title: Multiple abdominal telangiectases and lymphangiectases. A limited form of Osler-Weber-Rendu disease?
abstract: We describe a 23-year-old man with protein-losing enteropathy, iron deficiency anemia, and recurrent gastrointestinal bleeding. The patient eventually developed disseminated intravascular coagulation, portal vein thrombosis, and extensive small bowel infarction. The autopsy showed multiple telangiectases in the intestines, mesentery, liver, gallbladder, renal pelves, and diaphragm. In addition, lymphangiectases were found in the retroperitoneal space, intestines, and liver. These lesions appeared to have been the cause of the gastrointestinal bleeding and the protein-losing enteropathy. The case most likely represents Osler-Weber-Rendu disease without the usual manifestations in the skin and oral-nasal cavities.
authors.affiliation: Institute of Gastroenterology, Tokyo Women's Medical College, Japan.
authors.forename: R
authors.initials: R
authors.lastname: Baba
authors.forename: E
authors.initials: E
authors.lastname: Hashimoto
authors.forename: K
authors.initials: K
authors.lastname: Yashiro
authors.forename: K
authors.initials: K
authors.lastname: Nagasako
authors.forename: N
authors.initials: N
authors.lastname: Hayashi
authors.forename: T
authors.initials: T
authors.lastname: Nishikawa
authors.forename: J
authors.initials: J
authors.lastname: Ludwig
mesh_terms: D000328:Adult; D017809:Fatal Outcome; D006801:Humans; D008201:Lymphangiectasis, Intestinal / Q000150:complications* / Q000473:pathology; D008297:Male; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000150:complications* / Q000473:pathology*