Atrophic pigmented dermatofibrosarcoma presenting as infraorbital hyperpigmentation.
BACKGROUND
Pigmented dermatofibrosarcoma is a rare tumor of the skin and constitutes 1-5% of all dermatofibrosarcoma. Most cases present as polypoid multinodular growth. Occasional cases may be atrophic. We report an extraordinary case with progressive infraorbital atrophy.


METHODS
A 24-year-old woman came to us for a diffuse bluish atrophic lesion over the left infraorbital area. The lesion progressed gradually over 2 years. Histologic examination revealed mature spindle cell proliferation in the lower dermis and hypodermis. Interspersed were some heavily pigmented melanocytes.


CONCLUSIONS
We report an unusual case of progressive bluish discoloration and atrophy of the infraorbital area. This is a rare manifestation of dermatofibrosarcoma.
Chuan
M T
MT
Department of Dermatology, Cathay General Hospital, Taipei, Taiwan, Republic of China.
Tsai
T F
TF
Wu
M C
MC
Wong
T H
TH
D000328:Adult; D001284:Atrophy; D018223:Dermatofibrosarcoma / Q000175:diagnosis* / Q000473:pathology; D003937:Diagnosis, Differential; D018450:Disease Progression; D005148:Facial Dermatoses / Q000175:diagnosis* / Q000473:pathology; D005153:Facial Neoplasms / Q000175:diagnosis* / Q000473:pathology; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D017495:Hyperpigmentation / Q000175:diagnosis* / Q000473:pathology; D008544:Melanocytes / Q000473:pathology; D009915:Orbit; D012867:Skin / Q000473:pathology; D012878:Skin Neoplasms / Q000175:diagnosis* / Q000473:pathology; D012880:Skin Pigmentation