title: [Surgical treatment of the patients with pulmonary atresia, ventricular septal defect associated with major aorto-pulmonary collateral arteries--a report of two cases].
abstract: Two patients undergoing corrective operation for pulmonary atresia with ventricular septal defect associated with major aortopulmonary collateral arteries (MAPCAs) were reported. Both patients underwent staged surgical repair, first stage: unifocalization, and second stage: Rastelli type operation. Case 1 was a 13-year-old female who had a confluent central pulmonary artery and 1 MAPCA, unifocalized at 10 years of age. After the corrective operation, the ratio between peak right ventricular and peak left ventricular pressure (pRV/LV) was 0.5 and she followed a satisfactory post-operative course. Case 2 was a 11-year-old female who had a severe hypoplastic central pulmonary artery (3 mm in diameter) and 3 MAPCAs, and she underwent unifocalization twice. After the corrective operation, pRV/LV was 0.65 and her postoperative course was also satisfactory.
authors.affiliation: Department of Cardiovascular Surgery, Hiroshima City Hospital, Japan.
authors.forename: K
authors.initials: K
authors.lastname: Sangawa
authors.forename: O
authors.initials: O
authors.lastname: Oba
authors.forename: K
authors.initials: K
authors.lastname: Nakanishi
authors.forename: M
authors.initials: M
authors.lastname: Okada
authors.forename: H
authors.initials: H
authors.lastname: Yoshida
authors.forename: A
authors.initials: A
authors.lastname: Shiote
mesh_terms: D000293:Adolescent; D001011:Aorta; D001807:Blood Vessel Prosthesis / Q000379:methods*; D002648:Child; D003097:Collateral Circulation; D005260:Female; D006345:Heart Septal Defects, Ventricular / Q000601:surgery*; D006801:Humans; D011651:Pulmonary Artery / Q000601:surgery; D011652:Pulmonary Circulation; D011664:Pulmonary Valve / Q000002:abnormalities* / Q000601:surgery; D013771:Tetralogy of Fallot / Q000150:complications / Q000503:physiopathology / Q000601:surgery*