Phakomatosis pigmentovascularis: report of a case.
Phakomatosis pigmentovascularis is a rare cutaneous malformation characterized by a combination of melanocytic nevi and nevus flammeus. We report a 16-year-old boy with extensive and predominantly unilateral skin involvement combining features of speckled melanocytic nevi over a background of nevus flammeus. A brief review of the literature and classification of this phakomatosis is presented.
Mahroughan
M
M
Pinkus Dermatopathology Laboratory, Monroe, Michigan, USA.
Mehregan
A H
AH
Mehregan
D A
DA
D000293:Adolescent; D017668:Age of Onset; D018450:Disease Progression; D006801:Humans; D008297:Male; D009506:Nevus / Q000150:complications / Q000175:diagnosis / Q000503:physiopathology; D009508:Nevus, Pigmented / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology; D012867:Skin / Q000473:pathology*; D012878:Skin Neoplasms / Q000150:complications* / Q000175:diagnosis / Q000503:physiopathology; D013577:Syndrome