Scalp dermatitis, ectodermal dysplasia and cleft lip and palate: rapp-hodgkin or AEC syndrome.
A female infant with ectodermal dysplasia, bilateral cleft lip and palate and a recalcitrant scalp dermatitis is presented. She had features of both Rapp-Hodgkin syndrome and AEC syndrome. It has recently been suggested in the literature that these two syndrome are the same condition and this case report supports this viewpoint.
Rowan
D M
DM
Dermatology Clinic, Middlemore Hospital, Otahuhu, Auckland, New Zealand.
D000505:Alopecia / Q000382:microbiology / Q000473:pathology; D002971:Cleft Lip / Q000473:pathology*; D002972:Cleft Palate / Q000473:pathology*; D004476:Ectodermal Dysplasia / Q000473:pathology*; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D012536:Scalp Dermatoses / Q000382:microbiology / Q000473:pathology*; D013207:Staphylococcal Skin Infections / Q000473:pathology; D013577:Syndrome