title: Pachydermodactyly in two young girls.
abstract: Pachydermodactyly is a benign, superficial fibromatosis frequently observed in young males. We describe the condition in two young girls affected by Ehlers-Danlos syndrome (EDS) and tuberous sclerosis, respectively. We hypothesized that in the patient with tuberous sclerosis, pachydermodactyly is a clinical manifestation of the associated systemic disease, whereas obsessive-compulsive behavior is probably the main cause in the girl with EDS.
authors.affiliation: Department of Dermatology, University of Bologna, Italy.
authors.forename: F
authors.initials: F
authors.lastname: Bardazzi
authors.forename: I
authors.initials: I
authors.lastname: Neri
authors.forename: P A
authors.initials: PA
authors.lastname: Fanti
authors.forename: A
authors.initials: A
authors.lastname: Patrizi
mesh_terms: D001706:Biopsy; D002648:Child; D003094:Collagen; D004535:Ehlers-Danlos Syndrome / Q000150:complications / Q000473:pathology / Q000523:psychology; D005260:Female; D005347:Fibroblasts / Q000473:pathology; D005350:Fibroma / Q000473:pathology*; D005385:Fingers / Q000473:pathology*; D006801:Humans; D007642:Keratosis / Q000473:pathology; D009771:Obsessive-Compulsive Disorder / Q000150:complications; D012878:Skin Neoplasms / Q000473:pathology*; D014402:Tuberous Sclerosis / Q000150:complications / Q000473:pathology
chemical_list: D003094:Collagen