[Neurosurgical aspects of Rendu-Osler disease. Apropos of 6 recent cases and review of the literature].
Six patients with neurological complications in Rendu-Osler-Weber disease were reviewed. There were 4 patients (3 int the same family) with a brain abscess, one patient with a brain abscess and a spinal cord subarachnoid hemorrhage, one patient with a recurrent intracerebral hemorrhage due to a vascular malformation. The infectious complications are related to the presence of pulmonary arterio-venous fistula, which should be treated, whenever diagnosed. Because of the potentially severe outcome of these neurological complications of the Rendu-Osler-Weber disease, screening of the patient's relatives is highly recommended.
Emery
E
E
Service de Neurochirurgie, Hôpital Beaujon, Clichy.
Redondo
A
A
Ouahes
O
O
Berthelot
J L
JL
Bouali
I
I
Rey
A
A
D000328:Adult; D001922:Brain Abscess / Q000209:etiology* / Q000601:surgery; D002561:Cerebrovascular Disorders / Q000209:etiology* / Q000601:surgery; D002648:Child; D005260:Female; D006801:Humans; D008297:Male; D008875:Middle Aged; D013683:Telangiectasia, Hereditary Hemorrhagic / Q000150:complications* / Q000235:genetics / Q000601:surgery
Aspects neurochirurgicaux de la maladie de Rendu-Osler. A propos de 6 cas récents et revue de la littérature.