Scimitar sign with normal pulmonary venous drainage and systemic arterial supply. Scimitar syndrome or bronchopulmonary sequestration?
The classic definition of the scimitar syndrome is a triad of hypoplasia of the right lung with anomalous venous drainage and a systemic arterial supply of a variable degree. We report a case in which a scimitar-shaped anomalous vein was observed on the plain chest radiograph, but subsequently a pulmonary angiogram showed that it drained normally into the left atrium.
Cukier
A
A
Instituto do Coracão, Faculty of Medicine, University of São Paulo, Brazil.
Kavakama
J
J
Teixeira
L R
LR
Terra-Filho
M
M
Vargas
F S
FS
D000328:Adult; D001012:Aorta, Abdominal / Q000002:abnormalities; D001158:Arteries / Q000002:abnormalities; D001998:Bronchopulmonary Sequestration / Q000000981:diagnostic imaging*; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D008168:Lung / Q000002:abnormalities* / Q000098:blood supply; D011667:Pulmonary Veins / Q000000981:diagnostic imaging*; D011859:Radiography; D012587:Scimitar Syndrome / Q000000981:diagnostic imaging*