title: The cervical spine in the Klippel-Feil syndrome. A report of 57 cases.
abstract: We report 57 cases of the Klippel-Feil syndrome. Five had type I congenital cervical fusion, 48 type II and 4 type III. The symptoms and signs varied considerably. Patients with C2-C3 fusion often had symptoms associated with odontoid dysplasia and occipito-cervical instability. Twenty-one had progressive neurological symptoms and 19 were operated on: 3 had occiput-C3 posterior arthrodeses, 2 a single level fusion, 1 a laminectomy and anterior arthrodesis, and 13 had laminoplasties. Degenerative changes at the unfused segment and a narrow bony canal are high risk factors in the development of neurological compromise.
authors.affiliation: Department of Orthopaedic Surgery, Fukui Medical School, Japan.
authors.forename: H
authors.initials: H
authors.lastname: Baba
authors.forename: Y
authors.initials: Y
authors.lastname: Maezawa
authors.forename: N
authors.initials: N
authors.lastname: Furusawa
authors.forename: Q
authors.initials: Q
authors.lastname: Chen
authors.forename: S
authors.initials: S
authors.lastname: Imura
authors.forename: K
authors.initials: K
authors.lastname: Tomita
mesh_terms: D000293:Adolescent; D000328:Adult; D000368:Aged; D002574:Cervical Vertebrae / Q000473:pathology / Q000503:physiopathology* / Q000601:surgery; D002648:Child; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007593:Joint Instability / Q000000981:diagnostic imaging / Q000209:etiology; D007714:Klippel-Feil Syndrome / Q000473:pathology / Q000503:physiopathology* / Q000601:surgery; D008297:Male; D008875:Middle Aged; D009192:Myelography; D011379:Prognosis; D016059:Range of Motion, Articular; D013123:Spinal Fusion