Esophageal leiomyomatosis.
OBJECTIVE
To reassess the clinical and radiologic findings in patients with esophageal leiomyomatosis.


METHODS
A search of the authors' radiologic archives revealed six cases of esophageal leiomyomatosis in a 22-year period. The clinical findings and radiologic images were reviewed retrospectively.


RESULTS
The average age of the patients was 10.8 years (range, 6-18 years). Five patients presented with slowly progressive dysphagia. Barium studies revealed smooth, tapered narrowing of the distal esophagus in five patients and characteristic defects on the superomedial aspect of the gastric fundus abutting the cardia, presumably due to bulging of this thickened mass of muscle into the stomach, in four patients. In two patients, computed tomography (CT) revealed marked thickening of the distal esophageal wall.


CONCLUSIONS
Esophageal leiomyomatosis can be suggested in a pediatric patient with long-standing dysphagia in whom smooth, tapered distal esophageal narrowing is seen at barium study and circumferential esophageal wall thickening is seen at CT.
Levine
M S
MS
Department of Radiology, Hospital of the University of Pennsylvania, Philadelphia, PA 19104, USA.
Buck
J L
JL
Pantongrag-Brown
L
L
Buetow
P C
PC
Lowry
M A
MA
Sobin
L H
LH
D000293:Adolescent; D001466:Barium Sulfate; D002648:Child; D003287:Contrast Media; D003680:Deglutition Disorders / Q000209:etiology; D004938:Esophageal Neoplasms / Q000150:complications / Q000000981:diagnostic imaging / Q000453:epidemiology / Q000473:pathology; D004947:Esophagus / Q000473:pathology; D005260:Female; D006801:Humans; D018231:Leiomyomatosis / Q000150:complications / Q000000981:diagnostic imaging / Q000453:epidemiology / Q000473:pathology; D008297:Male; D012189:Retrospective Studies; D014057:Tomography, X-Ray Computed
D003287:Contrast Media; D001466:Barium Sulfate