A survey of patients with Ehlers-Danlos syndrome.
Ehlers-Danlos syndrome (EDS) is an inherited disorder of collagen biosynthesis. Nine types of the disorder are now recognized. A survey of 151 EDS patients showed a high percentage of the patients were classified as having Types I through IV. Bracing and fusion appear to be the most commonly used methods of orthopedic care. Surgical complications were common. The orthopedist was often the first practitioner to diagnose and treat the patient with EDS. A fundamental understanding of this complex disorder and its varied manifestations is essential to prevent major life-threatening complications.
Ainsworth
S R
SR
Department of Orthopaedic Surgery, Eastern Virginia Graduate School of Medicine, Norfolk.
Aulicino
P L
PL
D000328:Adult; D004535:Ehlers-Danlos Syndrome / Q000145:classification* / Q000150:complications / Q000628:therapy; D005128:Eye Diseases / Q000209:etiology; D005260:Female; D005831:Genital Diseases, Female / Q000209:etiology; D006331:Heart Diseases / Q000209:etiology; D006801:Humans; D007592:Joint Diseases / Q000209:etiology; D008297:Male; D009135:Muscular Diseases / Q000209:etiology; D007744:Obstetric Labor Complications / Q000209:etiology; D011247:Pregnancy; D011248:Pregnancy Complications / Q000209:etiology; D012871:Skin Diseases / Q000209:etiology; D014076:Tooth Diseases / Q000209:etiology