[Progressive course of idiopathic pulmonary fibrosis in 2 monozygotic twin sisters].
This is the report on a lethal course of idiopathic pulmonary fibrosis in two monozygotic twins. The specific aspects of familial idiopathic pulmonary fibrosis and the pattern of inheritance are discussed. The pattern is probably autosomal dominant with variable penetrance.
Thomas
H
H
Pneumologie-Allergologie, St. Elisabeth-Krankenhaus Dorsten.
Costabel
U
U
D000368:Aged; D002869:Chromosome Aberrations / Q000235:genetics; D025063:Chromosome Disorders; D004200:Diseases in Twins / Q000235:genetics*; D017809:Fatal Outcome; D005260:Female; D005799:Genes, Dominant; D006801:Humans; D010641:Phenotype; D011658:Pulmonary Fibrosis / Q000235:genetics*; D014430:Twins, Monozygotic