[A case of successfully operated hypertrophic obstructive cardiomyopathy in a child].
A case of surgical treatment of hypertrophic obstructive cardiomyopathy (HOCM) in a 5-year-old boy is reported. This is the youngest case in Japan. He had been diagnosed as HOCM and treated conservatively with beta-blocker and Ca-antagonist, but his complaints of dyspnea and chest oppression during efforts had increased. Cardiac catheterization showed a peak systolic pressure gradient of 110 mmHg between the left ventricle and systemic artery, and echocardiogram disclosed a systolic anterior motion (SAM) of the mitral valve and mitral regurgitation (MR). At operation transaortic septal myectomy and myotomy were performed according to preoperative findings by echocardiogram and MRI, and a marked reduction in pressure gradient and a decrease in SAM and MR were obtained. Thus, a satisfactory result can be obtained by myectomy and myotomy without mitral valve replacement in a pediatric patient with HOCM, based on the preoperative image analysis.
Takahashi
A
A
Second Division of Surgery, Children's Research Hospital, Kyoto Prefectural University of Medicine, Japan.
Wada
Y
Y
Kawai
T
T
Kobashi
T
T
Oga
K
K
Oka
T
T
D002312:Cardiomyopathy, Hypertrophic / Q000601:surgery*; D002675:Child, Preschool; D006346:Heart Septum / Q000601:surgery; D006801:Humans; D008297:Male