[Ehlers-Danlos syndrome type IV, revealed by a primary dissecting aneurysm of the left subclavian artery].
The authors report an unusual dissecting aneurysm of the left subclavian artery occurring in a patient suffering from the Ehlers-Danlos syndrome. Clinical history and skin biopsy permitted this diagnosis. Surgical treatment associated resection of the aneurysm, ligation of the proximal part of the subclavian artery and a prosthetic bypass between carotid and subclavian artery. Spontaneous dissecting aneurysm is a rare disease and one must think before surgery to arterial dysplasia. Technical features of the surgical treatment are discussed.
Noel
S F
SF
Service de Chirurgie cardiaque, thoracique et vasculaire, Hôpital G.R. Laënnec, Nantes.
Chaillou
P
P
Pistorius
M A
MA
Planchon
B
B
Patra
P
P
D000328:Adult; D000784:Aortic Dissection / Q000150:complications* / Q000601:surgery; D004535:Ehlers-Danlos Syndrome / Q000150:complications / Q000175:diagnosis*; D006801:Humans; D008297:Male; D013348:Subclavian Artery
Syndrome d'Ehlers-Danlos de type IV, révélé par un anévrysme disséquant primitif de l'artère sous-clavière gauche.