title: Management of ectopia lentis in a family with Marfan syndrome.
abstract: OBJECTIVE
  To determine the effectiveness of combined pars plana vitrectomy-lensectomy and open-loop anterior chamber lens implantation for the management of ectopia lentis associated with Marfan syndrome.
  
  
  METHODS
  Retrospective review of the medical records of 4 consecutive patients with Marfan syndrome who underwent combined pars plana lensectomy-vitrectomy and anterior chamber lens implantation at our institution between August 1994 and July 1995.
  
  
  RESULTS
  All patients demonstrated postoperative visual acuity of 20/25 or better during an average follow-up period of 6 months (range, 4-9 months). Two patients developed pseudophakic pupillary block and required YAG laser iridotomy postoperatively.
  
  
  CONCLUSIONS
  Pars plana lensectomy-vitrectomy and anterior chamber intraocular lens implantation appears to be an excellent technique for the management of ectopia lentis associated with Marfan syndrome. A bimanual, closed-system endosurgical technique avoids many of the complications previously associated with surgery for ectopia lentis.
authors.affiliation: Department of Ophthalmology, Eye Institute, Medical College of Wisconsin, Milwaukee.
authors.forename: S B
authors.initials: SB
authors.lastname: Koenig
authors.forename: W F
authors.initials: WF
authors.lastname: Mieler
mesh_terms: D000328:Adult; D000867:Anterior Chamber / Q000601:surgery; D004479:Ectopia Lentis / Q000209:etiology / Q000601:surgery*; D005192:Family Health; D006801:Humans; D007908:Lens, Crystalline / Q000601:surgery; D007910:Lenses, Intraocular; D008297:Male; D008382:Marfan Syndrome / Q000150:complications*; D008875:Middle Aged; D011183:Postoperative Complications; D012189:Retrospective Studies; D014792:Visual Acuity; D014821:Vitrectomy