title: The association of potentially lethal neurologic syndromes with scleromyxedema (papular mucinosis).
abstract: Two patients with scleromyxedema who had progressive neurologic impairment are described. One patient died, and one required prolonged mechanical ventilation. A review of the literature has produced 24 other cases of scleromyxedema in which neurologic changes were prominent.
authors.affiliation: Department of Dermatology, Jefferson Medical College, Philadelphia, PA 19107-5102.
authors.forename: G F
authors.initials: GF
authors.lastname: Webster
authors.forename: L Y
authors.initials: LY
authors.lastname: Matsuoka
authors.forename: D
authors.initials: D
authors.lastname: Burchmore
mesh_terms: D000328:Adult; D002908:Chronic Disease; D006801:Humans; D008297:Male; D008875:Middle Aged; D017520:Mucinoses / Q000150:complications* / Q000473:pathology; D009422:Nervous System Diseases / Q000209:etiology* / Q000276:immunology; D010266:Paraproteins / Q000032:analysis
chemical_list: D010266:Paraproteins