Decreased activity of the mitochondrial ATP-synthase in fibroblasts from children with late-infantile and juvenile neuronal ceroid lipofuscinosis.
Das
A M
AM
Department of Pediatrics, Hannover Medical School, Germany.
Kohlschütter
A
A
D000293:Adolescent; D002648:Child; D002675:Child, Preschool; D005347:Fibroblasts / Q000648:ultrastructure*; D006801:Humans; D007223:Infant; D007231:Infant, Newborn; D008928:Mitochondria / Q000201:enzymology*; D009472:Neuronal Ceroid-Lipofuscinoses / Q000201:enzymology*; D006180:Proton-Translocating ATPases / Q000378:metabolism*
D006180:Proton-Translocating ATPases