Corneal abnormalities associated with incontinentia pigmenti.
OBJECTIVE
To report corneal abnormalities associated with incontinentia pigmenti.


METHODS
Two girls, aged 2 1/2 and 5 years, with incontinentia pigmenti from one family underwent a complete ophthalmic examination.


RESULTS
We found vortex (whorl-like) epithelial keratitis characterized by epithelial microcysts that stained with fluorescein and midstromal radial mild haziness in daughters of a family with incontinentia pigmenti.


CONCLUSIONS
Incontinentia pigmenti should be included in the differential diagnosis of children with keratitis, particularly if there is evidence of characteristic dermatologic or other systemic manifestations.
Ferreira
R C
RC
Department of Ophthalmology, Federal University of São Paulo.
Ferreira
L C
LC
Forstot
L
L
King
R
R
D002675:Child, Preschool; D003315:Cornea / Q000002:abnormalities* / Q000473:pathology; D003316:Corneal Diseases / Q000209:etiology* / Q000473:pathology; D003560:Cysts / Q000209:etiology / Q000473:pathology; D005260:Female; D006801:Humans; D007184:Incontinentia Pigmenti / Q000150:complications* / Q000473:pathology; D007634:Keratitis / Q000209:etiology / Q000473:pathology