Otolaryngological manifestation of Gorlin Goltz syndrome.
A 46-year-old Jordanian man was seen in ENT clinic complaining of progressive left nasal obstruction and hearing loss for the last five years with a history of multiple surgical removal of dental cysts. Clinical and radiological investigation revealed a cystic mass occupying the left maxillary sinus protruding to the nasal cavity, calcification of the falx cerebri and bifid ribs. On these findings Gorlin-Goltz syndrome was confirmed. The case is presented and the literature reviewed.
al-Anazy
F H
FH
Department of ORL, King Abdul Aziz University Hospital, Riyadh, Kingdom of Saudia Arabia.
Zakzouk
S M
SM
D001478:Basal Cell Nevus Syndrome / Q000150:complications* / Q000473:pathology; D003560:Cysts / Q000150:complications* / Q000473:pathology; D006319:Hearing Loss, Sensorineural / Q000150:complications* / Q000473:pathology; D006801:Humans; D008297:Male; D008875:Middle Aged; D009296:Nasal Cavity