title: Coexistence of a graft with the preserved native liver in auxiliary partial orthotopic liver transplantation from a living donor for ornithine transcarbamylase deficiency.
abstract: BACKGROUND
  Auxiliary partial orthotopic liver transplantation (APOLT) has recently been performed in patients with noncirrhotic metabolic liver diseases. However, long-term outcomes for the preserved native liver and the transplanted liver graft have not been clearly established yet.
  
  
  METHODS
  The recipient was a 36-month-old girl with ornithine transcarbamylase deficiency. She underwent APOLT, using her father's left lateral segment.
  
  
  RESULTS
  Liver function was normalized soon after APOLT and the patient was able to ingest a normal diet without medication. Coexistence of the well-functioning native liver and graft was demonstrated in a computed tomography scan, Doppler ultrasonography, scintigraphy, and histological examination, during a relatively long-term follow-up period.
  
  
  CONCLUSIONS
  APOLT seems to be most useful for the treatment of noncirrhotic metabolic liver diseases.
authors.affiliation: Department of Transplantation and Immunology, Kyoto University Graduate School of Medicine, Kyoto University Hospital, Shogoin, Sakyo-ku, Japan.
authors.forename: S
authors.initials: S
authors.lastname: Uemoto
authors.forename: S
authors.initials: S
authors.lastname: Yabe
authors.forename: Y
authors.initials: Y
authors.lastname: Inomata
authors.forename: H
authors.initials: H
authors.lastname: Nishizawa
authors.forename: K
authors.initials: K
authors.lastname: Asonuma
authors.forename: H
authors.initials: H
authors.lastname: Egawa
authors.forename: T
authors.initials: T
authors.lastname: Kiuchi
authors.forename: H
authors.initials: H
authors.lastname: Okajima
authors.forename: Y
authors.initials: Y
authors.lastname: Yamaoka
authors.forename: H
authors.initials: H
authors.lastname: Yamabe
authors.forename: A
authors.initials: A
authors.lastname: Inui
authors.forename: T
authors.initials: T
authors.lastname: Fujisawa
authors.forename: K
authors.initials: K
authors.lastname: Tanaka
mesh_terms: D001706:Biopsy; D002675:Child, Preschool; D005260:Female; D006801:Humans; D008099:Liver / Q000000981:diagnostic imaging / Q000473:pathology / Q000502:physiology*; D016031:Liver Transplantation / Q000000981:diagnostic imaging / Q000379:methods / Q000473:pathology / Q000502:physiology*; D020163:Ornithine Carbamoyltransferase Deficiency Disease; D011859:Radiography