title: Corneal abnormalities associated with incontinentia pigmenti.
abstract: OBJECTIVE
  To report corneal abnormalities associated with incontinentia pigmenti.
  
  
  METHODS
  Two girls, aged 2 1/2 and 5 years, with incontinentia pigmenti from one family underwent a complete ophthalmic examination.
  
  
  RESULTS
  We found vortex (whorl-like) epithelial keratitis characterized by epithelial microcysts that stained with fluorescein and midstromal radial mild haziness in daughters of a family with incontinentia pigmenti.
  
  
  CONCLUSIONS
  Incontinentia pigmenti should be included in the differential diagnosis of children with keratitis, particularly if there is evidence of characteristic dermatologic or other systemic manifestations.
authors.affiliation: Department of Ophthalmology, Federal University of São Paulo.
authors.forename: R C
authors.initials: RC
authors.lastname: Ferreira
authors.forename: L C
authors.initials: LC
authors.lastname: Ferreira
authors.forename: L
authors.initials: L
authors.lastname: Forstot
authors.forename: R
authors.initials: R
authors.lastname: King
mesh_terms: D002675:Child, Preschool; D003315:Cornea / Q000002:abnormalities* / Q000473:pathology; D003316:Corneal Diseases / Q000209:etiology* / Q000473:pathology; D003560:Cysts / Q000209:etiology / Q000473:pathology; D005260:Female; D006801:Humans; D007184:Incontinentia Pigmenti / Q000150:complications* / Q000473:pathology; D007634:Keratitis / Q000209:etiology / Q000473:pathology