-Aneurysm of the pulmonary artery and pulmonary artery hypertension 22 years after Mustard reversal operation in transposition of great vessels-.
An increasing number of patients with transposition of great arteries reaches adult age after an atrial redirection operation. The well known late sequelae of the Mustard and Senning operations include supraventricular brady-tachyarrhythmias, dilatation and failure of the systemic ventricle, severe tricuspid valve incompetence, obstruction of either the systemic or pulmonary venous return as well as left ventricular outflow tract obstruction, and baffle leaks. The case of a 26-year-old woman with a rarer postoperative course, namely severe aneurysmal dilatation of the pulmonary artery and pulmonary arterial hypertension 22 years after a Mustard operation is described. The pros and contras of the available therapeutic alternatives are discussed.
Wagdi
P
P
Inselspital Bern, Schweiz.
Leijala
M
M
D000328:Adult; D000783:Aneurysm / Q000209:etiology* / Q000503:physiopathology; D006328:Cardiac Catheterization; D005260:Female; D005500:Follow-Up Studies; D005541:Forced Expiratory Volume / Q000502:physiology; D006439:Hemodynamics / Q000502:physiology; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology* / Q000503:physiopathology; D011183:Postoperative Complications / Q000209:etiology* / Q000503:physiopathology; D011651:Pulmonary Artery / Q000503:physiopathology; D014188:Transposition of Great Vessels / Q000503:physiopathology / Q000601:surgery*
Aneurysma der Pulmonalarterie und pulmonalarterielle Hypertonie 22 Jahre nach Mustard-Umkehroperation bei Transposition der grossen Gefässe.