title: Compromise of the spinal canal in Proteus syndrome.
abstract: We report on 2 children with spinal stenosis and neurologic sequelae. They illustrate the 2 ways in which spinal compromise may develop in Proteus syndrome--vertebral anomalies or tumor infiltration. In one patient, spinal stenosis resulted from an angular kyphoscoliosis. In the other, cord compression resulted from infiltration of a paraspinal, intrathoracic angiolipoma.
authors.affiliation: Department of Pediatrics, Rigshospitalet, Copenhagen, Denmark.
authors.forename: F
authors.initials: F
authors.lastname: Skovby
authors.forename: J M
authors.initials: JM
authors.lastname: Graham
authors.forename: S
authors.initials: S
authors.lastname: Sonne-Holm
authors.forename: M M
authors.initials: MM
authors.lastname: Cohen
mesh_terms: D018206:Angiolipoma / Q000150:complications / Q000473:pathology; D002648:Child; D006801:Humans; D007738:Kyphosis / Q000150:complications / Q000000981:diagnostic imaging / Q000473:pathology; D008297:Male; D016715:Proteus Syndrome / Q000150:complications* / Q000473:pathology; D011859:Radiography; D012600:Scoliosis / Q000150:complications; D013117:Spinal Cord Compression / Q000209:etiology; D013125:Spinal Neoplasms / Q000150:complications / Q000473:pathology; D013130:Spinal Stenosis / Q000000981:diagnostic imaging / Q000209:etiology*; D013131:Spine / Q000002:abnormalities