X-linked agammaglobulinemia presenting as pseudomonas aeruginosa septicemia.
Usually, presenting infections in children with agammaglobulinemia include pneumonia and otitis media caused by pyogenic bacteria. We report here two cases of Pseudomonas aeruginosa septicemia with ecthyma gangrenosum, in previously healthy boys, leading to the diagnosis of X-linked agammaglobulinemia.
Department of Internal Medicine, Centre Hospitalier Lyon-Sud, France.
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Zenone
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Souillet
D000361:Agammaglobulinemia / Q000150:complications / Q000175:diagnosis* / Q000235:genetics; D016470:Bacteremia / Q000150:complications*; D002675:Child, Preschool; D008040:Genetic Linkage; D006801:Humans; D008297:Male; D011552:Pseudomonas Infections / Q000150:complications*; D014960:X Chromosome