Systemic sclerosis associated with right ventricular cardiomyopathy.
Systemic sclerosis is an uncommon multisystem disorder of unknown aetiology which predominantly affects the skin. Cardiac involvement, which is far more common than was originally realized, may affect any part of the heart but most frequently affects the left ventricular myocardium. Right ventricular dysfunction is usually associated with pulmonary vascular disease. We report a case of systemic sclerosis associated with right ventricular cardiomyopathy in whom pulmonary artery pressures were normal.
Bewley
A P
AP
Department of Dermatology, University College London Medical School, U.K.
Cooper
J P
JP
Levell
N J
NJ
Walker
J M
JM
Dowd
P M
PM
D000328:Adult; D002311:Cardiomyopathy, Dilated / Q000209:etiology*; D019066:Facies; D005260:Female; D006801:Humans; D012595:Scleroderma, Systemic / Q000150:complications* / Q000473:pathology; D018497:Ventricular Dysfunction, Right / Q000209:etiology*