title: [The isolated agenesis of a branch of the pulmonary artery. A case report: its diagnosis and therapy].
abstract: We illustrate a case of so-called right pulmonary artery agenesis, discovered in a 3-month-old baby. This kind of malformation is rarely reported in neonatal age being most often discovered in the adulthood. The patient presented with cardiac failure, cyanosis and radiological features of cardiomegaly and left side pulmonary venous congestion. The diagnosis was strongly suspected by two-dimensional echocardiography and confirmed at cardiac catheterization. The patient was successfully operated upon with connection of main pulmonary artery to hilar right pulmonary artery. To the best of our knowledge, this is the first reported case of diagnosis and effective surgical therapy of right pulmonary artery agenesis in neonatal age.
authors.affiliation: Divisione di Cardiologia Emodinamica, Ospedale S Carlo, Potenza.
authors.forename: W
authors.initials: W
authors.lastname: Serino
authors.forename: G
authors.initials: G
authors.lastname: Argento
authors.forename: R
authors.initials: R
authors.lastname: Fiorilli
authors.forename: G
authors.initials: G
authors.lastname: Di Benedetto
authors.forename: F
authors.initials: F
authors.lastname: Velitti
mesh_terms: D001807:Blood Vessel Prosthesis; D004452:Echocardiography; D004562:Electrocardiography; D006801:Humans; D007223:Infant; D008297:Male; D011651:Pulmonary Artery / Q000002:abnormalities* / Q000000981:diagnostic imaging / Q000601:surgery; D011859:Radiography
vernacular_title: Agenesia isolata di un ramo dell'arteria polmonare. Presentazione di un caso: diagnosi e terapia.