[Sturge-Weber angiomatosis responsible for hemiplegia without cerebral infarction in term pregnancy].
During the third quarter of her pregnancy, a young woman with Sturge-Weber angiomatosis had a severe right hemiplegia with hemianopia and aphasia, followed 48 hours later by focal seizures. Neuroimaging did not show any cerebral lesion but contrast magnetic resonance imaging revealed a left hemispheric pial angiomatosis. The patient recovered progressively from the third day after a ceasarean. The hemianopia disappeared within 15 days, the hemiplegia within one month and the aphasia greatly improved within 3 months. Ten weeks after the clinical onset, we performed a positron emission tomography study. A decrease from 15 to 40% of the cerebral radioactivity was observed after injection of water (H2(15)O) or fluorodesoxyglucose (18FDG) in the left temporooccipital area adjacent to the meningeal angiomatosis. A chronic and focal olighemia, already reported in Sturge-Weber angiomatosis, might participate in the occurrence of this cortical metabolic depression.
Chabriat
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H
Service de Neurologie, Hôpital Saint-Antoine, Paris.
Pappata
S
S
Traykov
L
L
Kurtz
A
A
Bousser
M G
MG
D000328:Adult; D002540:Cerebral Cortex / Q000378:metabolism; D005260:Female; D006429:Hemiplegia / Q000209:etiology* / Q000378:metabolism; D006801:Humans; D011247:Pregnancy; D011248:Pregnancy Complications; D013341:Sturge-Weber Syndrome / Q000150:complications* / Q000378:metabolism; D013997:Time Factors; D014055:Tomography, Emission-Computed