title: Desmoplastic supratentorial neuroepithelial tumours of childhood: imaging in 5 patients.
abstract: Desmoplastic neuroepithelial tumours are rare supratentorial neoplasms of infancy with a favourable prognosis. We characterised their imaging findings by reviewing the clinical and radiological reports of five affected children. The tumours were massive, predominantly cystic and with preferential frontal and parietal lobe involvement. The cystic component was in the white matter, with no communication with the ventricle. The solid part was superficially, abutting a meningeal surface, and showed intense contrast enhancement. A heterogeneous predominantly solid mass was observed in one patient. Thinning and deformation of the skull adjacent to the tumour was shown in four cases. Peritumoral oedema was absent or moderate. No calcification or haemorrhage were present. Angiography showed a tumour blush from the internal or external carotid arteries in one case each. Follow-up (3 months-9 years, mean 4.5 years) showed no recurrence.
authors.affiliation: Department of Radiology, Hôpital des Enfants Malades, Paris, France.
authors.forename: F
authors.initials: F
authors.lastname: Rypens
authors.forename: M J
authors.initials: MJ
authors.lastname: Esteban
authors.forename: A
authors.initials: A
authors.lastname: Lellouch-Tubiana
authors.forename: C
authors.initials: C
authors.lastname: Bastien-Fagnou
authors.forename: D
authors.initials: D
authors.lastname: Renier
authors.forename: J
authors.initials: J
authors.lastname: Baraton
authors.forename: F
authors.initials: F
authors.lastname: Brunelle
mesh_terms: D000792:Angiography; D002675:Child, Preschool; D005260:Female; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D018302:Neoplasms, Neuroepithelial / Q000175:diagnosis* / Q000601:surgery; D015173:Supratentorial Neoplasms / Q000175:diagnosis* / Q000601:surgery; D014057:Tomography, X-Ray Computed