title: Pulmonary hypertension developing after alglucerase therapy in two patients with type 1 Gaucher disease complicated by the hepatopulmonary syndrome.
authors.affiliation: Division of Chest and Critical Care Medicine, Scripps Clinic and Research Foundation, La Jolla, CA 92037, USA.
authors.forename: A
authors.initials: A
authors.lastname: Dawson
authors.forename: D J
authors.initials: DJ
authors.lastname: Elias
authors.forename: D
authors.initials: D
authors.lastname: Rubenson
authors.forename: S H
authors.initials: SH
authors.lastname: Bartz
authors.forename: P R
authors.initials: PR
authors.lastname: Garver
authors.forename: A C
authors.initials: AC
authors.lastname: Kay
authors.forename: C M
authors.initials: CM
authors.lastname: Bloor
authors.forename: E
authors.initials: E
authors.lastname: Beutler
mesh_terms: D000328:Adult; D004108:Dilatation, Pathologic / Q000150:complications / Q000188:drug therapy; D005260:Female; D005776:Gaucher Disease / Q000150:complications / Q000188:drug therapy* / Q000473:pathology; D005962:Glucosylceramidase / Q000009:adverse effects*; D006529:Hepatomegaly / Q000150:complications* / Q000188:drug therapy; D006801:Humans; D006976:Hypertension, Pulmonary / Q000139:chemically induced*; D000860:Hypoxia / Q000150:complications* / Q000188:drug therapy; D008297:Male; D011651:Pulmonary Artery / Q000473:pathology*; D013577:Syndrome
chemical_list: C070292:alglucerase; D005962:Glucosylceramidase