Idiopathic restrictive cardiomyopathy with diffuse perimyocytic fibrosis--a rare observation.
Idiopathic restrictive cardiomyopathy (RCM) is rare. Even today little is understood of its etiology or underlying mechanisms, and definitive diagnostic criteria are lacking. In this report, we describe a case of idiopathic RCM in a young Japanese woman who died while awaiting cardiac transplantation during the 5-year course of the disease. Rare pathologic findings of diffuse perimyocytic fibrosis were revealed at autopsy.
Suzuki
T
T
Department of Cardiology, Sakakibara Heart Institute, Tokyo, Japan.
Ohtaki
E
E
Murai
T
T
Imai
M
M
Kawai
S
S
Kitaoka
M
M
Kitahara
K
K
Okada
R
R
Suzuki
S
S
D000328:Adult; D002313:Cardiomyopathy, Restrictive / Q000209:etiology / Q000473:pathology*; D005260:Female; D005355:Fibrosis; D006352:Heart Ventricles / Q000473:pathology; D006801:Humans; D009206:Myocardium / Q000473:pathology*