Rhabdomyosarcoma of the biliary tree
Rhabdomyosarcoma (RMS) of the biliary tree is a rare tumor in children that has a very poor prognosis. Preoperatively, it is often mistaken for a choledochal cyst. We report a case of RMS of the biliary tree in a 4-year-old girl who presented with abdominal pain and obstructive jaundice. The RMS was diagnosed at laparotomy; excision was not possible due to its size and localization. Chemotherapy achieved complete regression of the tumor observed at second-look surgery. Preoperative chemotherapy can now avoid mutilating surgical procedures and improve survival.
Sanz
N
Department of Pediatric Surgery, Hospital Nino Jesus, C/Menendez Pelayo 65, E-28009 Madrid, Spain
de Mingo L
Florez
F
Rollan
V