Weill-Marchesani syndrome complicated by secondary glaucoma. Case management with surgical lens extraction.
BACKGROUND
A case of the rare Weill-Marchesani syndrome is presented with characteristic spherophakia, lenticular myopia and secondary glaucoma. The difficulties of management are described.


RESULTS
Following failure of conservative medical treatment with timoptol, pilocarpine drops and diamox; laser iridotomies temporarily improved but did not halt progress of the glaucoma. Ultimate removal of the lens was required adequately to control the tensions, although this surgical procedure proved hazardous.


CONCLUSIONS
The difficulties of management in the Weill-Marchesani syndrome as reported in the literature, are confirmed in this case. Surgical removal of the lens to control the glaucoma may ultimately be the only option, but this procedure can be hazardous with vitreous loss and other complications to be expected.
J N
JN
Taylor
D000293:Adolescent; D002387:Cataract Extraction; D005124:Eye Abnormalities / Q000150:complications* / Q000503:physiopathology / Q000601:surgery; D005260:Female; D005901:Glaucoma / Q000209:etiology* / Q000503:physiopathology; D006130:Growth Disorders / Q000150:complications; D006801:Humans; D007429:Intraocular Pressure; D007908:Lens, Crystalline / Q000002:abnormalities* / Q000503:physiopathology / Q000601:surgery; D007910:Lenses, Intraocular; D009216:Myopia / Q000150:complications; D013577:Syndrome; D014792:Visual Acuity