title: Primary systemic amyloidosis. A report of 2 cases.
abstract: We report 2 cases of primary systemic amyloidosis. A monoclonal gammopathy was confirmed at the postmortem examination of the first patient. An extensive search for evidence of chronic infection, inflammation, neoplasms and paraproteinemia was conclusively negative in the other patient. The recognition of cutaneous signs of primary systemic amyloidosis is crucial to insure a rapid management aimed at postponing the fatal issue of the disease.
authors.affiliation: Department of Dermatology, University of Liège, Belgium.
authors.forename: B
authors.initials: B
authors.lastname: Dézfoulian
authors.forename: J E
authors.initials: JE
authors.lastname: Arrese
authors.forename: A
authors.initials: A
authors.lastname: Fernandez
authors.forename: I
authors.initials: I
authors.lastname: Stas
authors.forename: L
authors.initials: L
authors.lastname: Barthe
authors.forename: I
authors.initials: I
authors.lastname: Hansen
authors.forename: G E
authors.initials: GE
authors.lastname: Piérard
authors.forename: M
authors.initials: M
authors.lastname: de la Brassinne
authors.forename: C M
authors.initials: CM
authors.lastname: Lapière
mesh_terms: D000368:Aged; D000686:Amyloidosis / Q000150:complications / Q000175:diagnosis* / Q000473:pathology; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged