[Evolutive aneurysms in type IV Ehlers-Danlos' syndrome].
Ehlers-Danlos syndrome is one of the most frequent hereditary connective tissue diseases. Type 4 or Sack-Barabas syndrome differs by the seventy of arterial complications. The authors report a case of severely progressive aneurysms since thrombosis of the aneurysm of the left hepatic artery, splenic artery, and small aneurysms of the lower pancreatic artery and rapid development of severe ectasia of the coeliac trunk and the commun hepatic artery all occurred over a period of three months.
Adami
P
P
Département de Radiologie Viscérale, Centre Hospitalier, Besançon.
Manzoni
P
P
Rohmer
P
P
D000328:Adult; D000783:Aneurysm / Q000150:complications* / Q000000981:diagnostic imaging; D001158:Arteries / Q000503:physiopathology; D004535:Ehlers-Danlos Syndrome / Q000150:complications*; D006465:Hemoperitoneum / Q000209:etiology; D006499:Hepatic Artery / Q000000981:diagnostic imaging / Q000503:physiopathology*; D006801:Humans; D008297:Male; D010179:Pancreas / Q000098:blood supply; D013157:Splenic Artery / Q000000981:diagnostic imaging / Q000503:physiopathology*; D013927:Thrombosis / Q000000981:diagnostic imaging / Q000209:etiology*; D013997:Time Factors; D014057:Tomography, X-Ray Computed
Anévrismes évolutifs au cours d'un syndrome d'Ehlers-Danlos de type IV. A propos d'une observation.