[Localized cicatricial bullous pemphigoid of the Brunsting-Perry type].
Localized cicatricial pemphigoid of the Brunsting-Perry type is a very rare bullous condition, which has so far been reported in 51 cases. It is characterized by scarring blisters confined to the head, scalp and neck. Diagnosis can be difficult because of the discrete skin lesions, often repeatedly false-negative direct immunofluorescence, and the absence of circulating antibodies. We report on a 87-year-old male patient with the typical clinical feature of a cicatricial pemphigoid of the Brunsting-Perry type and give a review of the 51 cases published in the world literature.
Kurzhals
G
G
Dermatologische und Allergologische Abteilung, Städtisches Krankenhaus München-Schwabing, Ludwig-Maximilians Universität München.
Maciejewski
W
W
Agathos
M
M
Meurer
M
M
Mily
H
H
Breit
R
R
D000368:Aged; D000369:Aged, 80 and over; D001323:Autoantibodies / Q000032:analysis; D001485:Basement Membrane / Q000276:immunology / Q000473:pathology; D003094:Collagen / Q000276:immunology; D003176:Complement C3 / Q000032:analysis; D005148:Facial Dermatoses / Q000276:immunology / Q000473:pathology*; D005455:Fluorescent Antibody Technique; D006801:Humans; D007074:Immunoglobulin G / Q000032:analysis; D008297:Male; D010390:Pemphigoid, Benign Mucous Membrane / Q000276:immunology / Q000473:pathology*; D012867:Skin / Q000276:immunology / Q000473:pathology
D001323:Autoantibodies; D003176:Complement C3; D007074:Immunoglobulin G; D003094:Collagen