Prader-Willi syndrome--a case report of the multidisciplinary management of the orofacial problems.
A 24-year-old man with Prader-Willi syndrome presented with a class III malocclusion, featuring maxillary hypoplasia and severe enamel deficiency. Treatment involved orthodontic alignment, surgical advancement of the maxilla and restorative treatment to augment vertical facial height, improve the final occlusion and increase short clinical dental crown heights. The principal features of the syndrome and the management of this case are discussed.
Banks
P A
PA
Fairfield General Hospital, Bury, Greater Manchester, U.K.
Bradley
J C
JC
Smith
A
A
D000328:Adult; D003442:Crowns; D003743:Dental Enamel / Q000473:pathology; D003766:Dental Occlusion; D003776:Dental Porcelain; D017267:Dental Prosthesis Design; D006047:Gold Alloys; D006801:Humans; D008297:Male; D008313:Malocclusion, Angle Class III / Q000628:therapy; D008437:Maxilla / Q000002:abnormalities / Q000601:surgery; D016876:Metal Ceramic Alloys; D009971:Orthodontics, Corrective; D019340:Osteotomy, Le Fort; D011218:Prader-Willi Syndrome / Q000628:therapy*; D019228:Tooth Crown / Q000473:pathology; D014076:Tooth Diseases / Q000628:therapy*; D014716:Vertical Dimension
D006047:Gold Alloys; D016876:Metal Ceramic Alloys; D003776:Dental Porcelain