Crowned dens syndrome: a manifestation of hydroxy-apatite rheumatism.
Crowned dens syndrome is defined as an association of acute cervical pain and calcifications in the peri-odontoid space. The authors report one case of this rare localization of hydroxy-apatite rheumatism and review 12 similar cases in the literature. This disease affects only adult females. Patients present with inflammatory signs, can be treated with non-steroid anti-inflammatory drugs and recover without sequela. Calcium pyrophosphate dihydrate deposition can also lead to this syndrome. Other perioodontoid calcifications and ossifications, usually asymptomatic, appear only as a radiologically crowned dens.
Malca
S A
SA
Department of Neurosurgery, Hôpital Sainte Marguerite, Marseille, France.
Roche
P H
PH
Pellet
W
W
Combalbert
A
A
D000894:Anti-Inflammatory Agents, Non-Steroidal / Q000627:therapeutic use; D001172:Arthritis, Rheumatoid / Q000175:diagnosis* / Q000188:drug therapy; D017886:Durapatite; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D008875:Middle Aged; D009288:Naproxen / Q000627:therapeutic use; D009809:Odontoid Process / Q000473:pathology*; D014057:Tomography, X-Ray Computed
D000894:Anti-Inflammatory Agents, Non-Steroidal; D009288:Naproxen; D017886:Durapatite