Dabska tumor developing within a preexisting vascular malformation.
Malignant endovascular papillary angioendothelioma, first described by Dabska in 1969, is a rare vascular tumor that primarily affects children and is characterized by papillary proliferations of endothelial cells into vessel lumens. We report a case of this rare neoplasm in a boy with angiomatosis who developed Kasabach-Merritt syndrome. The tumor evolved as an ulcerated lesion superficially within a previous vascular malformation on his buttock. A review of the literature is presented.
Quecedo
E
E
Department of Dermatology, Hospital General Universitario, Valencia, Spain.
Martínez-Escribano
J A
JA
Febrer
I
I
Oliver
V
V
Velasco
M
M
Aliaga
A
A
D000293:Adolescent; D000740:Anemia / Q000473:pathology; D000798:Angiomatosis / Q000473:pathology*; D001165:Arteriovenous Malformations / Q000473:pathology; D002081:Buttocks; D004211:Disseminated Intravascular Coagulation / Q000473:pathology; D004730:Endothelium, Vascular / Q000473:pathology; D006390:Hemangioendothelioma / Q000473:pathology*; D006801:Humans; D008297:Male; D017445:Skin Diseases, Vascular / Q000473:pathology*; D012878:Skin Neoplasms / Q000473:pathology*; D012883:Skin Ulcer / Q000473:pathology; D013577:Syndrome; D013921:Thrombocytopenia / Q000473:pathology