[Our experience in the management of portal cavernoma in children].
The authors present 14 patients affected with portal cavernoma, diagnosed and controlled over the last 12 years. The splenomegaly (60%) and the digestive hemorrhages (40%) were the initial study causes. The cavernoma appeared idiopathic in 10 patients or secondary either to a catheterization of umbilical vein (3 cases) or onfalitis (1 case). The first clinical manifestation oscillated between the ages of 3 months to nine years. The diagnosis was performed in the initial cases (4 cases) using splenoportography (3 cases) and superior mesenteric arteriography (SMA) in the other. In the remaining cases the ultrasonography together with the endoscopic evidence of the varies backed up the diagnosis. Before the intervention, a SMA was performed in all cases. The surgical decision was taken with regards to the persistence of the digestive bleeding after the start of medical treatment with propranolol, cimetidine, and sucralfate, along with the existence of dangerous varices. Eight patients were operated on, two by the Warren technique, four by mesocaval jugular graft interposition (MJI) and two by azigo portal disconnection (APD). The shunts initially controlled the bleeding in all cases. There was one rebleeding instance at eleven months in a patient operated on by MJI, and in another by APD. Four patients continue medical treatment without problems, and two are free of treatment. Our experience with varies sclerosis is limited to two cases, although since the beginning of the treatment, one year ago, neither of them has bled.
Departamento de Cirugía Pediátrica, H. Universitario Materno-Infantil Vall d'Hebron, Barcelona.
J
J
Broto
D
D
Infante
R
R
Tormo
C
C
Marhuenda
J M
JM
Gil Vernet
J
J
Boix-Ochoa
D000792:Angiography; D002648:Child; D002675:Child, Preschool; D006392:Hemangioma, Cavernous / Q000150:complications / Q000473:pathology* / Q000601:surgery; D006801:Humans; D006975:Hypertension, Portal / Q000150:complications; D007223:Infant; D007601:Jugular Veins / Q000601:surgery; D008113:Liver Neoplasms / Q000150:complications / Q000473:pathology* / Q000601:surgery; D011169:Portal Vein / Q000473:pathology* / Q000601:surgery; D014182:Transplantation, Autologous
Nuestra experiencia en el manejo de la cavernomatosis portal en el niño.