title: Colonic stricture in cystic fibrosis unmasked by successful transjugular intrahepatic portosystemic stent shunt (TIPSS).
abstract: TIPSS was successfully performed in a 10-year-old female cystic fibrosis (CF) patient with bleeding gastric varices due to portal hypertension; precipitation of portosystemic encephalopathy later unveiled the presence of a latent colonic stricture associated with high potency pancreatic enzymes. The unusual sequence of events resulting from the co-existence of two CF pathologies are described, and the implications of treatment discussed.
authors.affiliation: Department of Child Health, Centre for Research into Human Development, University of Dundee, Ninewells Hospital and Medical School.
authors.forename: T J
authors.initials: TJ
authors.lastname: Ong
authors.forename: F E
authors.initials: FE
authors.lastname: Murray
authors.forename: D N
authors.initials: DN
authors.lastname: Redhead
authors.forename: A J
authors.initials: AJ
authors.lastname: MacGilchrist
authors.forename: J T
authors.initials: JT
authors.lastname: Anderson
authors.forename: A
authors.initials: A
authors.lastname: Mehta
mesh_terms: D002648:Child; D003106:Colon / Q000473:pathology*; D003251:Constriction, Pathologic / Q000150:complications; D003550:Cystic Fibrosis / Q000150:complications*; D004932:Esophageal and Gastric Varices / Q000150:complications*; D005260:Female; D006471:Gastrointestinal Hemorrhage / Q000150:complications*; D006801:Humans; D019168:Portasystemic Shunt, Transjugular Intrahepatic