Relapsing chronic low-dose corticosteroid-responsive multifocal motor neuropathy with conduction block.
Multifocal Motor Neuropathy (MMN) is a newly described disorder that might mimics the Motor Neuron Disease (MND). MMN is considered by some authors to be an entity distinct from Chronic Inflammatory Demyelinating Polyradiculoneuropathy (CIDP), nevertheless because a pure-motor variant of CIDP is well recognized and CIDP can present Partial Motor Conduction Block (PMCB), several authors believe that MMN can be a variant of CIDP. We describe a 27-year old male with a relapsing chronic low-dose corticosteroid-responsive MMN with conduction block. Our case stresses that MMN includes a wide range of motor neuropathies with different immunological profiles conditioning distinct treatment strategies.
de Carvalho
M
M
Department of Neurology, Centro de Estudos Egas Moniz, Hospital de Santa Mara, Lisbon, Portugal.
Luís
M L
ML
D000305:Adrenal Cortex Hormones / Q000627:therapeutic use*; D000328:Adult; D006801:Humans; D008297:Male; D008475:Median Nerve / Q000503:physiopathology*; D016472:Motor Neuron Disease / Q000188:drug therapy*; D009431:Neural Conduction / Q000502:physiology*; D012008:Recurrence; D013997:Time Factors
D000305:Adrenal Cortex Hormones