Congenital intrahepatic portocaval shunt associated with trimethylaminuria
A case of congenital portal-systemic shunting due to an intrahepatic connection diagnosed by ultrasound scanning and color Doppler in an 8-month-old girl is reported. She began to manifest trimethylaminuria 3 years later. At 7 years of age, she is asymptomatic without therapeutic measures except for diet. This is the seventh reported case and the third in a child to our knowledge.
Fernandez
MS
Departamento de Cirugia Pediatrica, Hospital Infantil "La Fe" de Valencia, Av. Campanar Ndegrees 21, 46009 Valencia, Spain
Gutierrez
C
Vila
JJ
Lopez
A
Ibanez
V
Sanguesa
C
Lluna
J
Barrios
JE