title: Preoperative MRI diagnosis of Lhermitte-Duclos disease: case report with associated enlarged vessel and syrinx.
abstract: BACKGROUND
  The most common primary cerebellar tumor is hemangioblastoma, a lesion which is associated with magnetic resonance imaging (MR)-detectable vascularity in over 60%. Lhermitte-Duclos disease is an uncommon cause of a cerebellar mass that is not typically vascular.
  
  
  METHODS
  Computed tomography (CT), MRI with and without contrast, and magnetic resonance venography was performed in a patient with a cerebellar mass.
  
  
  RESULTS
  The cerebellar mass was noted to have a prominent vessel, as well as an associated syrinx. In spite of MRI-detectable vascularity, the striped appearance of the lesion was felt to be typical of Lhermitte-Duclos disease. At surgery, the mass was resected and the diagnosis of Lhermitte-Duclos disease was confirmed.
  
  
  CONCLUSIONS
  The diagnosis of Lhermitte-Duclos disease should be made when MRI shows a parallel linear "tiger-striped" lesion of the cerebellum. The presence of an enlarged vessel and/or syrinx should not deter one from making the preoperative diagnosis.
authors.affiliation: Department of Radiology, UMDNJ-New Jersey Medical School, Newark 070103, USA.
authors.forename: L J
authors.initials: LJ
authors.lastname: Wolansky
authors.forename: G P
authors.initials: GP
authors.lastname: Malantic
authors.forename: R
authors.initials: R
authors.lastname: Heary
authors.forename: A H
authors.initials: AH
authors.lastname: Maniker
authors.forename: H J
authors.initials: HJ
authors.lastname: Lee
authors.forename: L R
authors.initials: LR
authors.lastname: Sharer
authors.forename: U J
authors.initials: UJ
authors.lastname: Patel
mesh_terms: D000328:Adult; D002528:Cerebellar Neoplasms / Q000000981:diagnostic imaging / Q000473:pathology*; D002531:Cerebellum / Q000000981:diagnostic imaging / Q000473:pathology*; D005260:Female; D005729:Ganglioneuroma / Q000473:pathology; D006801:Humans; D008279:Magnetic Resonance Imaging; D013116:Spinal Cord / Q000473:pathology; D014057:Tomography, X-Ray Computed