title: Sézary syndrome in an 11-year-old girl.
abstract: All forms of cutaneous T-cell lymphoma are rare in children. We describe an 11-year-old girl who had generalized exfoliative erythroderma, intense pruritus, peripheral lymphadenopathy, mycosis cells in the skin and lymph nodes, and Sézary cells in the peripheral blood. Results of a biopsy specimen of involved skin showed changes consistent with mycosis fungoides. A classic case of Sézary syndrome has not previously been reported in childhood or preadolescence.
authors.affiliation: Department of Pediatrics, University of Miami School of Medicine, FL 33101.
authors.forename: L
authors.initials: L
authors.lastname: Meister
authors.forename: A M
authors.initials: AM
authors.lastname: Duarte
authors.forename: J
authors.initials: J
authors.lastname: Davis
authors.forename: J L
authors.initials: JL
authors.lastname: Perez
authors.forename: L A
authors.initials: LA
authors.lastname: Schachner
mesh_terms: D000971:Antineoplastic Combined Chemotherapy Protocols / Q000627:therapeutic use; D002648:Child; D003131:Combined Modality Therapy; D005260:Female; D006801:Humans; D009182:Mycosis Fungoides / Q000188:drug therapy / Q000473:pathology; D011701:PUVA Therapy; D012751:Sezary Syndrome / Q000188:drug therapy / Q000473:pathology*; D012878:Skin Neoplasms / Q000188:drug therapy / Q000473:pathology*