Progressive encephalomyelitis with rigidity responsive to plasmapheresis and immunosuppression.
The stiff-man syndrome is reported in a 55-year-old woman who also had signs of severe bulbar musculature hypercontraction. These clinical features correspond to the progressive encephalomyelitis with rigidity syndrome. Diazepam was minimally beneficial, but after treatment with plasmapheresis and corticosteroids, she was still asymptomatic when seen 5 years later.
Fogan
L
L
Department of Neurology, Kaiser Permanente Medical Center, Panorama City, CA 94102-5497, USA.
D000305:Adrenal Cortex Hormones / Q000627:therapeutic use; D018450:Disease Progression; D004679:Encephalomyelitis / Q000150:complications* / Q000503:physiopathology / Q000628:therapy*; D005260:Female; D006801:Humans; D007165:Immunosuppression Therapy; D008875:Middle Aged; D009127:Muscle Rigidity / Q000209:etiology*; D010956:Plasmapheresis
D000305:Adrenal Cortex Hormones