[Marfan syndrome. Cardiovascular manifestations diagnosed by echocardiography].
Echocardiographic and clinical evaluation was undertaken in 33 adult patients with Marfan syndrome. Cardiovascular manifestations were found in 32 (97%), mitral valve prolapse in 23 (70%) and dilated aortic root (> or = 21 mm/m2) in 26 patients (79%). The aortic root diameter was 58-85 mm in six patients with proximal aortic dissection, 57-76 mm in four patients undergoing elective surgery and 35-49 mm in conservatively treated patients. Average age at surgery was 28 years. Echocardiography with Doppler is the method of choice for diagnosis and control of patients with Marfan syndrome.
Vik-Mo
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Klinisk-fysiologisk avdeling Haukeland sykehus, Bergen.
D000293:Adolescent; D000328:Adult; D000368:Aged; D000784:Aortic Dissection / Q000175:diagnosis / Q000601:surgery; D017545:Aortic Aneurysm, Thoracic / Q000175:diagnosis / Q000601:surgery; D015150:Echocardiography, Doppler; D005260:Female; D006331:Heart Diseases / Q000175:diagnosis* / Q000601:surgery; D006801:Humans; D008297:Male; D008382:Marfan Syndrome / Q000175:diagnosis*; D008875:Middle Aged; D008945:Mitral Valve Prolapse / Q000175:diagnosis / Q000601:surgery
Marfans syndrom. Kardiovaskulaere manifestasjoner diagnostisert med ekkokardiografi.