Acute intrahepatic portal vein thrombosis complicating cholangitis in biliary atresia.
A 2-year-old boy with Kasai portoenterostomy had systemic features suggestive of cholangitis and acute portal vein obstruction. The rapid rise in portal pressure caused a transient, severe decompensation of hepatic function. A superior mesenteric arterial angiogram confirmed the presence of diffuse intrahepatic portal vein thrombosis.


CONCLUSIONS
This case provides clinical and radiological evidence supporting an association between ascending cholangitis and acute intrahepatic portal vein thrombosis.
Cuffari
C
C
Service de Gastroentérologie-Nutrition, Hôpital Sainte-Justine, Montréal (Québec), Canada.
Seidman
E
E
DuBois
J
J
Brochu
P
P
Alvarez
F
F
D001656:Biliary Atresia / Q000473:pathology / Q000601:surgery*; D001706:Biopsy; D002675:Child, Preschool; D002761:Cholangitis / Q000175:diagnosis* / Q000473:pathology; D006801:Humans; D008099:Liver / Q000473:pathology; D008105:Liver Cirrhosis, Biliary / Q000175:diagnosis / Q000473:pathology; D008297:Male; D011169:Portal Vein / Q000473:pathology; D011171:Portoenterostomy, Hepatic; D011172:Portography; D011183:Postoperative Complications / Q000175:diagnosis* / Q000473:pathology; D013927:Thrombosis / Q000175:diagnosis* / Q000473:pathology