[Familial sacrococcygeal teratoma].
Familial sacrococcygeal teratomas are very rare. Up to now, only 8 kindreds (31 patients, including 1 Japanese kindreds) have been reported. All cases are Altman type IV variety. The tumor complex consists of a presacral teratoma and sacrococcygeal bony anomalies. The most common symptoms are constipation and anorectal stenosis. Two patients died. One died of meningitis following removal of a large benign tumor because of communication with a spinal arachinoid space. The other, with a large benign tumor, died as a result of malignant change, 10 years later after the first operation. The incidence of malignant change of familiar sacrococcygeal teratoma is rare in comparison with that of non-familiar sacrococcygeal teratomas.
Department of Pediatric Surgery, National Okayama Hospital, Children's Medical Center.
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T
Goto
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K
Aoyama
D000367:Age Factors; D005192:Family Health; D005260:Female; D006801:Humans; D008297:Male; D010375:Pedigree; D012447:Sacrum; D012737:Sex Factors; D013125:Spinal Neoplasms / Q000145:classification / Q000235:genetics*; D013724:Teratoma / Q000145:classification / Q000235:genetics*