Colonic stricture in cystic fibrosis unmasked by successful transjugular intrahepatic portosystemic stent shunt (TIPSS).
TIPSS was successfully performed in a 10-year-old female cystic fibrosis (CF) patient with bleeding gastric varices due to portal hypertension; precipitation of portosystemic encephalopathy later unveiled the presence of a latent colonic stricture associated with high potency pancreatic enzymes. The unusual sequence of events resulting from the co-existence of two CF pathologies are described, and the implications of treatment discussed.
Ong
T J
TJ
Department of Child Health, Centre for Research into Human Development, University of Dundee, Ninewells Hospital and Medical School.
Murray
F E
FE
Redhead
D N
DN
MacGilchrist
A J
AJ
Anderson
J T
JT
Mehta
A
A
D002648:Child; D003106:Colon / Q000473:pathology*; D003251:Constriction, Pathologic / Q000150:complications; D003550:Cystic Fibrosis / Q000150:complications*; D004932:Esophageal and Gastric Varices / Q000150:complications*; D005260:Female; D006471:Gastrointestinal Hemorrhage / Q000150:complications*; D006801:Humans; D019168:Portasystemic Shunt, Transjugular Intrahepatic