[Longitudinal psychological study in myotonic dystrophy].
The authors studied in two occasions a group of 12 patients with myotonic dystrophy in a mean interval of three years and a half between the examinations. The neuro-psychological battery included the following tests: Raven's progressive matrices (coloured and general scales), Wechsler children intelligence scale (WISC), Kohs' blocks and Piaget-Head. 50% of the patients had better scores on the second examination on RCPM, 81.89% on WISC-digit span, 63.67% on WISC-numbers, 44.44% on Piaget-Head 2 and 60% on Kohs' blocks. However, on Piaget-Head 1-3, the majority had worse results (87.56%) with statistical significative difference (p < 0.05). Though the scores from Kohs' blocks were better in 60% of the patients with p < 0.05, we have to consider that 60% had 0 point on first examination being their scores a little better on second one. This is enough to result on statistical significative difference, however, very low if compared to normal subjects.
Wigg
C M
CM
Instituto de Neurologia Deolindo Couto, Universidade Federal do Rio de Janeiro, Brasil.
Duro
L A
LA
D000293:Adolescent; D000328:Adult; D002648:Child; D004594:Electrophysiology; D005260:Female; D006801:Humans; D008137:Longitudinal Studies; D008297:Male; D008875:Middle Aged; D009223:Myotonic Dystrophy / Q000503:physiopathology / Q000523:psychology*; D011581:Psychological Tests; D011594:Psychometrics
Estudo psicológico longitudinal na distrofia miotônica.