title: Surgical treatment of congenital bronchopulmonary disease in children.
abstract: From 1987 to 1992, 22 children (age 0 days-14 years) were operated for congenital bronchopulmonary disease. One patient had a hamartoma. Four children had a bronchogenic cyst, in 1 patient combined with an esophageal duplication. Intrapulmonary sequestration was diagnosed in 3 children; one of whom had an esophageal duplication as well. Four children had localized emphysema. In 1 patient histology showed rhabdomyosarcoma. A lobectomy was performed following chemotherapy but recurrence was not resectable at a third thoracotomy. Ten patients had cystic adenomatoid malformation, 6 were dependent on artificial ventilation before surgery. Three patients with cystic adenomatoid malformation died in hospital: 2 after pneumonectomy who were shown to have bilateral disease and 1 died after bilobectomy and was shown to have a hypoplastic contralateral lung. Hospital morbidity involved 1 patient with recurrent pneumothorax, 2 with atelectasis of the operated lung and 3 with prolonged artificial ventilation. Late mortality involved 1 patient due to pulmonary rhabdomyosarcoma. After 1-26 months of follow-up there were no late complications. Adequate multidisciplinary treatment allows acceptable mortality and low morbidity in surgery for congenital bronchopulmonary disease in children.
authors: Department of Thoracic Surgery, Dijkzigt University Hospital, Rotterdam, The Netherlands.
authors: A J
authors: AJ
authors: Bogers
authors: F W
authors: FW
authors: Hazebroek
authors: J
authors: J
authors: Molenaar
authors: E
authors: E
authors: Bos
mesh_terms: D000293:Adolescent; D000367:Age Factors; D001982:Bronchial Diseases / Q000151:congenital / Q000601:surgery; D001994:Bronchogenic Cyst / Q000601:surgery; D001998:Bronchopulmonary Sequestration / Q000601:surgery; D002648:Child; D002675:Child, Preschool; D015615:Cystic Adenomatoid Malformation of Lung, Congenital / Q000601:surgery; D005260:Female; D006222:Hamartoma / Q000151:congenital / Q000601:surgery; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008171:Lung Diseases / Q000151:congenital* / Q000601:surgery*; D008175:Lung Neoplasms / Q000151:congenital / Q000601:surgery; D008297:Male; D011030:Pneumothorax / Q000601:surgery; D001261:Pulmonary Atelectasis / Q000601:surgery; D011656:Pulmonary Emphysema / Q000151:congenital / Q000601:surgery; D012127:Respiratory Distress Syndrome, Newborn / Q000601:surgery; D012141:Respiratory Tract Infections / Q000151:congenital; D016896:Treatment Outcome