Intrapelvic Wilms tumor: report of 2 cases and review of the literature.
Wilms tumor arising from the renal parenchyma usually presents initially as an abdominal mass. A review of the literature revealed fewer than 10 cases manifesting as a renal pelvic mass occupying primarily the collecting system. We have treated 2 patients with this unusual presentation: 1) a 4-month-old male infant whose initial radiological investigation demonstrated a left renal neoplasm measuring 10 x 7 x 5 cm.; bisection of the kidney showed a tumor completely filling the collecting system to the proximal ureter with extreme attenuation of the renal parenchyma, and 2) a 9-year-old boy who was hospitalized due to hematuria; ultrasonography, computerized tomography and magnetic resonance imaging showed a mass in the right renal pelvis; gross pathology displayed a 7 x 6 x 5 cm. polypoid mass occupying the renal pelvis without parenchymal involvement. Microscopically, both lesions were typical Wilms tumors. We discuss the characteristic clinical manifestations, diagnosis and treatment, and review the literature.
Department of Pediatrics, Chang-Gung Memorial Hospital, Kaohsiung, Taiwan, Republic of China.
C K
CK
Niu
W F
WF
Chen
J H
JH
Chuang
T J
TJ
Yu
Y L
YL
Wan
W J
WJ
Chen
D002648:Child; D006801:Humans; D007223:Infant; D007680:Kidney Neoplasms / Q000175:diagnosis*; D007682:Kidney Pelvis; D008297:Male; D009396:Wilms Tumor / Q000175:diagnosis*