Campomelic syndrome--laryngotracheomalacia treated with single-stage laryngotracheal reconstruction.
The campomelic syndrome is a rare osteochondrodysplasia which frequently leads to early death from pulmonary insufficiency. We describe a patient with anatomic compromise of the upper airway due to diffuse laryngotracheomalacia and a moderate subglottic stenosis, treated successfully with single-stage laryngotracheal reconstruction using a rib graft. To our knowledge this has not been previously described. A review of the current literature is included.
Otolaryngology Consultants of Memphis, TN 38105, USA.
L
L
Ruan
R B
RB
Mitchell
K D
KD
Pereira
R T
RT
Younis
R H
RH
Lazar
D000402:Airway Obstruction / Q000209:etiology / Q000601:surgery; D005145:Face / Q000002:abnormalities; D005269:Femur / Q000002:abnormalities; D006801:Humans; D007223:Infant; D007818:Laryngeal Diseases / Q000150:complications / Q000601:surgery*; D007829:Laryngostenosis / Q000601:surgery; D007830:Larynx / Q000601:surgery*; D008297:Male; D010009:Osteochondrodysplasias / Q000150:complications / Q000601:surgery; D013577:Syndrome; D014132:Trachea / Q000601:surgery*; D014133:Tracheal Diseases / Q000150:complications / Q000601:surgery*