A clinical case of neuro-Behçet syndrome without mucocutaneo-ocular symptoms: relationship with brain stem encephalitis.
The case of a 50 year old man with personality changes, dementia, and brain stem symptoms is presented. Magnetic resonance imaging (MRI) disclosed high signal areas mainly in the brain stem. Both a positive skin prick test and an HLA-B51 were demonstrated. These clinical findings were suggestive of neuro-Behçet syndrome, although there were no mucocutaneo-ocular symptoms characteristically associated with this disease. The relationship between neuro-Behçet syndrome and brain stem encephalitis, including a discrimination from multiple sclerosis, is discussed.
Kawanishi
Y
Y
Psychiatric Service, University of Tsukuba Hospital, Ibaraki, Japan.
Hori
T
T
Suzuki
T
T
Mizukami
K
K
Sasaki
M
M
Shiraishi
H
H
D001528:Behcet Syndrome / Q000175:diagnosis* / Q000523:psychology; D001933:Brain Stem / Q000473:pathology; D003704:Dementia / Q000175:diagnosis / Q000523:psychology; D003937:Diagnosis, Differential; D004660:Encephalitis / Q000175:diagnosis* / Q000523:psychology; D015235:HLA-B Antigens / Q000032:analysis; D059949:HLA-B51 Antigen; D006801:Humans; D007428:Intradermal Tests; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D009103:Multiple Sclerosis / Q000175:diagnosis / Q000523:psychology; D019965:Neurocognitive Disorders / Q000175:diagnosis* / Q000523:psychology
D015235:HLA-B Antigens; D059949:HLA-B51 Antigen