Systemic vasculitis.
The systemic vasculitides are comparatively rare but important disorders of childhood. Apart from Henoch-Schönlein purpura, which is the commonest example in paediatric practice, Kawasaki disease is most often encountered. Polyarteritis and Wagener's granulomatosis have a lower incidence but are associated with a high morbidity and mortality. Newer investigative procedures and therapeutic approaches have led to more accurate diagnoses and improved outcome but further advances await a better understanding of the vasculitides: polyarteritis; Kawasaki disease; Wagener's granulomatosis; and ANCA in childhood.
Dillon
M J
MJ
Hospital for Sick Children, London, UK.
D001167:Arteritis / Q000145:classification / Q000503:physiopathology / Q000628:therapy; D014890:Granulomatosis with Polyangiitis / Q000145:classification / Q000503:physiopathology / Q000628:therapy; D006801:Humans; D009080:Mucocutaneous Lymph Node Syndrome / Q000145:classification / Q000503:physiopathology / Q000628:therapy; D014657:Vasculitis / Q000145:classification*