Desquamative interstitial pneumonia in sibs.
We report on 2 sibs with desquamative interstitial pneumonia. The female died at age 1 7/12 years despite use of prednisolone and methylprednisolone, while the male, now age 3 years. is alive with oxygen support. The occurrence of desquamative interstitial pneumonia in sibs born to normal parents suggests that in some cases the disease is an autosomal-recessive trait.
Tsukahara
M
M
Department of Pediatrics, Yamaguchi University School of Medicine, Ube, Japan.
Yoshii
H
H
Imamura
T
T
Kamei
T
T
Koga
M
M
Furukawa
S
S
D005260:Female; D006801:Humans; D007223:Infant; D017563:Lung Diseases, Interstitial / Q000235:genetics* / Q000473:pathology; D008297:Male; D009679:Nuclear Family