Polyostotic fibrous dysplasia. A long-term follow up of 8 patients.
Eight patients who had polyostotic fibrous dysplasia were followed up for more than 10 years. One had the Albright syndrome. Two of 3 proximal femoral lesions which were treated before puberty by either curettage and bone grafting or by osteotomy, developed progressive deformity during the growth period. One of 2 proximal femoral lesions treated by curettage and bone grafting after the age of 18 also developed a deformity. Two tibial lesions operated on at the age of one and 30 years remained stable. The histological findings showed more active lesions in young patients compared with adults.
Ozaki
T
T
Department of Orthopaedic Surgery, Okayama Medical School, Japan.
Sugihara
M
M
Nakatsuka
Y
Y
Kawai
A
A
Inoue
H
H
D000293:Adolescent; D000328:Adult; D016025:Bone Transplantation; D002648:Child; D002675:Child, Preschool; D018450:Disease Progression; D005260:Female; D005359:Fibrous Dysplasia, Polyostotic / Q000000981:diagnostic imaging / Q000473:pathology / Q000601:surgery*; D005500:Follow-Up Studies; D006621:Hip Joint / Q000000981:diagnostic imaging; D006801:Humans; D007223:Infant; D008297:Male; D010027:Osteotomy; D011859:Radiography; D016896:Treatment Outcome