[Kartagener's syndrome with normal ciliary ultrastructure].
We present a case of a man with Kartagener's syndrome (KS) (situs inversus, sinusitis and bronchiectasias) and with clinical signs of respiratory infection. An electronic microscopy study was conducted, showing a normal bronchial cilium. Although, traditionally, KS has been associated to ultrastructural abnormalities of the cilium, some cases similar to ours have been described, suggesting the presence of functional ciliary disorders in absence of ultrastructural defects.
Steen
B C
BC
Servicio de Neumología, Hospital de la Princesa, Madrid.
Flórez Martín
S
S
Jiménez Ruiz
C A
CA
D000328:Adult; D001980:Bronchi / Q000473:pathology* / Q000648:ultrastructure; D002923:Cilia / Q000648:ultrastructure; D006801:Humans; D007619:Kartagener Syndrome / Q000175:diagnosis / Q000473:pathology*; D008297:Male
Síndrome de Kartagener con ultraestructura ciliar normal.