A possible late onset variation of Papillon-Lefèvre syndrome: report of 3 cases.
Three unusual cases of Papillon-Lefèvre syndrome with late onset of features and relatively mild periodontal disease are presented. These examples confirm some of the late onset of features and mild periodontal presentation of a previous case report. Bacteriologic associations, polymorphonuclear leukocyte chemotactic, phagocytic, and bactericidal activity, and therapeutics with regard to this syndrome are discussed.
Brown
R S
RS
Department of Oral Diagnostic Services, University of Texas Health Sciences, Houston.
Hays
G L
GL
Flaitz
C M
CM
O'Neill
P A
PA
Abramovitch
K
K
White
R R
RR
D000328:Adult; D016301:Alveolar Bone Loss / Q000473:pathology; D002448:Cell Adhesion; D002470:Cell Survival; D002634:Chemotaxis, Leukocyte / Q000502:physiology; D005260:Female; D005882:Gingival Diseases / Q000473:pathology; D006801:Humans; D007958:Leukocyte Count; D009504:Neutrophils / Q000502:physiology; D010214:Papillon-Lefevre Disease / Q000235:genetics / Q000473:pathology*; D010510:Periodontal Diseases / Q000473:pathology*; D010587:Phagocytosis / Q000502:physiology