Split notochord syndrome: case report.
Split notochord syndrome includes a cleft of the vertebral column associated with malformation of the central nervous system. Fourteen cases involving the lumbosacral spine have been reported in the literature. We report on a female neonate who had intact function of her lower extremities, a posterior midline lumbar defect bounded by two complete spinal canals that contained two spinal cords. A meningocele, a large bowel fistula, and a mature teratoma protruded through the cleft. The baby is doing well after repair of the anomaly and placement of a ventriculoperitoneal shunt.
Razack
N
N
Department of Neurological Surgery, University of Miami School of Medicine, Florida, USA.
Page
L K
LK
D001139:Arnold-Chiari Malformation / Q000473:pathology / Q000601:surgery; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007231:Infant, Newborn; D008159:Lumbar Vertebrae / Q000002:abnormalities / Q000473:pathology / Q000601:surgery; D008279:Magnetic Resonance Imaging; D008588:Meningocele / Q000175:diagnosis* / Q000473:pathology / Q000601:surgery; D009672:Notochord / Q000002:abnormalities* / Q000473:pathology / Q000601:surgery; D013125:Spinal Neoplasms / Q000473:pathology / Q000601:surgery; D013724:Teratoma / Q000473:pathology / Q000601:surgery; D017287:Ventriculoperitoneal Shunt