title: [A patient with Cornelia de Lange syndrome with difficulty in orotracheal intubation].
abstract: We experienced a difficult orotracheal intubation in a patient with Cornelia de Lange syndrome. The patient was an eight-year-old girl with Cornelia de Lange syndrome, cleft palate and tetralogy of Fallot who underwent emergency hemicolectomy for strangulation ileus. Orotracheal intubation using a Macintosh laryngoscope was unsuccessful. However, intubation using an endotracheal tube through the laryngeal mask airway with a fiberoptic bronchoscope was successful. The patient's condition was stable during both intubation and operation. In conclusion, we must be careful on endotracheal intubation of patients with congenital anomalies.
authors.affiliation: Department of Anesthesiology, Tokyo Women's Medical College, Daini Hospital.
authors.forename: Y
authors.initials: Y
authors.lastname: Tsukazaki
authors.forename: C
authors.initials: C
authors.lastname: Tachibana
authors.forename: K
authors.initials: K
authors.lastname: Satoh
authors.forename: T
authors.initials: T
authors.lastname: Fukada
authors.forename: Y
authors.initials: Y
authors.lastname: Ohe
mesh_terms: D000768:Anesthesia, General; D001999:Bronchoscopy; D002648:Child; D003082:Colectomy; D003635:De Lange Syndrome / Q000150:complications; D005260:Female; D005336:Fiber Optic Technology; D006801:Humans; D007415:Intestinal Obstruction / Q000150:complications / Q000601:surgery; D007442:Intubation, Intratracheal / Q000379:methods*; D017214:Laryngeal Masks