title: Dabska tumor developing within a preexisting vascular malformation.
abstract: Malignant endovascular papillary angioendothelioma, first described by Dabska in 1969, is a rare vascular tumor that primarily affects children and is characterized by papillary proliferations of endothelial cells into vessel lumens. We report a case of this rare neoplasm in a boy with angiomatosis who developed Kasabach-Merritt syndrome. The tumor evolved as an ulcerated lesion superficially within a previous vascular malformation on his buttock. A review of the literature is presented.
authors.affiliation: Department of Dermatology, Hospital General Universitario, Valencia, Spain.
authors.forename: E
authors.initials: E
authors.lastname: Quecedo
authors.forename: J A
authors.initials: JA
authors.lastname: Martínez-Escribano
authors.forename: I
authors.initials: I
authors.lastname: Febrer
authors.forename: V
authors.initials: V
authors.lastname: Oliver
authors.forename: M
authors.initials: M
authors.lastname: Velasco
authors.forename: A
authors.initials: A
authors.lastname: Aliaga
mesh_terms: D000293:Adolescent; D000740:Anemia / Q000473:pathology; D000798:Angiomatosis / Q000473:pathology*; D001165:Arteriovenous Malformations / Q000473:pathology; D002081:Buttocks; D004211:Disseminated Intravascular Coagulation / Q000473:pathology; D004730:Endothelium, Vascular / Q000473:pathology; D006390:Hemangioendothelioma / Q000473:pathology*; D006801:Humans; D008297:Male; D017445:Skin Diseases, Vascular / Q000473:pathology*; D012878:Skin Neoplasms / Q000473:pathology*; D012883:Skin Ulcer / Q000473:pathology; D013577:Syndrome; D013921:Thrombocytopenia / Q000473:pathology