Sézary syndrome in an 11-year-old girl.
All forms of cutaneous T-cell lymphoma are rare in children. We describe an 11-year-old girl who had generalized exfoliative erythroderma, intense pruritus, peripheral lymphadenopathy, mycosis cells in the skin and lymph nodes, and Sézary cells in the peripheral blood. Results of a biopsy specimen of involved skin showed changes consistent with mycosis fungoides. A classic case of Sézary syndrome has not previously been reported in childhood or preadolescence.
Meister
L
L
Department of Pediatrics, University of Miami School of Medicine, FL 33101.
Duarte
A M
AM
Davis
J
J
Perez
J L
JL
Schachner
L A
LA
D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D002648:Child; D003131:Combined Modality Therapy; D005260:Female; D006801:Humans; D009182:Mycosis Fungoides / Q000188:drug therapy / Q000473:pathology; D011701:PUVA Therapy; D012751:Sezary Syndrome / Q000188:drug therapy / Q000473:pathology*; D012878:Skin Neoplasms / Q000188:drug therapy / Q000473:pathology*