Porokeratotic eccrine ostial and dermal duct nevus of late onset: more frequent than previously suggested?
We describe the case of a 10-year-old boy with a porokeratotic eccrine ostial and dermal duct nevus (PEODDN) of late onset. The patient had an 8-year history of multiple keratotic papules on the dorsal surface, and multiple yellowish pitting lesions on the plantar surface of the right foot. Light-microscopic studies of both lesions showed multiple cornoid lamella-like parakeratotic columns, which exclusively arose over eccrine sweat ducts in which the acrosyringium was dilated. Although PEODDN is considered to be a congenital hamartoma of eccrine origin, a review of the literature showed us that the frequency of a late-onset variant may be as high as 26%.
Valks
R
R
Department of Dermatology, Hospital Universitario de la Princesa, Madrid, Spain.
Abajo
P
P
Fraga
J
J
Aragüés
M
M
García-Diez
A
A
D002648:Child; D004108:Dilatation, Pathologic / Q000473:pathology; D004439:Eccrine Glands / Q000473:pathology*; D005534:Foot Diseases / Q000473:pathology*; D006222:Hamartoma / Q000151:congenital; D006801:Humans; D007642:Keratosis / Q000473:pathology; D008297:Male; D009506:Nevus / Q000473:pathology*; D017499:Porokeratosis / Q000473:pathology*; D012878:Skin Neoplasms / Q000473:pathology*; D013543:Sweat Gland Diseases / Q000151:congenital