[Hiramaya disease: disease or syndrome?].
Hirayama's disease, a benign juvenile amyotrophy of "oblique" topography of an upper limb, has been acknowledged in the international literature. 4 cases are reported in this paper. However there present some differences: presence of antigangliosides antibodies in 1 case, cryoglobulinemia in another case developing bilaterally, conduction blocks in a third case. Finally, in the patient illustrating the typical form, the neuroradiological abnormalities considered as characteristic of cervical spine compression by Hirayama are lacking.
Billé-Turc
F
F
Service de Neurologie, Hôpital St Joseph, Marseille.
Billé
J
J
Azulay
J P
JP
Padovani
R
R
Serratrice
G
G
D000293:Adolescent; D000328:Adult; D005260:Female; D005542:Forearm; D006801:Humans; D008297:Male; D009134:Muscular Atrophy, Spinal / Q000150:complications / Q000175:diagnosis*; D013577:Syndrome; D009626:Terminology as Topic
La maladie d'Hirayama, maladie ou syndrome?