Cholecystoappendicostomy in a child with Alagille syndrome.
The authors performed a partial biliary diversion on a 10-month-old child with Alagille syndrome using the appendix vermiformis as a conduit between the gallbladder and the abdominal wall skin. Three years later the patient is well, and his previously severe pruritus is controlled. The appendix has a lumen closer to that of the biliary tree, does not accumulate significant amounts of bile, and provides a smaller stoma. The small bowel is undisturbed, and there is less interference with a possible future liver transplant.
Gauderer
M W
MW
Department of Pediatric Surgery, Children's Hospital, Greenville Hospital System, South Carolina 29605-4253, USA.
Boyle
J T
JT
D016738:Alagille Syndrome / Q000150:complications / Q000601:surgery*; D000714:Anastomosis, Surgical; D001065:Appendix / Q000601:surgery*; D005704:Gallbladder / Q000601:surgery*; D006801:Humans; D007223:Infant; D008297:Male; D011537:Pruritus / Q000209:etiology