title: Omenn's reticulosis associated with the nephrotic syndrome.
abstract: Omenn's reticulosis is an inherited severe combined immunodeficiency characterized by neonatal exfoliative erythroderma. A newborn baby who had minimal change nephrotic syndrome and Omenn's reticulosis is reported. Abnormalities in lymphocyte function could explain both the nephropathy and the cutaneous changes.
authors.affiliation: Service de Dermatologie, Hôpital Saint-Louis, Paris, France.
authors.forename: M
authors.initials: M
authors.lastname: Rybojad
authors.forename: S
authors.initials: S
authors.lastname: Cambiaghi
authors.forename: I
authors.initials: I
authors.lastname: Moraillon
authors.forename: M D
authors.initials: MD
authors.lastname: Vignon-Pennmen
authors.forename: P
authors.initials: P
authors.lastname: Morel
authors.forename: V
authors.initials: V
authors.lastname: Baudoin
authors.forename: C
authors.initials: C
authors.lastname: Loirat
mesh_terms: D003873:Dermatitis, Exfoliative / Q000150:complications; D006801:Humans; D007231:Infant, Newborn; D008206:Lymphatic Diseases / Q000150:complications* / Q000473:pathology; D008297:Male; D009404:Nephrotic Syndrome / Q000150:complications*; D016511:Severe Combined Immunodeficiency / Q000150:complications*; D012878:Skin Neoplasms / Q000150:complications* / Q000473:pathology