The association of potentially lethal neurologic syndromes with scleromyxedema (papular mucinosis).
Two patients with scleromyxedema who had progressive neurologic impairment are described. One patient died, and one required prolonged mechanical ventilation. A review of the literature has produced 24 other cases of scleromyxedema in which neurologic changes were prominent.
Webster
G F
GF
Department of Dermatology, Jefferson Medical College, Philadelphia, PA 19107-5102.
Matsuoka
L Y
LY
Burchmore
D
D
D000328:Adult; D002908:Chronic Disease; D006801:Humans; D008297:Male; D008875:Middle Aged; D017520:Mucinoses / Q000150:complications* / Q000473:pathology; D009422:Nervous System Diseases / Q000209:etiology* / Q000276:immunology; D010266:Paraproteins / Q000032:analysis
D010266:Paraproteins