[Primary intestinal lymphangiectasis].
Primary intestinal lymphangiectasia (PIL), first described in 1961, is a rare disease of childhood. Oedema, hypoproteinaemia and diarrhoea are characteristic symptoms. Bioptic demonstration of dilated lymphatic capillary vessels in intestinal villi and increased intestinal protein loss are diagnostic. Two patients successfully treated with a low fat diet, containing medium chain triglycerides (MCT) are reported.
Andersen
U M
UM
Paediatrisk afdeling, Randers Centralsygehus.
Lund
H T
HT
D002648:Child; D005260:Female; D006801:Humans; D007223:Infant; D008201:Lymphangiectasis, Intestinal / Q000000981:diagnostic imaging / Q000178:diet therapy / Q000473:pathology; D008297:Male; D011859:Radiography
Primaer intestinal lymfangiektasi.