title: [Anesthetic management of a pediatric patient with Cornelia de Lange syndrome].
abstract: We did anesthetic management on a pediatric patient with Cornelia de Lange syndrome presenting a peculiar look, variable physical deformities, and some growth and mental retardations. An 8-year-old male patient was scheduled for inguinal hernioplasty under general anesthesia. This patient had been suffering from dehydration for apodeisis and self-destructive tendency due to psychologic stress. Anesthesia was induced and maintained with sevoflurane and N2O in oxygen. The area of skin incision was infiltrated with 0.25 % bupivacaine for the purpose of post-operative analgesia, and as a result, psychologically and physically stable condition was obtained during post-operative periods. It is necessary to understand not only the patient's physical conditions but also mental ones in order to make the anesthetic management safer and more satisfactory.
authors.affiliation: Department of Anesthesiology, Sagamihara Kyodo Hospital.
authors.forename: H
authors.initials: H
authors.lastname: Nagai
authors.forename: Y
authors.initials: Y
authors.lastname: Noda
authors.forename: K
authors.initials: K
authors.lastname: Mase
authors.forename: S
authors.initials: S
authors.lastname: Ogawa
authors.forename: H
authors.initials: H
authors.lastname: Suzuki
mesh_terms: D000698:Analgesia; D000768:Anesthesia, General / Q000379:methods*; D018685:Anesthetics, Inhalation; D000779:Anesthetics, Local; D002045:Bupivacaine; D002648:Child; D003635:De Lange Syndrome / Q000150:complications* / Q000523:psychology; D004987:Ethers; D006552:Hernia, Inguinal / Q000601:surgery; D006801:Humans; D008297:Male; D008738:Methyl Ethers; D009609:Nitrous Oxide; D010100:Oxygen; D010149:Postoperative Pain / Q000517:prevention & control; D000077149:Sevoflurane
chemical_list: D018685:Anesthetics, Inhalation; D000779:Anesthetics, Local; D004987:Ethers; D008738:Methyl Ethers; D000077149:Sevoflurane; D009609:Nitrous Oxide; D010100:Oxygen; D002045:Bupivacaine