The cervical spine in the Klippel-Feil syndrome. A report of 57 cases.
We report 57 cases of the Klippel-Feil syndrome. Five had type I congenital cervical fusion, 48 type II and 4 type III. The symptoms and signs varied considerably. Patients with C2-C3 fusion often had symptoms associated with odontoid dysplasia and occipito-cervical instability. Twenty-one had progressive neurological symptoms and 19 were operated on: 3 had occiput-C3 posterior arthrodeses, 2 a single level fusion, 1 a laminectomy and anterior arthrodesis, and 13 had laminoplasties. Degenerative changes at the unfused segment and a narrow bony canal are high risk factors in the development of neurological compromise.
Baba
H
H
Department of Orthopaedic Surgery, Fukui Medical School, Japan.
Maezawa
Y
Y
Furusawa
N
N
Chen
Q
Q
Imura
S
S
Tomita
K
K
D000293:Adolescent; D000328:Adult; D000368:Aged; D002574:Cervical Vertebrae / Q000473:pathology / Q000503:physiopathology* / Q000601:surgery; D002648:Child; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007593:Joint Instability / Q000000981:diagnostic imaging / Q000209:etiology; D007714:Klippel-Feil Syndrome / Q000473:pathology / Q000503:physiopathology* / Q000601:surgery; D008297:Male; D008875:Middle Aged; D009192:Myelography; D011379:Prognosis; D016059:Range of Motion, Articular; D013123:Spinal Fusion