Autoimmune exocrinopathy presenting as recurrent parotitis of childhood.
OBJECTIVE
To describe a case of autoimmune exocrinopathy in a child at the age of 3 months who presented with the original diagnosis of recurrent parotitis.


METHODS
This a case report of a 9-year-old girl with recurrent parotitis who was later found to have Sjögren's syndrome. The literature relating to primary Sjögren's syndrome in the pediatric population is reviewed.


METHODS
The patient was seen in the rheumatology and otolaryngology clinics at a university medical center.


METHODS
This study did not address therapy.


METHODS
Diagnosis of Sjögren's syndrome.


RESULTS
The patient had xerostomia, an abnormal result of a salivary gland biopsy, SSA and SSB antibodies, and the histocompatibility antigens HLA-B8 and HLA-DR3 that are associated with Sjögren's syndrome.


CONCLUSIONS
Primary Sjögren's syndrome should be considered in cases of recurrent parotitis of childhood. More studies are needed to assess the natural history of autoimmune exocrinopathy in children.
Hearth-Holmes
M
M
Department of Medicine, Louisiana State University Medical Center, Shreveport 71130-3932.
Baethge
B A
BA
Abreo
F
F
Wolf
R E
RE
D001327:Autoimmune Diseases / Q000175:diagnosis*; D002648:Child; D003937:Diagnosis, Differential; D005260:Female; D006801:Humans; D010309:Parotitis / Q000175:diagnosis*; D012008:Recurrence; D012859:Sjogren's Syndrome / Q000175:diagnosis*