Pachydermodactyly in two young girls.
Pachydermodactyly is a benign, superficial fibromatosis frequently observed in young males. We describe the condition in two young girls affected by Ehlers-Danlos syndrome (EDS) and tuberous sclerosis, respectively. We hypothesized that in the patient with tuberous sclerosis, pachydermodactyly is a clinical manifestation of the associated systemic disease, whereas obsessive-compulsive behavior is probably the main cause in the girl with EDS.
Bardazzi
F
F
Department of Dermatology, University of Bologna, Italy.
Neri
I
I
Fanti
P A
PA
Patrizi
A
A
D001706:Biopsy; D002648:Child; D003094:Collagen; D004535:Ehlers-Danlos Syndrome / Q000150:complications / Q000473:pathology / Q000523:psychology; D005260:Female; D005347:Fibroblasts / Q000473:pathology; D005350:Fibroma / Q000473:pathology*; D005385:Fingers / Q000473:pathology*; D006801:Humans; D007642:Keratosis / Q000473:pathology; D009771:Obsessive-Compulsive Disorder / Q000150:complications; D012878:Skin Neoplasms / Q000473:pathology*; D014402:Tuberous Sclerosis / Q000150:complications / Q000473:pathology
D003094:Collagen