Treatment of presumed arrhythmogenic right ventricular dysplasia in an adolescent.
Familial arrhythmogenic right ventricular dysplasia is a rare cardiomyopathy that is usually diagnosed on postmortem examination or on presentation with progressive congestive heart failure. We present a patient in whom an automatic implantable cardioverter-defibrillator was inserted prophylactically. A review of the condition and possible therapies is included.
Kirsch
L R
LR
Department of Pediatrics, New York Hospital-Cornell University Medical Center, New York 10021.
Weinstock
D J
DJ
Magid
M S
MS
Levin
A R
AR
Gold
J P
JP
D000293:Adolescent; D001145:Arrhythmias, Cardiac / Q000209:etiology* / Q000235:genetics / Q000628:therapy*; D017147:Defibrillators, Implantable; D004719:Endomyocardial Fibrosis / Q000150:complications / Q000473:pathology; D005260:Female; D006330:Heart Defects, Congenital / Q000150:complications* / Q000235:genetics / Q000473:pathology; D006352:Heart Ventricles / Q000002:abnormalities / Q000473:pathology; D006801:Humans; D017379:Hypertrophy, Left Ventricular / Q000150:complications / Q000473:pathology