Wiskott-Aldrich syndrome in a Jamaican.
A 3-week-old boy presented with severe thrombocytopenia and recurrent infections. He was subsequently found to have Wiskott-Aldrich Syndrome, a rare X-linked disorder. Splenectomy was performed and he died of post-splenectomy sepsis despite prophylactic antibiotic therapy. This is the first recorded case in the English-speaking Caribbean.
Walters
J P
JP
Department of Pathology, U.W.I., Jamaica.
Morais
P
P
D006801:Humans; D007231:Infant, Newborn; D007563:Jamaica; D008297:Male; D011008:Pneumococcal Infections / Q000209:etiology; D011183:Postoperative Complications; D012008:Recurrence; D013156:Splenectomy; D014923:Wiskott-Aldrich Syndrome / Q000175:diagnosis* / Q000601:surgery