[Dermatofibrosis lenticularis disseminata with osteopoikilosis. Buschke-Olldendorff syndrome].
Buschke-Ollendorff syndrome is characterized by the coincidence of dermato-fibrosis lenticularis disseminata and focal sclerotic bone dysplasia (osteopoikilosis). The case of a 39-year-old female is presented and the characteristic clinical, histopathological and radiological manifestations of this rare disease are reviewed. As focal bone lesions in Buschke-Ollendorff's syndrome are mostly asymptomatic, the rate of diagnosis could be increased if locations of predilection were subjected to X-ray examinations on clinical observation of the typical cutaneous manifestations.
Ramme
K
K
Hautklinik Minden.
Kolde
G
G
Stadler
R
R
D000328:Adult; D000818:Animals; D001842:Bone and Bones / Q000473:pathology; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D010026:Osteosclerosis / Q000175:diagnosis* / Q000473:pathology; D011817:Rabbits; D012594:Scleroderma, Localized / Q000175:diagnosis* / Q000473:pathology; D013577:Syndrome
Dermatofibrosis lenticularis disseminata mit Osteopoikilie. Buschke-Ollendorff-Syndrom.