[Psychogenic hand dystonia and hereditary polyneuropathy with liability to pressure palsies. A contribution to etiology of dystonias].
We report on a case of a female who had developed a fixed flexion contracture of the 4th and 5th fingers of the right hand which was painless and at-rest right in the beginning at the age of 19. By means of neurographical examinations a hereditary neuropathy with liability to pressure palsies was established in her and her mother, which had clinically manifested with symptoms of the ulnar nerve at the affected hand. The dystonic symptoms did not show any progression within ten years follow-up. A remarkable feature of the course was the twice repeated occurrence of short, sudden and complete remissions immediately following invasive diagnostic procedures. The thorough discussion of differential diagnostic aspects and the analysis of the familiar situation and psychodynamics of the patient resulted in the diagnosis of a psychogenic hand dystonia.
Strenge
H
H
Klinik für Neurologie, Christian-Albrechts-Universität Kiel.
Speidel
H
H
Albert
E
E
Helbig
B
B
D000328:Adult; D003286:Contracture / Q000235:genetics / Q000523:psychology*; D003291:Conversion Disorder / Q000175:diagnosis / Q000523:psychology*; D003937:Diagnosis, Differential; D004421:Dystonia / Q000235:genetics / Q000523:psychology*; D005190:Family / Q000523:psychology; D005260:Female; D006227:Hand Deformities, Acquired / Q000235:genetics / Q000523:psychology*; D006801:Humans; D009460:Neurologic Examination; D011115:Polyneuropathies / Q000235:genetics* / Q000523:psychology; D012008:Recurrence; D013315:Stress, Psychological / Q000150:complications