Bednar tumor pattern in recurring giant cell fibroblastoma.
Giant cell fibroblastoma (GCF) and Bednar tumor (BT) have been perceived as two rare, not directly related, soft tissue neoplasms. Recent studies, separately conducted on each process, have presented evidence indicating that, in each instance, the tumor seemed to be related to the dermatofibrosarcoma protuberans. The case being reported provides additional evidence supporting those previous results and, for the first time, documents a direct link between GCF and BT, as seen in this girl who had a vulvar GCF resected at 1-year of age, with recurrence, 1.5 years later, as a mixed BT-GCF.
De Chadarévian
J P
JP
Department of Pathology, St. Christopher's Hospital for Children, Philadelphia, PA 19134-1095.
Coppola
D
D
Billmire
D F
DF
D005260:Female; D005354:Fibrosarcoma / Q000473:pathology* / Q000601:surgery; D006801:Humans; D007223:Infant; D009364:Neoplasm Recurrence, Local; D012983:Soft Tissue Neoplasms / Q000473:pathology* / Q000601:surgery