[A case of ectopic familial pheochromocytoma].
This is a report of the occurrence of familial ectopic pheochromocytoma in two brothers, whose father had bilateral adrenal pheochromocytoma. Both brother complained of hypertension. In the first case, a 22-year-old man presented with much higher than normal norepinephrine. Abdominal CT and chest CT scanning and 123I-MIBG scintigraphy revealed an extraadrenal tumor in the chest on the bilateral adrenal grands. Bilateral adrenectomy was performed. In the second case, the 20-year-old brother was found to have an abdominal mass that was diagnosed as ectopic pheochromocytoma originating in the intra-abdominal paraaorta according to abdominal CT scanning and 131I-MIBG scintigraphy. The tumor was resected.
Nakada
J
J
Department of Urology, Jikei University School of Medicine.
Oishi
Y
Y
Onodera
S
S
Igarashi
H
H
Nishida
A
A
Kinoshita
T
T
Mochizuki
S
S
D000008:Abdominal Neoplasms / Q000175:diagnosis / Q000235:genetics* / Q000601:surgery; D000310:Adrenal Gland Neoplasms / Q000175:diagnosis / Q000235:genetics* / Q000601:surgery; D000315:Adrenalectomy; D000328:Adult; D001012:Aorta, Abdominal; D006801:Humans; D008297:Male; D008479:Mediastinal Neoplasms / Q000175:diagnosis / Q000235:genetics* / Q000601:surgery; D009679:Nuclear Family; D010673:Pheochromocytoma / Q000175:diagnosis / Q000235:genetics* / Q000601:surgery