Pseudoxanthoma elasticum-like papillary dermal elastolysis. A report of two cases and review of the literature.
Pseudoxanthoma elasticum-like papillary dermal elastolysis is a peculiar idiopathic elastolytic disorder with cutaneous lesions clinically resembling pseudoxanthoma elasticum with partial or total band-like elastolysis of the papillary dermis histopathologically, and without systemic complications. We here report 2 new cases and review the clinicopathological features of patients with this diagnosis in the literature. The possible pathogenesis of this recently described entity is discussed.
Vargas-Díez
E
E
Department of Dermatology, Hospital Universitario de la Princesa, Madrid, Spain.
Peñas
P F
PF
Fraga
J
J
Aragües
M
M
García-Díez
A
A
D000368:Aged; D004547:Elastic Tissue / Q000473:pathology*; D005260:Female; D006801:Humans; D011561:Pseudoxanthoma Elasticum / Q000473:pathology*; D017444:Skin Diseases, Papulosquamous / Q000473:pathology