Aggressive polyfibromatosis: a 10 year follow-up.
Polyfibromatosis syndrome is a condition characterized by the occurrence of several cutaneous fibrotic conditions including Dupuytren's contracture and keloid formation. A 10 year follow-up of a patient with an aggressive type of polyfibromatosis associated with erosive arthropathy is presented. The underlying pathogenesis and management of this uncommon condition is discussed.
Lee
Y C
YC
St John's Institute of Dermatology, St Thomas' Hospital, London, United Kingdom.
Chan
H H
HH
Black
M M
MM
D004387:Dupuytren Contracture / Q000150:complications* / Q000175:diagnosis; D018222:Desmoid Tumors / Q000150:complications* / Q000175:diagnosis; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D008875:Middle Aged; D010003:Osteoarthritis / Q000150:complications* / Q000175:diagnosis