title: [Frontal lobe-type dementia associated with motor neuron disease].
abstract: A case of presenile dementia with dominant frontal disfunction, progressive aphasia and Motor Neuron Disease with prominent bulbar signs is reported. Considering the clinical examination, the measurements of the regional cerebral flow (SPECT) and the histological appearances, we suggest the diagnosis of Dementia of Frontal Lobe Type and Motor Neuron Disease. We reviewed other disorders labelled Primary Frontal or Fronto-temporal Dementias and we discuss this new dementia and the difficulty in its classification.
authors.affiliation: Servico de Neurologia, Hospitais da Universidade de Coimbra.
authors.forename: I
authors.initials: I
authors.lastname: Santana
authors.forename: M C
authors.initials: MC
authors.lastname: Macario
authors.forename: O
authors.initials: O
authors.lastname: Rebelo
authors.forename: M M
authors.initials: MM
authors.lastname: Pires
mesh_terms: D001706:Biopsy; D001921:Brain / Q000000981:diagnostic imaging / Q000473:pathology; D003704:Dementia / Q000175:diagnosis* / Q000473:pathology; D003937:Diagnosis, Differential; D005260:Female; D005625:Frontal Lobe / Q000473:pathology; D006801:Humans; D008279:Magnetic Resonance Imaging; D008875:Middle Aged; D016472:Motor Neuron Disease / Q000175:diagnosis* / Q000473:pathology; D009483:Neuropsychological Tests; D015899:Tomography, Emission-Computed, Single-Photon; D014057:Tomography, X-Ray Computed
vernacular_title: Demencia do tipo frontal associada a doenca do neuronio motor.