Multiple pulmonary-artery aneurysms due to mucoid vasculopathy--angiographic and histological observations.
Multiple peripheral pulmonary artery aneurysms were diagnosed by computed tomography and confirmed angiographically in a 7-year-old boy. On histological examination unusual mucoid vasculopathic changes were noted in the pulmonary artery aneurysms and pulmonary vasculature as a part of systemic vascular involvement. This case demonstrates a new association between mucoid vasculopathic changes and pulmonary aneurysms. Mucoid vasculopathy could represent one more disorder having a causative role in the etiology of intrapulmonary arterial aneurysms.
Gupta
A K
AK
Department of Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India.
Sandhyamani
S
S
Ravimandalam
K
K
Rao
V R
VR
Neelakandhan
K S
KS
Joseph
S
S
Unni
M
M
Rao
A S
AS
D000783:Aneurysm / Q000000981:diagnostic imaging* / Q000209:etiology / Q000473:pathology / Q000601:surgery; D002648:Child; D006801:Humans; D008168:Lung / Q000473:pathology; D008297:Male; D009083:Mucopolysaccharidoses / Q000150:complications / Q000000981:diagnostic imaging* / Q000473:pathology / Q000601:surgery; D011651:Pulmonary Artery / Q000000981:diagnostic imaging* / Q000473:pathology / Q000601:surgery; D011859:Radiography