Pulmonary hypertension developing after alglucerase therapy in two patients with type 1 Gaucher disease complicated by the hepatopulmonary syndrome.
Dawson
A
A
Division of Chest and Critical Care Medicine, Scripps Clinic and Research Foundation, La Jolla, CA 92037, USA.
Elias
D J
DJ
Rubenson
D
D
Bartz
S H
SH
Garver
P R
PR
Kay
A C
AC
Bloor
C M
CM
Beutler
E
E
D000328:Adult; D004108:Dilatation, Pathologic / Q000150:complications / Q000188:drug therapy; D005260:Female; D005776:Gaucher Disease / Q000150:complications / Q000188:drug therapy* / Q000473:pathology; D005962:Glucosylceramidase / Q000009:adverse effects*; D006529:Hepatomegaly / Q000150:complications* / Q000188:drug therapy; D006801:Humans; D006976:Hypertension, Pulmonary / Q000139:chemically induced*; D000860:Hypoxia / Q000150:complications* / Q000188:drug therapy; D008297:Male; D011651:Pulmonary Artery / Q000473:pathology*; D013577:Syndrome
C070292:alglucerase; D005962:Glucosylceramidase