title: Dedifferentiated cystic nephroma with malignant mesenchymoma as the dedifferentiated component.
abstract: Cystic tumors of the kidney are uncommon and usually do not have solid areas. We report a predominantly cystic renal tumor with solid anaplastic component showing rhabdomyoblastic and cartilaginous differentiation in a 26-month-old girl. Terminology and pathogenesis of tumor progression are discussed along with a review of reports of tumors associated with cystic nephroma.
authors.affiliation: Servico de Anatomia Patologica e Citopatologia, Instituto Nacional do Cancer, Rio de Janeiro, Brazil.
authors.forename: P A
authors.initials: PA
authors.lastname: Faria
authors.forename: M C
authors.initials: MC
authors.lastname: Zerbini
mesh_terms: D002454:Cell Differentiation; D002675:Child, Preschool; D005260:Female; D005434:Flow Cytometry; D006801:Humans; D007150:Immunohistochemistry; D007680:Kidney Neoplasms / Q000473:pathology*; D008637:Mesenchymoma / Q000473:pathology*; D007690:Polycystic Kidney Diseases / Q000188:drug therapy / Q000473:pathology*; D012208:Rhabdomyosarcoma / Q000473:pathology; D009396:Wilms Tumor / Q000188:drug therapy / Q000473:pathology*