title: Coats' disease and central nervous system venous malformation.
abstract: Primary retinal telangiectasis or Coats' disease is a non-hereditary retinal vascular abnormality consisting of incompetent telangiectatic and aneurysmal retinal vessels. It is characteristically found unilaterally in boys and occasionally may be associated with other systemic disorders. The authors report the first case of primary retinal telangiectasis with a concomitant diffuse central nervous system venous abnormality.
authors.affiliation: Johns Hopkins Center for Hereditary Eye Diseases, Wilmer Opthalmological Institute, Baltimore, MD, USA.
authors.forename: J M
authors.initials: JM
authors.lastname: Robitaille
authors.forename: L
authors.initials: L
authors.lastname: Monsein
authors.forename: E I
authors.initials: EI
authors.lastname: Traboulsi
mesh_terms: D000783:Aneurysm / Q000150:complications* / Q000473:pathology; D002533:Cerebral Angiography; D002550:Cerebral Veins / Q000002:abnormalities* / Q000473:pathology; D002648:Child; D003287:Contrast Media; D005451:Fluorescein Angiography; D005654:Fundus Oculi; D005682:Gadolinium; D019786:Gadolinium DTPA; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D009942:Organometallic Compounds; D004369:Pentetic Acid / Q000031:analogs & derivatives; D012164:Retinal Diseases / Q000150:complications* / Q000175:diagnosis; D012171:Retinal Vessels / Q000002:abnormalities* / Q000473:pathology; D013684:Telangiectasis / Q000150:complications* / Q000175:diagnosis; D014792:Visual Acuity
chemical_list: D003287:Contrast Media; D009942:Organometallic Compounds; D004369:Pentetic Acid; D005682:Gadolinium; D019786:Gadolinium DTPA