Right outflow tract obstruction by a pedunculated neurofibroma: case report and literature review.
Right outflow tract obstruction due to neurofibroma is rare, with only four cases identified in the world literature. Obstruction due to a pedunculated neurofibroma has never been reported. A 36-year-old woman with no known heart disease presenting with dyspnea, palpitations and chest pain was shown on echocardiogram to have a mobile right ventricular mass. Cardiac catheterization revealed normal coronary arteries and right ventricular outflow tract obstruction by a pedunculated mass, which was surgically removed and histologically proven to be a benign neurofibroma. Following surgery the patient's symptoms disappeared, with no recurrence three years postoperatively.
Henderson
W
W
Vancouver Hospital, British Columbia.
Huckell
V F
VF
English
J C
JC
Fradet
G
G
D000328:Adult; D000790:Angiocardiography; D005260:Female; D006338:Heart Neoplasms / Q000150:complications* / Q000473:pathology; D006352:Heart Ventricles / Q000000981:diagnostic imaging / Q000473:pathology; D006801:Humans; D018810:Magnetic Resonance Angiography; D009455:Neurofibroma / Q000150:complications* / Q000473:pathology; D014694:Ventricular Outflow Obstruction / Q000000981:diagnostic imaging / Q000209:etiology*