The ectrodactyly-ectodermal dysplasia-clefting syndrome: a literature review and case report.
Ectrodactyly, atypical anhidrotic ectodermal dysplasia, and cleft lip and palate are the principal manifestations of ectrodactyly-ectodermal dysplasia-clefting syndrome. Intraorally, the common manifestations of the syndrome are hypodontia, enamel hypoplasia, and generalized microdontia. In addition, the patient may suffer from xerostomia and have a deeply fissured tongue. The oral mucosa appears, in some patients, to have an increased susceptibility to candidiasis. This case report describes a patient who exhibits many of the manifestations of the syndrome and explains ways in which many of the anomalies of the dentition can be esthetically and functionally corrected.
King
N M
NM
Department of Children's Dentistry and Orthodontics, University of Hong Kong, Faculty of Dentistry, Prince Philip Dental Hospital, Hong Kong.
Tong
M C
MC
Ling
J Y
JY
D000015:Abnormalities, Multiple; D000293:Adolescent; D000848:Anodontia / Q000628:therapy; D002971:Cleft Lip / Q000150:complications; D002972:Cleft Palate / Q000150:complications; D004476:Ectodermal Dysplasia; D005385:Fingers / Q000002:abnormalities; D005532:Foot Deformities, Congenital; D006228:Hand Deformities, Congenital; D006801:Humans; D008297:Male; D008313:Malocclusion, Angle Class III / Q000209:etiology / Q000628:therapy*; D009971:Orthodontics, Corrective / Q000379:methods; D013577:Syndrome; D014034:Toes / Q000002:abnormalities; D014071:Tooth Abnormalities