Acute cardiac tamponade secondary to congenital factor V deficiency.
Spontaneous cardiac tamponade secondary to a congenital coagulation defect has never been reported. We report a case of acute cardiac tamponade in a patient with a known factor V deficiency. This patient presented with classic signs of acute cardiac tamponade and an enlarged cardiac silhouette. After diagnostic two-dimensional echocardiography and treatment with fresh-frozen plasma, the patient underwent emergent pericardiocentesis followed by complete pericardiectomy.
Schultz
S C
SC
Division of Cardiovascular Surgery, Georgetown University School of Medicine, Washington, D.C., USA.
Breall
J
J
Hannan
R
R
D000208:Acute Disease; D000328:Adult; D002305:Cardiac Tamponade / Q000175:diagnosis / Q000209:etiology* / Q000628:therapy; D004452:Echocardiography; D005166:Factor V Deficiency / Q000097:blood / Q000150:complications / Q000151:congenital*; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D010492:Pericardiectomy; D010951:Plasma Exchange