Renal angiomyolipoma associated with neurofibromatosis and primary carcinoid of mesentery.
A patient with von Recklinghausen's disease manifested by dermal neurofibromatosis and cafe-au-lait spots presented with complaints of malaise, weight loss, lower extremity weakness, and a palpable left lower abdominal quadrant mass. Evaluation revealed a lumbar neurofibroma, a localized primary carcinoid tumor of the mesentery, and a left renal angiomyolipoma. Although an association between neurofibromatosis and carcinoid has been previously reported, we believe this is the first report documenting the association of all three entities.
Stone
N N
NN
Department of Urology, Mount Sinai Services, Elmhurst Hospital Center, New York.
Atlas
I
I
Kim
U S
US
Kwan
D
D
Leventhal
I
I
Waxman
J S
JS
D002276:Carcinoid Tumor / Q000175:diagnosis; D005260:Female; D006391:Hemangioma / Q000175:diagnosis; D006801:Humans; D007680:Kidney Neoplasms / Q000175:diagnosis; D008067:Lipoma / Q000175:diagnosis; D008643:Mesentery; D008875:Middle Aged; D009378:Neoplasms, Multiple Primary / Q000175:diagnosis; D009455:Neurofibroma / Q000175:diagnosis; D009456:Neurofibromatosis 1 / Q000175:diagnosis; D010534:Peritoneal Neoplasms / Q000175:diagnosis; D013120:Spinal Cord Neoplasms / Q000175:diagnosis