title: [Congenital asplenia. A childhood immune deficit often detected too late].
abstract: We report a case of fatal pneumococcal sepsis in a previously healthy 22 month old child. At postmorten examination the patient was found to have an atrophic spleen. When other malformations are not associated, congenital asplenia is generally diagnosed after death related to pneumococcal infection.
authors.affiliation: Service d'Anatomie et de Cytologie Pathologiques, Hôpital Necker-Enfants Malades, Paris.
authors.forename: S
authors.initials: S
authors.lastname: Ferlicot
authors.forename: J F
authors.initials: JF
authors.lastname: Emile
authors.forename: J L
authors.initials: JL
authors.lastname: Le Bris
authors.forename: G
authors.initials: G
authors.lastname: Chéron
authors.forename: N
authors.initials: N
authors.lastname: Brousse
mesh_terms: D017809:Fatal Outcome; D006801:Humans; D007107:Immune System / Q000502:physiology*; D007223:Infant; D008297:Male; D013154:Spleen / Q000002:abnormalities*
vernacular_title: L'asplénie congénitale. Un déficit immunitaire de l'enfant de découverte souvent trop tardive.