[Moebius syndrome: therapeutic proposals from 2 cases].
Moebius syndrome is a congenital bilateral palsy of the sixth and seventh cranial nerves. It results a total absence of facial expression and a severe strabismus. Social life is greatly disturbed. Other anomalies may be associated, especially other cranial palsies and Poland syndrome. The etiology of this syndrome isn't clearly established. Stem necrosis secondary to a vascular deficiency is often admitted. We report two observations. We emphasize the importance of a complete maxillo-facial treatment including maxillo-mandibular anomaly. Both patient underwent orthognathic surgery. The first one for class II and the second for class III anomaly. One patient underwent a facial reanimation by temporal muscle transfer. Orthognathic surgery must be realized prior to facial reanimation. A correction of the strabismus is possible. Moebius syndrome is a rare (200 observations) but very severe malformation. Maxillofacial surgery is able to improve the morphological and relational aspect of Moebius syndrome.
Braye
F
F
Service de Stomatologie, Chirurgie Maxillo-faciale et Plastique de la face, centre hospitalier, Lyon-Sud, Pierre-Bénite.
Souchere
B
B
Franc
C
C
Freidel
M
M
D000293:Adolescent; D000328:Adult; D003389:Cranial Nerve Diseases / Q000151:congenital* / Q000523:psychology / Q000601:surgery; D005149:Facial Expression; D005158:Facial Paralysis / Q000151:congenital* / Q000523:psychology / Q000601:surgery; D005260:Female; D006801:Humans; D007398:Interpersonal Relations; D008297:Male; D008312:Malocclusion, Angle Class II / Q000601:surgery; D008313:Malocclusion, Angle Class III / Q000601:surgery; D009886:Ophthalmoplegia / Q000151:congenital* / Q000523:psychology / Q000601:surgery; D010027:Osteotomy / Q000379:methods; D019340:Osteotomy, Le Fort; D010243:Paralysis / Q000151:congenital / Q000601:surgery; D011045:Poland Syndrome / Q000473:pathology; D013285:Strabismus / Q000151:congenital / Q000601:surgery; D013524:Surgical Flaps; D013577:Syndrome; D013703:Temporal Muscle / Q000637:transplantation