Spinal cord compression due to extramedullary hematopoiesis in the proliferative phase of polycythemia vera.
Extramedullary hematopoiesis is a common accompaniment of a variety of hematologic diseases such as hereditary spherocytosis, thalassemia and myelofibrosis. The association of extramedullary hematopoiesis with polycythemia vera in the proliferative phase is much less usual. We report a patient who presented with paraplegia due to spinal cord compression; clinical investigation revealed a paravertebral hematopoietic tumor, and the diagnosis of polycythemia vera was then established.
de Morais
J C
JC
University Hospital, Federal University of Rio de Janeiro, Brazil.
Spector
N
N
Lavrado
F P
FP
Nobre
L F
LF
de Mattos
J P
JP
Pulcheri
W
W
Nucci
M
M
Novis
S
S
de Oliveira
H P
HP
D001853:Bone Marrow / Q000473:pathology; D017809:Fatal Outcome; D019337:Hematologic Neoplasms / Q000150:complications* / Q000473:pathology; D006411:Hematopoiesis, Extramedullary; D006801:Humans; D008297:Male; D008875:Middle Aged; D010264:Paraplegia / Q000209:etiology; D011087:Polycythemia Vera / Q000150:complications* / Q000473:pathology / Q000628:therapy; D013117:Spinal Cord Compression / Q000209:etiology*