title: Aggressive polyfibromatosis: a 10 year follow-up.
abstract: Polyfibromatosis syndrome is a condition characterized by the occurrence of several cutaneous fibrotic conditions including Dupuytren's contracture and keloid formation. A 10 year follow-up of a patient with an aggressive type of polyfibromatosis associated with erosive arthropathy is presented. The underlying pathogenesis and management of this uncommon condition is discussed.
authors.affiliation: St John's Institute of Dermatology, St Thomas' Hospital, London, United Kingdom.
authors.forename: Y C
authors.initials: YC
authors.lastname: Lee
authors.forename: H H
authors.initials: HH
authors.lastname: Chan
authors.forename: M M
authors.initials: MM
authors.lastname: Black
mesh_terms: D004387:Dupuytren Contracture / Q000150:complications* / Q000175:diagnosis; D018222:Desmoid Tumors / Q000150:complications* / Q000175:diagnosis; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D008875:Middle Aged; D010003:Osteoarthritis / Q000150:complications* / Q000175:diagnosis