[Caroli's disease, congenital hepatic fibrosis and renal polycystosis: a little frequent association].
We report the case of a woman with Caroli's syndrome (Caroli's disease and congenital hepatic fibrosis) and adult polycystic kidney disease. Whereas the association of these two entities with autosomal-recessive-polycystic kidney disease has been widely reported, its association with adult-polycystic kidney disease is very infrequent.
Rodríguez Rodríguez
E
E
Servicio de Medicina Interna. Hospital Universitario de Canarias. La Laguna, Tenerife.
Santolaria Fernández
F
F
González Reimers
E
E
Alvarez Argüelles
H
H
Cruz Díaz
M
M
Rodríguez Moreno
F
F
Oramas Rodríguez
J
J
D000328:Adult; D016767:Caroli Disease / Q000150:complications* / Q000000981:diagnostic imaging; D005260:Female; D006801:Humans; D008103:Liver Cirrhosis / Q000150:complications* / Q000151:congenital / Q000473:pathology; D007690:Polycystic Kidney Diseases / Q000150:complications* / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed
Enfermedad de Caroli, fibrosis hepática congénita y poliquistosis renal: una asociación poco frecuente.