[Congenital cystic bile duct dilatation. Presentation of clinical symptoms, diagnostic possibilities and therapy based on 6 cases].
METHODS
Congenital cystic dilatation of the bile ducts represents an uncommon anomaly of the biliary system. We report on 6 patients suffering from cystic biliary duct dilatations which were treated in our hospital between 1980 and 1992. Clinical signs included upper abdominal pain, white or clay-colored stool, icterus and/or palpable tumor. According to the classification of Todani, 4 children had type Ia cysts, 1 child a type Va cyst and 1 child a type Ia cyst with extrahepatic biliary atresia.


RESULTS
Among the diagnostic methods sonography is preeminent and permitted demonstration of intra- and extrahepatic biliary duct dilatations in all of our patients. In 2 patients small cystic dilatations could be distinguished from hepatic vessels by colour-coded Doppler sonography.


CONCLUSIONS
The treatment of choice is the resection of the dilated extrahepatic biliary ducts followed by hepaticojejunostomy using the Roux-en-Y-technique.
Ries
M
M
Klinik mit Poliklinik für Kinder und Jugendliche, Universität Erlangen-Nürnberg.
Deeg
K H
KH
Hümmer
H P
HP
Behrens
R
R
D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging / Q000601:surgery; D000713:Anastomosis, Roux-en-Y; D002648:Child; D002675:Child, Preschool; D015529:Choledochal Cyst / Q000000981:diagnostic imaging* / Q000601:surgery; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D007582:Jejunostomy; D008111:Liver Function Tests; D008297:Male; D011183:Postoperative Complications / Q000209:etiology / Q000601:surgery; D012086:Reoperation; D013577:Syndrome; D014463:Ultrasonography
Angeborene zystische Gallengangerweiterungen. Darstellung der klinischen Symptomatik, der diagnostischen Möglichkeiten und der Therapie anhand von 6 Erkrankungsfällen.