Cystic lung disease in systemic sclerosis: a case report with high resolution computed tomography findings.
A 31-year old black female presented with limited scleroderma. Although she had no chest symptoms, chest radiographs showed a basal reticular pattern with large cysts in both lung fields. High resolution computed tomography revealed almost complete effacement of normal lung architecture by multiple large cysts, honeycombing and interstitial fibrosis. Cystic lung disease is an uncommon manifestation of interstitial lung disease in systemic sclerosis, and its natural history needs to be better defined.
Bergemann
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A
Department of Medicine, Baragwanath Hospital, Johannesburg, South Africa.
Tikly
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M
D000328:Adult; D018501:Antirheumatic Agents / Q000627:therapeutic use; D003560:Cysts / Q000150:complications* / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D008171:Lung Diseases / Q000150:complications* / Q000000981:diagnostic imaging; D009543:Nifedipine / Q000627:therapeutic use; D010396:Penicillamine / Q000627:therapeutic use; D011658:Pulmonary Fibrosis / Q000150:complications* / Q000000981:diagnostic imaging; D012595:Scleroderma, Systemic / Q000150:complications* / Q000175:diagnosis / Q000188:drug therapy; D014057:Tomography, X-Ray Computed
D018501:Antirheumatic Agents; D010396:Penicillamine; D009543:Nifedipine