A possible late onset variation of Papillon-Lefèvre syndrome: report of 3 cases.
Three unusual cases of Papillon-Lefèvre syndrome with late onset of features and relatively mild periodontal disease are presented. These examples confirm some of the late onset of features and mild periodontal presentation of a previous case report. Bacteriologic associations, polymorphonuclear leukocyte chemotactic, phagocytic, and bactericidal activity, and therapeutics with regard to this syndrome are discussed.
Department of Oral Diagnostic Services, University of Texas Health Sciences, Houston.
R S
RS
Brown
G L
GL
Hays
C M
CM
Flaitz
P A
PA
O'Neill
K
K
Abramovitch
R R
RR
White
D000328:Adult; D016301:Alveolar Bone Loss / Q000473:pathology; D002448:Cell Adhesion; D002470:Cell Survival; D002634:Chemotaxis, Leukocyte / Q000502:physiology; D005260:Female; D005882:Gingival Diseases / Q000473:pathology; D006801:Humans; D007958:Leukocyte Count; D009504:Neutrophils / Q000502:physiology; D010214:Papillon-Lefevre Disease / Q000235:genetics / Q000473:pathology*; D010510:Periodontal Diseases / Q000473:pathology*; D010587:Phagocytosis / Q000502:physiology