[Oculopharyngeal myopathies: value of myotomy of the superior sphincter of the esophagus. Apropos of a case].
Since 3 years, a 74 year-old man suffered of swallowing impairment, weight loss, bilateral ptosis and proximal muscular weakness. Electron microscopy disclosed intranuclear tubular filaments and confirmed the diagnosis of oculopharyngeal muscular dystrophy. Upper oesophageal sphincter myotomy was performed with complete improvement. Four months after surgery, swallowing disorders were not recurrent and weight gain was substantial.
Vignes
S
S
Service de médecine interne, hôpital de la Pitié-Salpétrière, Paris, France.
Lacau Saint Guily
J
J
Colin
J Y
JY
Eymard
B
B
Wechsler
B
B
Godeau
P
P
D000368:Aged; D001763:Blepharoptosis / Q000209:etiology / Q000601:surgery; D003680:Deglutition Disorders / Q000209:etiology / Q000601:surgery; D004943:Esophagogastric Junction / Q000601:surgery*; D006801:Humans; D008297:Male; D009136:Muscular Dystrophies / Q000150:complications / Q000601:surgery*; D009801:Oculomotor Muscles; D010609:Pharyngeal Muscles