[Dedifferentiated chondrosarcoma with maxillary involvement. An anatomo-clinical study, surgical treatment and prosthetic rehabilitation. Apropos of a case].
A 19 year old girl presented with a dedifferentiated chondrosarcoma of maxilla. The recurring tumor, diagnosed initially from the provoked pain, appeared on the scan image as a heterogeneous mass containing numerous calcifications. Histology showed, within a well differentiated chondrosarcoma, an anaplastic sarcomatous zone of the malignant fibrous histiocytoma (MFH) type. This histologic appearance is consistent with a poorer clinical prognosis. Radical surgery of the 4th tumor recurrence was combined with maxillofacial prosthetic rehabilitation. This appears to be first reported case of a dedifferentiated chondrosarcoma of the MFH type located in the maxilla.
Paume
P
P
Service de Chirurgie Plastique, H.I.A. Bégin, Saint-Mandé.
Grippari
J L
JL
Payement
G
G
Dandrau
J P
JP
Cariou
J L
JL
Bellavoir
A
A
D000328:Adult; D002813:Chondrosarcoma / Q000473:pathology* / Q000532:radiotherapy / Q000534:rehabilitation / Q000601:surgery; D003131:Combined Modality Therapy; D005260:Female; D005354:Fibrosarcoma / Q000473:pathology; D018219:Histiocytoma, Benign Fibrous / Q000473:pathology; D006801:Humans; D008441:Maxillary Neoplasms / Q000473:pathology* / Q000532:radiotherapy / Q000534:rehabilitation / Q000601:surgery; D009364:Neoplasm Recurrence, Local; D010158:Palatal Obturators