title: Dental management of a child with Huntington's disease: case report.
abstract: Huntington's Disease is a chronic, progressive, hereditary disorder of unknown etiology. Onset occurs between 35 and 42 years of age and is characterized by chorea, behavioral changes, dementia, and irregular gait. Dyslalia is a common feature due to the severe darting movements of the tongue and head. Huntington's Disease is rarely diagnosed in children (less than 1% of all cases are documented in children under 10 years of age). This is a case report of an 11 year 5 month old white male, diagnosed at age 5, who was brought to the University of Minnesota Hospital Dental Clinic for an oral examination. The findings are presented, and the management of patients with Huntington's Disease is discussed.
authors.affiliation: The Children's Hospital, Denver, CO.
authors.forename: M A
authors.initials: MA
authors.lastname: da Fonseca
authors.forename: P O
authors.initials: PO
authors.lastname: Walker
mesh_terms: D002648:Child; D003730:Dental Care for Persons with Disabilities; D006801:Humans; D006816:Huntington Disease; D008297:Male; D009910:Oral Hygiene