forename: N
authors.initials: N
authors.lastname: Hachich
authors.forename: E
authors.initials: E
authors.lastname: Lopez
authors.forename: C
authors.initials: C
authors.lastname: Baunin
authors.forename: J P
authors.initials: JP
authors.lastname: Olives
authors.forename: I
authors.initials: I
authors.lastname: Armelin
authors.forename: J L
authors.initials: JL
authors.lastname: Bonafé
mesh_terms: D002675:Child, Preschool; D006801:Humans; D007410:Intestinal Diseases / Q000150:complications; D008297:Male; D016715:Proteus Syndrome
vernacular_title: Syndrome Protée.