Cystic adenomatoid malformation involving an entire lung in a 22-year-old woman.
Congenital cystic adenomatoid malformation is an uncommon cause of respiratory distress in infants and is a rare entity in adults. Presentation in older patients is that of recurrent pulmonary infections. Usually a single lobe is involved. This report describes congenital cystic adenomatoid malformation involving the entire right lung in a 22-year-old woman presenting with gastrointestinal bleeding due to cavernous transformation of the portal and splenic veins.
Lackner
R P
RP
Department of Surgery, University of Nebraska Medical Center, Omaha 68198-2315, USA.
Thompson
A B
AB
Rikkers
L F
LF
Galbraith
T A
TA
D000328:Adult; D015615:Cystic Adenomatoid Malformation of Lung, Congenital / Q000175:diagnosis* / Q000601:surgery; D004932:Esophageal and Gastric Varices / Q000175:diagnosis; D005260:Female; D006471:Gastrointestinal Hemorrhage / Q000175:diagnosis; D006801:Humans; D011013:Pneumonectomy; D011169:Portal Vein / Q000473:pathology; D013162:Splenic Vein / Q000473:pathology