Monomelic amyotrophy following trauma and immobilization in children.
Two children aged 9 and 11 years suffered from left elbow sprain and right anterior tibial tuberosity cortical fracture respectively and were treated with plaster cast immobilization for about 30 days. They regained normal strength afterwards, but 9 and 2 months later developed insidious progressive weakness and wasting in the affected limb, mainly evident in the musculature surrounding the site of injury and sparing hand and foot muscles. Two to three years later the condition stabilized. Sensory abnormalities were not found. Electromyographic examination showed neurogenic pattern confined to the impaired extremity. The focal quality and the unusual disposition of muscle involvement suggest a correlation between trauma and/or immobilization and monomelic amyotrophy.
Paradiso
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Department of Neurology, Hospital Nacional de Pediatría Jaun Garrahan,Buenos Aires, Argentina.
D000293:Adolescent; D002370:Casts, Surgical / Q000009:adverse effects*; D002648:Child; D004551:Elbow Joint; D004576:Electromyography; D005073:Evoked Potentials, Somatosensory; D005500:Follow-Up Studies; D006801:Humans; D007103:Immobilization / Q000009:adverse effects*; D008297:Male; D016472:Motor Neuron Disease / Q000209:etiology* / Q000503:physiopathology; D018482:Muscle, Skeletal / Q000503:physiopathology; D009431:Neural Conduction; D013180:Sprains and Strains / Q000601:surgery*; D013978:Tibial Fractures / Q000601:surgery*; D013997:Time Factors