Intrasellar paraganglioma: report of a case in a sibship of von Hippel-Lindau disease.
Although uncommon, paragangliomas are known to affect the central nervous system. Those that arise in the sellar region are particularly rare. We report the clinicopathological features of a paraganglioma occurring in the setting of von Hippel-Lindau disease, a disorder in which paragangliomas are known to occur. We also present a review of the literature.
Scheithauer
B W
BW
Department of Pathology and Laboratory Medicine, Mayo Clinic, Rochester, Minnesota, USA.
Parameswaran
A
A
Burdick
B
B
D000293:Adolescent; D006801:Humans; D007150:Immunohistochemistry; D008279:Magnetic Resonance Imaging; D008297:Male; D008854:Microscopy, Electron; D010235:Paraganglioma / Q000150:complications* / Q000175:diagnosis / Q000473:pathology; D012658:Sella Turcica; D012888:Skull Neoplasms / Q000150:complications* / Q000175:diagnosis / Q000473:pathology; D006623:von Hippel-Lindau Disease / Q000150:complications*