Von Hippel-Lindau disease complicated by acute pancreatitis and Evan's syndrome.
Von Hippel-Lindau syndrome (VHL) is an autosomal dominant disorder characterized by renal cysts, retinal angiomas, central nervous system hemangioblastomas, and pancreatic cysts. Evan's syndrome is a hematologic disorder characterized by autoimmune thrombocytopenia and autoimmune hemolytic anemia. We present the first case of acute pancreatitis and Evan's syndrome that developed in a patient with von Hippel-Lindau syndrome.
Tenner
S
S
Center for Pancreatic Disease, Brigham and Women's Hospital, Harvard Medical School, Boston, MA 02115, USA.
Roston
A
A
Lichtenstein
D
D
Sica
G
G
Carr-Locke
D
D
Banks
P A
PA
D000208:Acute Disease; D000328:Adult; D000744:Anemia, Hemolytic, Autoimmune / Q000209:etiology*; D006801:Humans; D008297:Male; D010195:Pancreatitis / Q000209:etiology*; D013577:Syndrome; D013921:Thrombocytopenia / Q000209:etiology*; D006623:von Hippel-Lindau Disease / Q000150:complications*