Management of ectopia lentis in a family with Marfan syndrome.
OBJECTIVE
To determine the effectiveness of combined pars plana vitrectomy-lensectomy and open-loop anterior chamber lens implantation for the management of ectopia lentis associated with Marfan syndrome.


METHODS
Retrospective review of the medical records of 4 consecutive patients with Marfan syndrome who underwent combined pars plana lensectomy-vitrectomy and anterior chamber lens implantation at our institution between August 1994 and July 1995.


RESULTS
All patients demonstrated postoperative visual acuity of 20/25 or better during an average follow-up period of 6 months (range, 4-9 months). Two patients developed pseudophakic pupillary block and required YAG laser iridotomy postoperatively.


CONCLUSIONS
Pars plana lensectomy-vitrectomy and anterior chamber intraocular lens implantation appears to be an excellent technique for the management of ectopia lentis associated with Marfan syndrome. A bimanual, closed-system endosurgical technique avoids many of the complications previously associated with surgery for ectopia lentis.
Koenig
S B
SB
Department of Ophthalmology, Eye Institute, Medical College of Wisconsin, Milwaukee.
Mieler
W F
WF
D000328:Adult; D000867:Anterior Chamber / Q000601:surgery; D004479:Ectopia Lentis / Q000209:etiology / Q000601:surgery*; D005192:Family Health; D006801:Humans; D007908:Lens, Crystalline / Q000601:surgery; D007910:Lenses, Intraocular; D008297:Male; D008382:Marfan Syndrome / Q000150:complications*; D008875:Middle Aged; D011183:Postoperative Complications; D012189:Retrospective Studies; D014792:Visual Acuity; D014821:Vitrectomy