Fibrous dysplasia of the temporal bone: ten new cases demonstrating the spectrum of otologic sequelae.
monostotic. Although most patients had a conductive hearing loss, 17% of patients demonstrated profound sensorineural hearing loss ascribable to the lesion, and facial nerve sequelae were noted in nearly 10% of cases. Cholesteatoma complicated almost 40% of cases, usually in the form of a canal cholesteatoma. Ten new cases of temporal bone fibrous dysplasia are described not only to further clarify the spectrum of otologic sequelae but also to help illustrate available treatment options. In addition, this report documents, in three new cases, the previously undescribed progression of conductive hearing loss to profound sensorineural deafness secondary to fibrous dysplasia.
Megerian
C A
CA
Department of Otolaryngology, Massachusetts Eye and Ear Infirmary, Boston 02114, USA.
Sofferman
R A
RA
McKenna
M J
MJ
Eavey
R D
RD
Nadol
J B
JB
D000293:Adolescent; D000328:Adult; D002648:Child; D002675:Child, Preschool; D002781:Cholesteatoma / Q000209:etiology*; D004427:Ear Diseases / Q000209:etiology*; D005260:Female; D005357:Fibrous Dysplasia of Bone / Q000150:complications* / Q000175:diagnosis; D005358:Fibrous Dysplasia, Monostotic / Q000150:complications / Q000175:diagnosis; D005359:Fibrous Dysplasia, Polyostotic / Q000150:complications / Q000175:diagnosis; D005500:Follow-Up Studies; D006314:Hearing Loss, Conductive / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis / Q000209:etiology* / Q000601:surgery; D006801:Humans; D007223:Infant; D008297:Male; D008875:Middle Aged; D013701:Temporal Bone