title: [Dermatofibrosis lenticularis disseminata with osteopoikilosis. Buschke-Olldendorff syndrome].
abstract: Buschke-Ollendorff syndrome is characterized by the coincidence of dermato-fibrosis lenticularis disseminata and focal sclerotic bone dysplasia (osteopoikilosis). The case of a 39-year-old female is presented and the characteristic clinical, histopathological and radiological manifestations of this rare disease are reviewed. As focal bone lesions in Buschke-Ollendorff's syndrome are mostly asymptomatic, the rate of diagnosis could be increased if locations of predilection were subjected to X-ray examinations on clinical observation of the typical cutaneous manifestations.
authors.affiliation: Hautklinik Minden.
authors.forename: K
authors.initials: K
authors.lastname: Ramme
authors.forename: G
authors.initials: G
authors.lastname: Kolde
authors.forename: R
authors.initials: R
authors.lastname: Stadler
mesh_terms: D000328:Adult; D000818:Animals; D001842:Bone and Bones / Q000473:pathology; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D010026:Osteosclerosis / Q000175:diagnosis* / Q000473:pathology; D011817:Rabbits; D012594:Scleroderma, Localized / Q000175:diagnosis* / Q000473:pathology; D013577:Syndrome
vernacular_title: Dermatofibrosis lenticularis disseminata mit Osteopoikilie. Buschke-Ollendorff-Syndrom.