title: Chylous pleural effusion associated with primary lymphedema and lymphangioma-like malformations.
abstract: We describe a patient with a chylous pleural effusion associated with primary lymphedema of his right leg and abdominal wall. On evaluation a generalized, severe hypoplasia of the lymphatic system turned out to be associated with hyperplastic, lymphangioma-like malformations.
authors.affiliation: Department of Pulmonology, Academic Medical Center, Amsterdam, The Netherlands.
authors.forename: P
authors.initials: P
authors.lastname: Bresser
authors.forename: J G
authors.initials: JG
authors.lastname: Kromhout
authors.forename: J A
authors.initials: JA
authors.lastname: Reekers
authors.forename: T L
authors.initials: TL
authors.lastname: Verhage
mesh_terms: D000328:Adult; D002916:Chylothorax / Q000209:etiology*; D006801:Humans; D008202:Lymphangioma / Q000150:complications; D008208:Lymphatic System / Q000002:abnormalities*; D008209:Lymphedema / Q000150:complications*; D008297:Male; D010996:Pleural Effusion / Q000209:etiology*