Retroperitoneal lymphangiomyoma in an infant.
Lymphangiomyomatosis (LAM) is a benign tumor-like lesion of lymphatic vessels with unknown etiology. 80 cases of LAM are presently described. So far, it appears that only women in their reproductive years seem to be affected. Here, we describe the first LAM in an 11-months-old infant with a presumably local form of LAM. This leads us to consider the possibility that this tumor-like lesion may originate from a hamartomateous malformation. The diagnosis is based on pre-operative sonography and CT, as well as on histological and immunohistochemical examination of the tumor.
Fuchs
J
J
Department of Pediatric Surgery, Hannover Medical School, Germany.
Maschek
H
H
von Schweinitz
D
D
Glüer
S
S
Mildenberger
H
H
D005260:Female; D006801:Humans; D007223:Infant; D008203:Lymphangiomyoma / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery; D010534:Peritoneal Neoplasms / Q000175:diagnosis / Q000473:pathology* / Q000601:surgery; D010537:Peritoneum / Q000473:pathology* / Q000601:surgery; D014057:Tomography, X-Ray Computed; D014463:Ultrasonography