Non-operative management of a splenic laceration in a patient with the Proteus syndrome.
An adult patient with the Proteus syndrome sustained a grade III splenic laceration after falling off a horse. Clinical features of this rare disorder include subcutaneous and visceral hamartomatous tumours. The patient also suffered from chronic intravascular coagulation associated with extensive haemangiomatosis (Kasabach-Merritt syndrome). Considering the visceral anomalies and abnormal coagulation, a non-operative approach was preferred despite considerable transfusion requirement, and the patient successfully underwent embolisation of the splenic artery. This is the first reported case of splenic injury in a patient with Proteus syndrome.
Ceelen
W
W
Department of Surgery, University Hospital, Gent University Medical School, Belgium.
De Waele
J
J
Kunnen
M
M
de Hemptinne
B
B
D000328:Adult; D004621:Embolization, Therapeutic; D006801:Humans; D008297:Male; D016715:Proteus Syndrome / Q000150:complications*; D013154:Spleen / Q000293:injuries*; D014949:Wounds, Nonpenetrating / Q000628:therapy*