Hearing loss in infants with craniofacial anomalies.
Results of auditory brainstem response (ABR) evaluation of 145 infants, ages 6 months and younger with craniofacial anomalies (CFA), were examined to determined predicted degree and nature of hearing loss. Approximately 50% of infants demonstrated at least mild bilateral hearing loss. Presence and degree of hearing loss varied by CFA. All infants with bilateral aural atresia exhibited at least a moderate bilateral hearing loss; less than 20% of infants with isolated external ear anomalies (ear tags, isolated microtia) exhibited any degree of hearing loss. In 92% of infants with hearing loss, results of ABR were consistent with primarily conductive dysfunction. Implications for early identification and audiologic management of infants with CFA and hearing loss are discussed.
Hayes
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Audiology, Speech Pathology, and Learning Service, Children's Hospital, Denver, CO 80218.
D000161:Acoustic Stimulation; D002971:Cleft Lip / Q000503:physiopathology; D002972:Cleft Palate / Q000503:physiopathology; D004431:Ear, External / Q000002:abnormalities; D016057:Evoked Potentials, Auditory, Brain Stem / Q000502:physiology; D005147:Facial Bones / Q000002:abnormalities*; D005260:Female; D006312:Hearing Loss, Bilateral / Q000503:physiopathology*; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008297:Male; D011930:Reaction Time / Q000502:physiology; D012886:Skull / Q000002:abnormalities*