title: [Idiopathic retroperitoneal fibrosis: effectiveness of surgery combined with corticosteroid therapy].
abstract: Idiopathic retroperitoneal fibrosis (ERF) is a rare disease characterized by non-neoplastic fibroblastic and inflammatory proliferation. We describe a case of a 58-year-old man presenting with abdominal pain, weight loss and abdominal mass on clinical examination. The patient was evaluated by abdominal CT scan and magnetic resonance imaging which disclosed a periaortic soft-tissue mass with marked longitudinal extension below renal arteries origin. The diagnosis of ERF was histologically confirmed after surgical exploration and biopsies followed by extensive ablation of fibrous tissue. After 6 months of low-doses of postoperative steroid therapy retroperitoneal fibrous tissue had almost disappeared on CT examination.
authors.affiliation: Divisione Medicina II, Ospedale Civile di Belluno.
authors.forename: V
authors.initials: V
authors.lastname: Vincenzi
authors.forename: F
authors.initials: F
authors.lastname: Costan Biedo
authors.forename: P
authors.initials: P
authors.lastname: D'Andrea
authors.forename: F
authors.initials: F
authors.lastname: Favretti
authors.forename: G
authors.initials: G
authors.lastname: De Marchi
authors.forename: A
authors.initials: A
authors.lastname: Basevi
mesh_terms: D003131:Combined Modality Therapy; D006801:Humans; D008297:Male; D008875:Middle Aged; D011241:Prednisone / Q000627:therapeutic use; D012185:Retroperitoneal Fibrosis / Q000188:drug therapy / Q000601:surgery / Q000628:therapy*
chemical_list: D011241:Prednisone
vernacular_title: Fibrosi retroperitoneale idiopatica: efficacia della terapia associata chirurgica e corticosteroidea.