Severe unconjugated hyperbilirubinaemia with infradiaphragmatic total anomalous pulmonary venous connection.
An 8 day old girl with infradiaphragmatic total anomalous pulmonary venous connection presented with severe unconjugated hyperbilirubinaemia; exchange transfusion resulted in haemodynamic deterioration. Hyperbilirubinaemia is a rare complication of this condition, however exchange transfusion should be avoided. The diagnosis can be made on the neonatal unit by ultrasound demonstration of dilated hepatic portal veins.
Burch
M
M
Department of Cardiology, Hospital for Sick Children, London.
Dyamenahalli
U
U
Sullivan
I D
ID
D005078:Exchange Transfusion, Whole Blood; D005260:Female; D006801:Humans; D006932:Hyperbilirubinemia / Q000209:etiology* / Q000473:pathology; D007231:Infant, Newborn; D011169:Portal Vein / Q000000981:diagnostic imaging / Q000473:pathology; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000000981:diagnostic imaging; D013997:Time Factors; D014463:Ultrasonography