Rhabdomyosarcoma of the biliary tree.
Rhabdomyosarcoma (RMS) of the biliary tree is a rare tumor in children that has a very poor prognosis. Preoperatively, it is often mistaken for a choledochal cyst. We report a case of RMS of the biliary tree in a 4-year-old girl who presented with abdominal pain and obstructive jaundice. The RMS was diagnosed at laparotomy; excision was not possible due to its size and localization. Chemotherapy achieved complete regression of the tumor observed at second-look surgery. Preoperative chemotherapy can now avoid mutilating surgical procedures and improve survival.
Sanz
N
N
Department of Pediatric Surgery, Hospital Niño Jesús, C/Menéndez Pelayo 65, E-28009 Madrid, Spain.
de Mingo
L
L
Flórez
F
F
Rollán
V
V
D000713:Anastomosis, Roux-en-Y; D001650:Bile Duct Neoplasms / Q000188:drug therapy / Q000473:pathology / Q000601:surgery*; D017734:Bile Ducts, Extrahepatic / Q000473:pathology / Q000601:surgery*; D016026:Bone Marrow Transplantation; D017024:Chemotherapy, Adjuvant; D002675:Child, Preschool; D003131:Combined Modality Therapy; D005260:Female; D006801:Humans; D009367:Neoplasm Staging; D012208:Rhabdomyosarcoma / Q000188:drug therapy / Q000473:pathology / Q000601:surgery*