A case of primary intestinal lymphangiectasia.
A 26-year-old male patient who had an 8 years history of recurrent peripheral edema with diarrhea and hypoproteinemia was evaluated. Endoscopic jejunal and ileal biopsy revealed markedly dilated mucosal lymph vessels with no evidence of inflammation. 99mTc-labeled human serum albumin (HSA) scintigraphy showed significant activity accumulating in the gastrointestinal tract to represent 99mTc-HSA leakage into the bowel lumen. A diagnosis of protein losing enteropathy and intestinal lymphangiectasia could be made. After treatment with a high protein and fat restricted diet, his symptoms subsided and the serum protein level was normalized.
Won
K C
KC
Department of Internal Medicine, College of Medicine, Yeungnam University, Taegu, Korea.
Jang
B I
BI
Kim
T N
TN
Lee
H W
HW
Chung
M K
MK
Lee
H W
HW
D000328:Adult; D001706:Biopsy; D016099:Endoscopy, Gastrointestinal; D006801:Humans; D007421:Intestine, Small / Q000473:pathology; D008201:Lymphangiectasis, Intestinal / Q000175:diagnosis* / Q000000981:diagnostic imaging; D008297:Male; D011877:Radionuclide Imaging; D013668:Technetium Tc 99m Aggregated Albumin
D013668:Technetium Tc 99m Aggregated Albumin