Respiratory function in the prune-belly syndrome.
Respiratory function was evaluated in 11 patients with prune-belly syndrome. Nine had evidence of gas trapping and six of restrictive lung disease. These abnormalities of lung function appear to be secondary to the musculoskeletal disorder associated with prune-belly syndrome rather than parenchymal lung disease.
Crompton
C H
CH
Department of Pediatrics, Hospital for Sick Children, Toronto, Canada.
MacLusky
I B
IB
Geary
D F
DF
D000293:Adolescent; D000328:Adult; D002648:Child; D006801:Humans; D008168:Lung / Q000503:physiopathology*; D008297:Male; D011535:Prune Belly Syndrome / Q000503:physiopathology*; D012115:Residual Volume / Q000502:physiology; D012129:Respiratory Function Tests; D014109:Total Lung Capacity / Q000502:physiology