title: [A morphological study of ciliary abnormalities in patients with immotile cilia syndrome].
abstract: The present study has the aim of studying the morphological aspects of ciliary abnormalities in patients affected by immotile-dyskinetik cilia syndrome. Five patients affected by primary ciliary dyskinesia have been studied, examining by TEM the cells obtained by bronchial brushing during fiberoptic bronchoscopy. Many types of anomalies have been observed, and a morphologic classification was proposed. The frequency of abnormal cilia appears to be correlated to the severity of respiratory pathology. The morphological anomalies are not specific for this pathology.
authors.affiliation: Dipartimento di Anatomia Umana ed Istologia, Università di Firenze, Italia.
authors.forename: M
authors.initials: M
authors.lastname: Gulisano
authors.forename: L
authors.initials: L
authors.lastname: Canu
authors.forename: A
authors.initials: A
authors.lastname: Pacini
authors.forename: F
authors.initials: F
authors.lastname: Tanda
authors.forename: S
authors.initials: S
authors.lastname: Marceddu
authors.forename: P
authors.initials: P
authors.lastname: Pirina
authors.forename: P
authors.initials: P
authors.lastname: Pacini
mesh_terms: D000328:Adult; D001980:Bronchi / Q000473:pathology*; D001999:Bronchoscopy; D002923:Cilia / Q000473:pathology*; D002925:Ciliary Motility Disorders / Q000473:pathology*; D003593:Cytoplasm / Q000473:pathology; D005260:Female; D005336:Fiber Optic Technology; D006801:Humans; D008297:Male; D008854:Microscopy, Electron
vernacular_title: Studio morfologico delle anomalie ciliari in pazienti affetti da sindrome delle ciglia immobili.