title: Intra-abdominal desmoplastic small round cell tumour.
abstract: Intra-abdominal desmoplastic small round cell tumour is a rare tumour which has only recently been described. It demonstrates epithelial, mesenchymal and neural features and has an aggressive clinical course. We report a case of a 15 year old male with this tumour who, after debulking surgery and chemotherapy, relapsed with disease 1 month later. After further debulking surgery, extensive chemotherapy and bone marrow transplantation he relapsed with disease 5 months later and died. Total survival was 20 months.
authors.affiliation: Gribbles Pathology, Adelaide, Australia.
authors.forename: J R
authors.initials: JR
authors.lastname: Miliauskas
authors.forename: R L
authors.initials: RL
authors.lastname: Abbott
authors.forename: R
authors.initials: R
authors.lastname: Sarre
mesh_terms: D000008:Abdominal Neoplasms / Q000473:pathology*; D000293:Adolescent; D017809:Fatal Outcome; D006801:Humans; D008297:Male; D009364:Neoplasm Recurrence, Local