Chylous pleural effusion associated with primary lymphedema and lymphangioma-like malformations.
We describe a patient with a chylous pleural effusion associated with primary lymphedema of his right leg and abdominal wall. On evaluation a generalized, severe hypoplasia of the lymphatic system turned out to be associated with hyperplastic, lymphangioma-like malformations.
Bresser
P
P
Department of Pulmonology, Academic Medical Center, Amsterdam, The Netherlands.
Kromhout
J G
JG
Reekers
J A
JA
Verhage
T L
TL
D000328:Adult; D002916:Chylothorax / Q000209:etiology*; D006801:Humans; D008202:Lymphangioma / Q000150:complications; D008208:Lymphatic System / Q000002:abnormalities*; D008209:Lymphedema / Q000150:complications*; D008297:Male; D010996:Pleural Effusion / Q000209:etiology*