[Lumbo-sacroiliac hyperostosis with retroperitoneal fibrosis in spondarthritis hyperostotical pustulo-psoriatica--with sternocostoclavicular hyperostosis and superior and inferior venous obstruction syndrome: pathogenetic hypothesis of fibro-osteopathia psoriatica].
We report two cases of retroperitoneal fibrosis which were found in 38 patients with "spondarthritis hyperostotica pustulo-psoriatica" (spond.hyp.p.-p.). Spond.hyp.p.-p. is associated with sternocosto-clavicular hyperostosis and resembles pustulotic arthroosteitis and SAPHO syndrome. However, as dermatologically and osteo-histopathologically documented, it is an enthesiopathic and hyperostotic form of spondarthritis psoriatica. Both cases show a lumbosacroiliac hyperostosis (LSIH) which is a rare analogue to sternocosto-clavicular hyperostosis (SCCH). Facultative paraosseous connective-tissue proliferation results in a new form of retroperitoneal fibrosis with sacroiliac origin. Mediastinal and pelvic masses cause superior and inferior vena caval obstruction syndromes. Because of proven psoriasis in pelvic bone with para-periostal
Schilling
F
F
Freier wissenschaftlicher Mitarbeiter in der Klinik für Radiologie, Johannes-Gutenberg-Universität Mainz.
Schweden
F
F
D015535:Arthritis, Psoriatic / Q000000981:diagnostic imaging*; D003097:Collateral Circulation / Q000502:physiology; D003251:Constriction, Pathologic / Q000000981:diagnostic imaging; D017809:Fatal Outcome; D005500:Follow-Up Studies; D006801:Humans; D015218:Hyperostosis, Sternocostoclavicular / Q000000981:diagnostic imaging*; D007085:Ilium / Q000000981:diagnostic imaging; D008159:Lumbar Vertebrae / Q000000981:diagnostic imaging; D008297:Male; D008875:Middle Aged; D012185:Retroperitoneal Fibrosis / Q000000981:diagnostic imaging*; D012447:Sacrum / Q000000981:diagnostic imaging; D013167:Spondylitis, Ankylosing / Q000000981:diagnostic imaging*; D013350:Subclavian Vein / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed; D014682:Vena Cava, Inferior / Q000000981:diagnostic imaging; D014689:Venous Insufficiency / Q000000981:diagnostic imaging*