title: Mondini dysplasia with recurrent meningitis.
abstract: Mondini dysplasia is a congenital malformation of the inner ear, commonly associated with hearing impairment, cerebrospinal fluid otorrhea/rhinorrhea and recurrent meningitis. Two such cases are described, with hearing impairment, cerebrospinal fluid rhinorrhea, and several episodes of meningitis. Diagnosis was confirmed by high-resolution computed tomography. After surgical correction of the malformation, there was no recurrent episode of meningitis at subsequent follow-up. To avoid the suffering and the sequelae of recurrent meningitis, an early diagnosis and prompt surgical intervention are crucial for such patients.
authors.affiliation: Department of Pediatrics, National Taiwan University Hospital, Taipei, R.O.C.
authors.forename: M Y
authors.initials: MY
authors.lastname: Lu
authors.forename: P I
authors.initials: PI
authors.lastname: Lee
authors.forename: C Y
authors.initials: CY
authors.lastname: Lee
authors.forename: C J
authors.initials: CJ
authors.lastname: Hsu
mesh_terms: D002648:Child; D002675:Child, Preschool; D004427:Ear Diseases / Q000150:complications* / Q000000981:diagnostic imaging / Q000601:surgery; D007758:Ear, Inner / Q000002:abnormalities* / Q000473:pathology; D016057:Evoked Potentials, Auditory, Brain Stem; D005260:Female; D005402:Fistula / Q000150:complications* / Q000601:surgery; D006319:Hearing Loss, Sensorineural / Q000175:diagnosis / Q000209:etiology; D006801:Humans; D008581:Meningitis / Q000209:etiology*; D013577:Syndrome; D014057:Tomography, X-Ray Computed