Extrarenal Wilms' tumor. Unusual presentation in the lumbosacral region.
True extrarenal Wilms' tumor is a rare malignant neoplasm most frequently presenting in the retroperitoneal or inguinal regions. We report an unusual subcutaneous lumbosacral (LS) region extrarenal Wilms' tumor without associated teratomatous tumor elements or associated neural tube defect in a 2 1/2-year-old girl. Pathologic review revealed features of true extrarenal Wilms' tumor, and the patient remains in complete remission following surgery and combination chemotherapy. This report illustrates the importance of early surgical intervention and pathologic examination of similar soft tissue masses in children.
Fahner
J B
JB
Division of Pediatric Hematology/Oncology, Butterworth Hospital, Grand Rapids, MI 49503.
Switzer
R
R
Freyer
D R
DR
Mann
J D
JD
Mann
R J
RJ
D003609:Dactinomycin / Q000008:administration & dosage; D003951:Diagnostic Errors; D005260:Female; D006801:Humans; D007223:Infant; D008067:Lipoma / Q000175:diagnosis; D008161:Lumbosacral Region; D012983:Soft Tissue Neoplasms / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery; D014750:Vincristine / Q000008:administration & dosage; D009396:Wilms Tumor / Q000175:diagnosis / Q000188:drug therapy / Q000601:surgery
D003609:Dactinomycin; D014750:Vincristine