title: [Anesthesia in Kearns-Sayre syndrome (mitochondrial myopathy)].
abstract: We report the case of a 27-year-old woman with a history of Kearns-Sayre syndrome and a double mitral lesion who underwent surgery without complications. Anesthetic induction was achieved with propofol and fentanyl, and maintenance was with nitrous oxide and oxygen through a face mask. There were no instances of O2 desaturation or hemodynamic alterations. The postoperative period transpired without adverse events and the patient was released 24 h after surgery. The management of anesthesia in this rare mitochondrial disease is described, and anesthetic alternatives are discussed as depending on clinical findings that can occur in the context of these syndromes.
authors.affiliation: Servicio de Anestesiología, Reanimación y Terapéutica del Dolor, Hospital de la Santa Creu i Sant Pau, Barcelona.
authors.forename: S
authors.initials: S
authors.lastname: Sabaté
authors.forename: M
authors.initials: M
authors.lastname: Ferrándiz
authors.forename: P
authors.initials: P
authors.lastname: Paniagua
authors.forename: J M
authors.initials: JM
authors.lastname: Villamor
authors.forename: F
authors.initials: F
authors.lastname: Vilanova
authors.forename: J M
authors.initials: JM
authors.lastname: Villar-Landeira
mesh_terms: D000027:Abortion, Incomplete / Q000601:surgery; D000328:Adult; D000758:Anesthesia; D000932:Antiemetics / Q000008:administration & dosage; D005260:Female; D006801:Humans; D007625:Kearns-Sayre Syndrome; D011247:Pregnancy; D011292:Premedication
chemical_list: D000932:Antiemetics
vernacular_title: Anestesia en el síndrome de Kearns-Sayre (miopatía mitocondrial).