Postoperative metabolic decompensation in maple syrup urine disease is completely prevented by insulin.
Biggemann
B
B
Universitäts-Kinderklinik, Heinrich-Heine Universität, Düsseldorf, Germany.
Zass
R
R
Wendel
U
U
D000293:Adolescent; D005260:Female; D006801:Humans; D007328:Insulin / Q000627:therapeutic use*; D008375:Maple Syrup Urine Disease / Q000150:complications* / Q000178:diet therapy; D010289:Parenteral Nutrition, Total; D011183:Postoperative Complications / Q000378:metabolism / Q000517:prevention & control*; D012600:Scoliosis / Q000209:etiology / Q000601:surgery; D013167:Spondylitis, Ankylosing / Q000209:etiology / Q000601:surgery
D007328:Insulin