Cardiac surgery with extracorporeal circulation in severe factor VII deficiency.
We describe here successful open heart surgery with extracorporeal circulation and haemodilution in a child with severe congenital factor VII deficiency. Substitution therapy was realized with factor VII concentrate (SD proconvertin concentrate, Bio-Transfusion). This is the first report case of successful cardiac surgery in severe congenital factor VII deficiency.
Ferster
A
A
Department of Haematology, Hôpital Universitaire des Enfants Reine Fabiola, Free University Brussels (ULB), Belgium.
Capouet
V
V
Deville
A
A
Fondu
P
P
Corazza
F
F
D002675:Child, Preschool; D005112:Extracorporeal Circulation; D005167:Factor VII / Q000008:administration & dosage / Q000032:analysis / Q000235:genetics; D005168:Factor VII Deficiency; D006344:Heart Septal Defects, Atrial / Q000601:surgery*; D006438:Hemodilution; D006801:Humans; D008297:Male; D011182:Postoperative Care; D011300:Preoperative Care; D011517:Prothrombin Time
D005167:Factor VII