Type IV laryngotracheoesophageal clefts: surgical management for long-term survival.
Complete laryngotracheoesophageal clefts (types III and IV) are rare congenital anomalies that occur when the primitive foregut fails to separate into the tracheobronchial tree and the esophagus. This article summarizes a 10-year institutional experience with six infants who had type IV clefts, presents a modification of the authors' surgical approach, and identifies pitfalls in the management of these infants. Three of the six children are long-term survivors. The recognition of specific complicating issues leads to a standardized approach, which can result in successful repair and long-term survival.
Simpson
B B
BB
Department of Pediatric Surgery, Massachusetts General Hospital, Boston 02114, USA.
Ryan
D P
DP
Donahoe
P K
PK
Schnitzer
J J
JJ
Kim
S H
SH
Doody
D P
DP
D000015:Abnormalities, Multiple / Q000145:classification / Q000000981:diagnostic imaging / Q000196:embryology / Q000601:surgery*; D001999:Bronchoscopy; D003937:Diagnosis, Differential; D004947:Esophagus / Q000002:abnormalities*; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D007231:Infant, Newborn; D007830:Larynx / Q000002:abnormalities*; D008297:Male; D011859:Radiography; D013270:Stomach / Q000002:abnormalities; D016019:Survival Analysis; D014132:Trachea / Q000002:abnormalities*; D016896:Treatment Outcome