Superficial siderosis of the central nervous system.
Two patients with superficial siderosis of the central nervous system are reported. Both developed progressive deafness over many years; one with associated anosmia and partial seizures; the other with progressive ataxia and diplopia. The cerebrospinal fluid was xanthochromic in one and the protein was raised in both. Magnetic resonance imaging revealed a hypodense rim around the eighth cranial nerve, cerebellum, brain stem and spinal cord. Despite extensive investigations the cause of the superficial siderosis in both patients remains undetermined.
O'Riordan
J I
JI
Department of Neurology, Adelaide Hospital, Dublin.
Javed
M
M
McShane
D
D
Hutchinson
M
M
Murphy
R
R
D000328:Adult; D002490:Central Nervous System / Q000473:pathology; D002493:Central Nervous System Diseases / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology; D005260:Female; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis / Q000209:etiology*; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D008875:Middle Aged; D012806:Siderosis / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology