title: [Rare variants of cutaneous T-cell lymphomas].
abstract: Besides the classical forms of cutaneous T-cell lymphoma (C-CTCL), such as mycosis fungoides and Sézary's syndrome, unique variants may be encountered. The classification of these rare cutaneous T cell lymphomas is problematic and controversial. Newer classifications of lymphoma in general, such as the Revised European-American Lymphoma (REAL) Classification, emphasize well-established clinico-pathological entities. It seems appropriate to attempt to bring greater clarity to the classification of cutaneous T-cell lymphomas using the same principles. In this review, we list and characterize the rare variants of cutaneous T-cell lymphoma, such as (1) clinical, histological and immunological variants of mycosis fungoides; (2) progressive cutaneous T-cell lymphoma (P-CTCL) including transformed classical cutaneous T-cell lymphoma (TC-CTCL) and primary progressive cutaneous T-cell lymphoma (PP-CTCL); (3) angiocentric and angioimmunoblastic cutaneous T-cell lymphomas; (4) large cell anaplastic, CD30+ cutaneous T-cell lymphoma; (5) HTLV-I-associated adult T-cell leukemia/lymphoma (ATLL); (6) cutaneous manifestations of primary extracutaneous T-cell neoplasias; (7) unclassifiable cutaneous T-cell lymphoma.
authors.affiliation: Hautklinik und Poliklinik, Freie Universität Berlin.
authors.forename: S
authors.initials: S
authors.lastname: Goerdt
authors.forename: C
authors.initials: C
authors.lastname: Trautmann
authors.forename: B
authors.initials: B
authors.lastname: Kütting
authors.forename: J
authors.initials: J
authors.lastname: Ramaker
authors.forename: M
authors.initials: M
authors.lastname: Schmuth
authors.forename: E
authors.initials: E
authors.lastname: Thiel
authors.forename: T
authors.initials: T
authors.lastname: Luger
authors.forename: H
authors.initials: H
authors.lastname: Stein
authors.forename: C E
authors.initials: CE
authors.lastname: Orfanos
mesh_terms: D015703:Antigens, CD / Q000032:analysis; D014408:Biomarkers, Tumor / Q000032:analysis; D001706:Biopsy; D005260:Female; D006801:Humans; D016410:Lymphoma, T-Cell, Cutaneous / Q000145:classification / Q000175:diagnosis* / Q000473:pathology; D008297:Male; D009182:Mycosis Fungoides / Q000145:classification / Q000175:diagnosis / Q000473:pathology; D011379:Prognosis; D012751:Sezary Syndrome / Q000145:classification / Q000175:diagnosis / Q000473:pathology; D012867:Skin / Q000473:pathology; D012878:Skin Neoplasms / Q000145:classification / Q000175:diagnosis* / Q000473:pathology
chemical_list: D015703:Antigens, CD; D014408:Biomarkers, Tumor