title: Sudden death as a presenting symptom of hypertrophic cardiomyopathy: treatment with an implantable cardioverter defibrillator.
abstract: Aborted sudden death as the presenting manifestation of hypertrophic cardiomyopathy in a 14-year-old child is reported. Documented ventricular fibrillation was the cause of cardiac arrest. No ventricular arrhythmia was induced during programmed electrical stimulation. An implantable cardioverter-defibrillator was indicated. As the patient had a family history of myocardial disease, he had undergone a cardiovascular evaluation 4 years before the major event, and was found normal. It is suggested that normal physical examination, ECG, echocardiogram should not rule out the diagnosis of hypertrophic cardiomyopathy when a family history is present. Left ventricular hypertrophy may develop during childhood in patients with hypertrophic cardiomyopathy.
authors.affiliation: Department of Cardiology, Toulon Naval, Hospital St. Anne, Marseille, France.
authors.forename: P
authors.initials: P
authors.lastname: Talard
authors.forename: S
authors.initials: S
authors.lastname: Lévy
authors.forename: J
authors.initials: J
authors.lastname: Bonal
authors.forename: F
authors.initials: F
authors.lastname: Paganelli
authors.forename: C
authors.initials: C
authors.lastname: Bouchiat
authors.forename: G
authors.initials: G
authors.lastname: Cellarier
authors.forename: G V
authors.initials: GV
authors.lastname: Dussarat
mesh_terms: D000293:Adolescent; D002312:Cardiomyopathy, Hypertrophic / Q000150:complications / Q000175:diagnosis* / Q000628:therapy*; D016757:Death, Sudden, Cardiac / Q000209:etiology / Q000517:prevention & control; D017147:Defibrillators, Implantable; D004562:Electrocardiography; D006323:Heart Arrest / Q000209:etiology*; D006801:Humans; D008297:Male