[Two cases of the successful treatment of TAPVR with asplenia syndrome in neonates and infants].
Two patients of asplenia syndrome with pulmonary venous obstruction underwent TAPVR repair in the period of neonate (14 days) and infant (49 days). Associated procedures were necessary to adjust pulmonary blood flow (central shunt in 1, PA banding in 1). Both patients required subsequent surgical procedures; right modified BT shunt, due to kinking of central shunt in one patient and rePA banding for reduction of pulmonary blood flow in another patient. One patient died 4 months after the first operation of arrhythmia. Another patient is doing well in 7 months after the first operation. The TAPVR repair in the early period of infant or naonate is necessary to prevent progress of pulmonary venous obstruction. Adjustment of pulmonary blood flow is important for management of patients of asplenia syndrome after TAPVR repair.
Suzuki
Y
Y
Department of Cardiovascular Surgery, Hachiouji Children's Hospital, Tokyo, Japan.
Oiwa
H
H
Nakayama
S
S
Nakamoto
M
M
Ikegami
H
H
Noma
K
K
D005260:Female; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D011667:Pulmonary Veins / Q000002:abnormalities* / Q000601:surgery*; D011668:Pulmonary Veno-Occlusive Disease / Q000601:surgery; D013154:Spleen / Q000002:abnormalities*