[Type IV Ehlers-Danlos syndrome disclosed by acute obstructive renal insufficiency].
A 64 year-old man was admitted for congestive heart failure induced by an acute renal failure due to obstruction. Retroperitoneal periaortic-aneurysmal fibrosis was the etiology of the obstruction. Type IV Ehlers-Danlos syndrome was diagnosed based upon clinical and histological cutaneous signs.
Roger
D
D
Service de Néphrologie, CHU Dupuytren, Limoges.
Peyronnet
P
P
Bedane
C
C
Rolle
F
F
Bonnetblanc
J M
JM
Leroux-Robert
C
C
D058186:Acute Kidney Injury / Q000209:etiology*; D017544:Aortic Aneurysm, Abdominal / Q000175:diagnosis / Q000209:etiology*; D001027:Aortography; D004535:Ehlers-Danlos Syndrome / Q000150:complications* / Q000473:pathology; D006801:Humans; D008297:Male; D008875:Middle Aged; D012185:Retroperitoneal Fibrosis / Q000209:etiology*; D012867:Skin / Q000473:pathology
Un syndrome d'Ehlers-Danlos de type IV révélé par une insuffisance rénale aiguë obstructive.