[Idiopathic retroperitoneal fibrosis: effectiveness of surgery combined with corticosteroid therapy].
Idiopathic retroperitoneal fibrosis (ERF) is a rare disease characterized by non-neoplastic fibroblastic and inflammatory proliferation. We describe a case of a 58-year-old man presenting with abdominal pain, weight loss and abdominal mass on clinical examination. The patient was evaluated by abdominal CT scan and magnetic resonance imaging which disclosed a periaortic soft-tissue mass with marked longitudinal extension below renal arteries origin. The diagnosis of ERF was histologically confirmed after surgical exploration and biopsies followed by extensive ablation of fibrous tissue. After 6 months of low-doses of postoperative steroid therapy retroperitoneal fibrous tissue had almost disappeared on CT examination.
Vincenzi
V
V
Divisione Medicina II, Ospedale Civile di Belluno.
Costan Biedo
F
F
D'Andrea
P
P
Favretti
F
F
De Marchi
G
G
Basevi
A
A
D003131:Combined Modality Therapy; D006801:Humans; D008297:Male; D008875:Middle Aged; D011241:Prednisone / Q000627:therapeutic use; D012185:Retroperitoneal Fibrosis / Q000188:drug therapy / Q000601:surgery / Q000628:therapy*
D011241:Prednisone
Fibrosi retroperitoneale idiopatica: efficacia della terapia associata chirurgica e corticosteroidea.