title: Successful staged surgical correction of congenital segmental spinal dysgenesis and complete rotary subluxation of the thoracolumbar spine in an infant.
abstract: Congenital segmental spinal dysgenesis is a rare lesion that usually is associated with neurological deficits. Affected infants who are neurologically intact may suffer progressive kyphosis and subsequent neurological deterioration. Results of external casting, laminectomy with spinal fixation, or bone grafting of the defect have been disappointing. The authors present a successful staged surgical management scheme consisting of complete resection of the dysraphic vertebral bodies, maintenance of normal vertebral distance with rib strut grafting, and fusion with autogenous bone.
authors.affiliation: Department of General Surgery, Scott & White Clinic and Memorial Hospital, Temple, Texas, USA.
authors.forename: E G
authors.initials: EG
authors.lastname: Ford
authors.forename: B A
authors.initials: BA
authors.lastname: Jaufmann
authors.forename: S C
authors.initials: SC
authors.lastname: Kaste
authors.forename: L J
authors.initials: LJ
authors.lastname: Foody
authors.forename: T E
authors.initials: TE
authors.lastname: Kuivila
mesh_terms: D016025:Bone Transplantation; D002370:Casts, Surgical; D005260:Female; D006801:Humans; D007231:Infant, Newborn; D007738:Kyphosis / Q000209:etiology; D008159:Lumbar Vertebrae / Q000002:abnormalities* / Q000601:surgery; D012272:Ribs; D016135:Spinal Dysraphism / Q000601:surgery*; D013123:Spinal Fusion; D013168:Spondylolisthesis / Q000151:congenital* / Q000601:surgery; D013904:Thoracic Vertebrae / Q000002:abnormalities* / Q000601:surgery; D014182:Transplantation, Autologous