Progressive systemic sclerosis and IgA deficiency in a young man.
A 21-year-old man presented with an IgA deficiency and symptoms reminiscent of a systemic lupus erythematosus. After 7 years systemic sclerosis developed involving the lungs, oesophagus, central nervous system and reproductive system. Connective tissue disease and its relationship to IgA deficiency will be discussed.
Veen
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Zuiderziekenhuis Department of Medicine, Rotterdam, The Netherlands.
Swaak
A J
AJ
D000328:Adult; D002561:Cerebrovascular Disorders / Q000150:complications; D006801:Humans; D017098:IgA Deficiency / Q000150:complications*; D007159:Immunologic Tests; D008180:Lupus Erythematosus, Systemic / Q000097:blood / Q000150:complications / Q000276:immunology; D008297:Male; D009460:Neurologic Examination; D012595:Scleroderma, Systemic / Q000150:complications*