title: Warm heart operation in a patient with myotonic dystrophy.
abstract: Myotonic dystrophy is the most severe form of myotonic disorder. Hypothermia or hyperkalemia may cause generalized muscle contraction during heart operations. We successfully repaired an atrial septal defect and pulmonary stenosis in a patient with myotonic dystrophy using systemic normothermia with continuous normokalemic coronary perfusion. This is the second reported case of a patient with myotonic dystrophy who underwent a cardiac operation.
authors.affiliation: Department of Cardiovascular Surgery, Tenri Hospital, Nara, Japan.
authors.forename: T
authors.initials: T
authors.lastname: Sakai
authors.forename: S
authors.initials: S
authors.lastname: Miki
authors.forename: Y
authors.initials: Y
authors.lastname: Ueda
authors.forename: T
authors.initials: T
authors.lastname: Nomoto
authors.forename: S
authors.initials: S
authors.lastname: Hashimoto
authors.forename: K
authors.initials: K
authors.lastname: Takahashi
mesh_terms: D000328:Adult; D006348:Cardiac Surgical Procedures / Q000379:methods*; D002315:Cardiopulmonary Bypass / Q000379:methods; D005260:Female; D006344:Heart Septal Defects, Atrial / Q000150:complications / Q000601:surgery; D006801:Humans; D009223:Myotonic Dystrophy / Q000150:complications; D011666:Pulmonary Valve Stenosis / Q000150:complications / Q000601:surgery