[Malignant bilateral pheochromocytoma and von Recklinghausen disease].
OBJECTIVE
To review the main features of malignant pheochromocytoma and its relationship to von Recklinghausen's neurofibromatosis.


RESULTS
We report on a case of malignant bilateral pheochromocytoma with hepatic and pulmonary metastasis, associated with von Recklinghausen's neurofibromatosis. Surgery achieved good results and the patient is well seven years postoperatively.


CONCLUSIONS
Approximately 10% of the pheochromocytomas are malignant and treatment is principally by surgery. (131) metaiodobenzylguanidine may be useful in cases with metastasis, residual tumor or local relapse.
Martín Huéscar
A
A
Servicio de Urología, Hospital Covadonga, Oviedo, Asturias, España.
Fernández Gómez
J M
JM
Martínez Gómez
F J
FJ
Regadera Sejas
F J
FJ
Sahagun Argùello
J L
JL
Rabade Rey
C J
CJ
D000310:Adrenal Gland Neoplasms / Q000150:complications* / Q000473:pathology; D000328:Adult; D006801:Humans; D008113:Liver Neoplasms / Q000556:secondary; D008175:Lung Neoplasms / Q000556:secondary; D008297:Male; D009456:Neurofibromatosis 1 / Q000150:complications*; D010673:Pheochromocytoma / Q000150:complications* / Q000473:pathology / Q000556:secondary