title: Congenital longitudinal deficiency of the fibula (fibular hemimelia). Parental refusal of amputation.
abstract: Fibular hemimelia with significant limb-length inequality is usually best treated with foot ablation and prosthetic fitting. Parents tend to be reluctant to agree to allow their child's foot to be amputated at an early age, especially when the foot is near normal and the limb length is not grossly abnormal. Experience with some families of children with fibular hemimelia who initially refused amputation of the affected limb prompted a retrospective review of the treatment experience with these children. Twenty-four children with 36 affected limbs were treated during the last three decades. Amputation of the foot was performed for 16 limbs in 12 of the 24 patients. The 12 patients whose limbs were not amputated were reviewed in detail. Six of these children were advised to have an amputation, but their families refused to consent. These children were managed by specially designed prostheses to incorporate their foot deformity and limb-length inequality. Four patients required subsequent corrective surgical procedures in an attempt to stabilize the feet or lengthen the limb. To facilitate treatment decisions for both the clinic team as well as the involved families, the authors propose a more practical classification of fibular hemimelia.
authors.affiliation: Children's Hospital, University of Manitoba, Winnipeg, Canada.
authors.forename: M
authors.initials: M
authors.lastname: Letts
authors.forename: N
authors.initials: N
authors.lastname: Vincent
mesh_terms: D000015:Abnormalities, Multiple / Q000145:classification* / Q000601:surgery; D000293:Adolescent; D000671:Amputation, Surgical; D002648:Child; D002675:Child, Preschool; D005260:Female; D005360:Fibula / Q000002:abnormalities* / Q000601:surgery; D005528:Foot / Q000601:surgery; D005532:Foot Deformities, Congenital / Q000145:classification; D006801:Humans; D008297:Male; D010290:Parents; D012189:Retrospective Studies