title: Incontinentia pigmenti (Bloch-Sulzberger syndrome) manifesting as painful periungual and subungual tumours.
abstract: A 25-year-old lady presented with painful periungual tumours which were associated with lytic changes of underlying terminal phalanges. She had been previously treated as a case of chronic paronychia but the problem recurred. She was subsequently diagnosed as a case of Incontinentia pigmenti which is a rare genodermatosis with mixed ectodermal and mesodermal polydysplasias, onchychodystrophy being a very rare manifestation. She was treated by excision of painful finger lesions, but there is no specific treatment for the underlying condition.
authors.affiliation: Department of Plastic Surgery, Frenchay Hospital, Bristol, UK.
authors.forename: A
authors.initials: A
authors.lastname: Adeniran
authors.forename: P L
authors.initials: PL
authors.lastname: Townsend
authors.forename: R D
authors.initials: RD
authors.lastname: Peachey
mesh_terms: D000328:Adult; D005260:Female; D006801:Humans; D007184:Incontinentia Pigmenti / Q000150:complications*; D007636:Keratoacanthoma / Q000209:etiology* / Q000601:surgery; D009262:Nails / Q000601:surgery*; D012871:Skin Diseases / Q000209:etiology* / Q000601:surgery