[The function of the segmental motoneurons in Wilson-Konovalov's hepatocerebral dystrophy].
12 patients were examined by means of stimulative electromyography. Chronaximetric studies were carried out in 18 patients. The maximal amplitude of H-potential revealed the decrease of reflex excitability of the motoneurons pool. The stimulus value which is necessary for evoking H-reflex of liminal size testified the high reflex excitability of some alpha-motoneurons part. These motoneurons may take part in hyperkinesis development. The direct electrical excitability of motor units was elevated that was confirmed by motor response values. The motor analyzer functional rearrangement was revealed after stereotaxic operations as evidenced by dynamics of H-reflex and M-response parameters.
Starikov
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D000293:Adolescent; D000328:Adult; D002907:Chronaxy; D004576:Electromyography; D006181:H-Reflex; D006527:Hepatolenticular Degeneration / Q000503:physiopathology* / Q000601:surgery; D006801:Humans; D009046:Motor Neurons / Q000502:physiology*; D009047:Motor Neurons, Gamma / Q000502:physiology*; D014202:Tremor / Q000503:physiopathology