[An unusual association: Jaffe-Linchtenstein syndrome, arcuate ligament syndrome and hepatic adenoma].
A case of a woman affected by an unusual association of rare diseases, is presented. The patient was referred to our department for acute anaemia. Preoperative investigations revealed that the patient was affected by fibrous polyostotic dysplasia, so called Jaffè-Lichtenstein syndrome. The presence of skin brown spot and endocrine disorders requiring pill administration, allows to classify the patient as carrier of Albright syndrome. Moreover, the angiography pointed out a celiac trunc stenosis (Dunbar syndrome). The long-standing administration of the pill could be the cause of bleeding adenoma. The patient underwent hepatic resection. We did not treat the Dunbar syndrome because of poor symptoms. From literature, we review some opinions on the fibrous dysplasia of the bone.
Fontana
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Divisione di Chirurgia B, Ospedale G. Bosco, Torino.
Leli
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R
Della Beffa
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D000236:Adenoma / Q000150:complications / Q000473:pathology* / Q000601:surgery; D000328:Adult; D005260:Female; D005359:Fibrous Dysplasia, Polyostotic / Q000150:complications / Q000175:diagnosis*; D006470:Hemorrhage / Q000150:complications; D006801:Humans; D008099:Liver / Q000473:pathology* / Q000601:surgery; D008113:Liver Neoplasms / Q000150:complications / Q000473:pathology* / Q000601:surgery; D013577:Syndrome
Una insolita associazione: sindrome di Jaffè-Linchtenstein, sindrome del legamento arcuato e adenoma epatico.