[Three-quadrant syndrome in Klippel-Trenaunay syndrome and primary lymphedema of both legs].
A 34-year-old woman with extensive Klippel-Trenaunay syndrome is presented. Clinical and radiological tests demonstrated that three quadrants are affected with haemangiomas, varicose veins and bone abnormalities. In addition, our patient suffers from congenital lymphoedema of both legs. Associated findings such as intestinal haemangiomata, vascular hamartomas, lipoma or arteriovenous abnormalities of the spinal cord were not apparent. The treatment is only symptomatic with compression bandages and an orthopaedic appliance for compensation of the different leg length.
Schmid
M H
MH
Dermatologische Klinik und Poliklinik, Ludwig-Maximilians-Universität, München.
Trautner
B
B
Plewig
G
G
D000328:Adult; D001458:Bandages; D005260:Female; D006801:Humans; D007715:Klippel-Trenaunay-Weber Syndrome / Q000175:diagnosis* / Q000628:therapy; D008209:Lymphedema / Q000151:congenital* / Q000628:therapy; D010348:Patient Care Team; D018608:Ultrasonography, Doppler; D014648:Varicose Veins / Q000175:diagnosis / Q000628:therapy