Mesenteric neurofibroma in von Recklinghausen's disease.
The authors report the case of a 6-year-old boy admitted for surgical removal of a 5- x 4-cm neurofibroma over the left wrist. On routine clinical examination a mobile firm, nodular, central abdominal mass was discovered. At laparotomy a tumor (measuring 7 x 5 x 3 cm) arising from the ileal mesentery was found. Complete excision of the mass together with a segment of ileum, followed by end-to-end bowel anastomosis was performed. Histological examination showed that the main elements of the mass consisted of wavy, long-spindled cells that crossed irregularly (pallisading negative). Special stains and immunocytochemistry for S-100 protein confirmed the mass to be a neurofibroma of the mesentery. The patient had an uneventful postoperative course and no signs of recurrence or fresh tumor have been recognized in the 4 years since his operation.
Kataria
R
R
Department of Peditatric Surgery, All India Institute of Medical Sciences, New Delhi, India.
Bhatnagar
V
V
Gupta
S D
SD
Mitra
D K
DK
D000714:Anastomosis, Surgical; D002648:Child; D005500:Follow-Up Studies; D006801:Humans; D007082:Ileum / Q000098:blood supply / Q000601:surgery; D008297:Male; D008643:Mesentery / Q000473:pathology* / Q000601:surgery; D009364:Neoplasm Recurrence, Local; D009455:Neurofibroma / Q000473:pathology* / Q000601:surgery; D009456:Neurofibromatosis 1 / Q000473:pathology*; D010534:Peritoneal Neoplasms / Q000473:pathology* / Q000601:surgery; D009418:S100 Proteins / Q000032:analysis; D014953:Wrist / Q000473:pathology
D009418:S100 Proteins