Malignant occipital astrocytoma in a patient with Lhermitte-Duclos disease (cerebellar dysplastic gangliocytoma).
A case of Lhermitte-Duclos disease (dysplastic gangliocytoma of the cerebellum) is described. Seventeen years after the diagnosis was made, the patient developed a malignant astrocytoma of the cerebrum, an association only once previously reported. The clinical presentation and radiological features are presented.
Domingo
Z
Z
Department of Neurosurgery, Groote Schuur Hospital, University of Cape Town, South Africa.
Fisher-Jeffes
N D
ND
de Villiers
J C
JC
D000328:Adult; D001254:Astrocytoma / Q000150:complications* / Q000175:diagnosis / Q000473:pathology*; D001932:Brain Neoplasms / Q000150:complications / Q000175:diagnosis* / Q000473:pathology*; D002528:Cerebellar Neoplasms / Q000150:complications* / Q000473:pathology*; D002531:Cerebellum / Q000473:pathology*; D003922:Diabetes Mellitus, Type 1 / Q000150:complications; D005260:Female; D005729:Ganglioneuroma / Q000150:complications* / Q000473:pathology; D006801:Humans; D008279:Magnetic Resonance Imaging; D009778:Occipital Lobe / Q000473:pathology*; D014057:Tomography, X-Ray Computed