title: Chest-wall reconstruction for spondylocostal dysostosis.
abstract: A child with respiratory insufficiency due to a lethal syndrome known as spondylocostal dysostosis is described. Severe chest-wall deformities with resultant paradoxical chest-wall motion were successfully corrected by surgical reconstruction of the right thorax. We conclude that patients with the severe lethal form of the syndrome may benefit from aggressive surgical correction of the thoracic abnormality.
authors.affiliation: Department of Surgery, Childrens Hospital, Los Angeles, Calif.
authors.forename: L S
authors.initials: LS
authors.lastname: Nichter
authors.forename: S D
authors.initials: SD
authors.lastname: Chapin
authors.forename: W
authors.initials: W
authors.lastname: Wells
authors.forename: S E
authors.initials: SE
authors.lastname: Downey
mesh_terms: D000015:Abnormalities, Multiple / Q000601:surgery*; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D011183:Postoperative Complications / Q000601:surgery; D012086:Reoperation; D012131:Respiratory Insufficiency / Q000209:etiology / Q000601:surgery; D012272:Ribs / Q000002:abnormalities* / Q000601:surgery; D012600:Scoliosis / Q000209:etiology / Q000601:surgery; D013131:Spine / Q000002:abnormalities* / Q000601:surgery; D013526:Surgical Mesh