title: [Caroli's disease, congenital hepatic fibrosis and renal polycystosis: a little frequent association].
abstract: We report the case of a woman with Caroli's syndrome (Caroli's disease and congenital hepatic fibrosis) and adult polycystic kidney disease. Whereas the association of these two entities with autosomal-recessive-polycystic kidney disease has been widely reported, its association with adult-polycystic kidney disease is very infrequent.
authors.affiliation: Servicio de Medicina Interna. Hospital Universitario de Canarias. La Laguna, Tenerife.
authors.forename: E
authors.initials: E
authors.lastname: Rodríguez Rodríguez
authors.forename: F
authors.initials: F
authors.lastname: Santolaria Fernández
authors.forename: E
authors.initials: E
authors.lastname: González Reimers
authors.forename: H
authors.initials: H
authors.lastname: Alvarez Argüelles
authors.forename: M
authors.initials: M
authors.lastname: Cruz Díaz
authors.forename: F
authors.initials: F
authors.lastname: Rodríguez Moreno
authors.forename: J
authors.initials: J
authors.lastname: Oramas Rodríguez
mesh_terms: D000328:Adult; D016767:Caroli Disease / Q000150:complications* / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D008103:Liver Cirrhosis / Q000150:complications* / Q000151:congenital / Q000473:pathology; D007690:Polycystic Kidney Diseases / Q000150:complications* / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed
vernacular_title: Enfermedad de Caroli, fibrosis hepática congénita y poliquistosis renal: una asociación poco frecuente.