Chronic thromboembolic pulmonary hypertension and vascular transformation of the lymph node sinuses.
Chronic thromboembolic pulmonary hypertension (CTEPH) is a disease often not recognized until it is far advanced. Medical management does not reverse the effects of the disease, nor does it prevent its progression. Pulmonary thromboendarterectomy is the preferred treatment. We present the case of a patient in whom CTEPH was mistaken for an interstitial lung disease with mediastinal lymph node enlargement. The mediastinal lymph node enlargement was due to vascular transformation of the lymph node sinuses (VTS). This is an unusual case of chronic thromboembolic pulmonary hypertension with vascular transformation of the lymph node sinuses.
Meysman
M
M
Dept of Internal Medicine, Academic Hospital, University of Brussels (AZ-VUB), Belgium.
Diltoer
M
M
Raeve
H D
HD
Monsieur
I
I
Huyghens
L
L
D000328:Adult; D002908:Chronic Disease; D003937:Diagnosis, Differential; D006801:Humans; D006976:Hypertension, Pulmonary / Q000175:diagnosis* / Q000209:etiology*; D017563:Lung Diseases, Interstitial / Q000175:diagnosis; D008198:Lymph Nodes / Q000098:blood supply / Q000473:pathology; D008297:Male; D013923:Thromboembolism / Q000175:diagnosis*; D014652:Vascular Diseases / Q000473:pathology