Congenital histiocytosis X.
Congenital histiocytosis X involving multiple organs is a rare disease that causes rapid mortality in intrauterine and neonatal life. The diagnosis of histiocytosis X (Letterer-Siwe disease) should be considered in a neonate with vesiculated crusting skin lesions. We present clinical, radiographic and histopathological findings in a neonate with congenital histiocytosis who died of respiratory failure due to diffuse infiltration of lungs with histiocytic cells.
Vade
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Department of Radiology, Loyola University Medical Center, Maywood, Illinois 60153.
Hayani
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Pierce
K L
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D003937:Diagnosis, Differential; D005260:Female; D006646:Histiocytosis, Langerhans-Cell / Q000151:congenital* / Q000000981:diagnostic imaging; D006801:Humans; D007231:Infant, Newborn; D008168:Lung / Q000000981:diagnostic imaging; D008171:Lung Diseases / Q000151:congenital* / Q000000981:diagnostic imaging; D011859:Radiography; D012131:Respiratory Insufficiency / Q000209:etiology