Case report 771: Melorheostosis in association with desmoid tumor.
Melorheostosis is a rare congenital disease, some 300 cases have been reported in the literature. The main purpose of this case report is twofold: (1) to present an unusual case of melorheostosis of the right hand, beginning in infancy, with serial radiographic studies to show the gradual progression of the disease; and (2) to present the first case with the development of "aggressive" fibromatosis (desmoid tumor) of the adjacent soft tissues, associated with melorheostosis.
Ippolito
V
V
Department of Orthopedic Oncology, Hospital of the Good Samaritan, Los Angeles, California.
Mirra
J M
JM
Motta
C
C
Chiodera
P
P
Bonetti
M F
MF
D002648:Child; D005260:Female; D005350:Fibroma / Q000150:complications* / Q000175:diagnosis / Q000000981:diagnostic imaging; D006225:Hand / Q000601:surgery; D006801:Humans; D008279:Magnetic Resonance Imaging; D008557:Melorheostosis / Q000150:complications* / Q000175:diagnosis / Q000000981:diagnostic imaging; D011859:Radiography; D012983:Soft Tissue Neoplasms / Q000150:complications* / Q000175:diagnosis / Q000000981:diagnostic imaging