title: [CT study of 17 cases of congenital cochlear abnormality. Embryologic and anatomo-functional relationship].
abstract: In this review of cochlear malformations, 17 cases were studied by CT scan (high resolution-target program) including 10 males and 7 females. The anomaly was bilateral in 12 cases and unilateral in 7 (the latter included 2 Mondini type aplasias and one Michel). The cochlear malformation (whose most frequent expression was the cochlear hypoplasia with 1 or 1 1/2 spires-65% of the cases) was associated to semicircular canals and/or vestibular aqueduct anomaly in 82% of the patients; it was exclusively of the anterior labyrinth in 18% of the cases. A middle ear malformation coexisted in 29%: in 3 cases with malleoincudal dysmorphy only and with tympanic aplasia in 2 others. These cochlear anomalies with CT expression were discussed considering the embryology, in view of a possible gestational dating, moreover relating to the hipocusia type: perceptive or combined.
authors.affiliation: Departamento de TAC do Hospital CUF, Lisboa.
authors.forename: J C
authors.initials: JC
authors.lastname: Maurício
authors.forename: L
authors.initials: L
authors.lastname: Biscoito
authors.forename: G
authors.initials: G
authors.lastname: Branco
mesh_terms: D000015:Abnormalities, Multiple / Q000000981:diagnostic imaging / Q000453:epidemiology; D000293:Adolescent; D000328:Adult; D002648:Child; D003051:Cochlea / Q000002:abnormalities* / Q000000981:diagnostic imaging* / Q000503:physiopathology; D007758:Ear, Inner / Q000002:abnormalities / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D008297:Male; D014057:Tomography, X-Ray Computed
vernacular_title: Estudo por tc de 17 casos de anomalia congénita coclear. Tentativa de relação embriológica e anátomo-funcional.