The surgical management of incomplete testicular feminization syndrome in three sisters.
Three sisters with incomplete testicular feminization syndrome are presented. Most of the patients with this syndrome are females and surgery is an important part of their multidisciplinary treatment. Two of the sisters had gonadectomies, herniorrhaphies, vaginoplasty with neurovascular pudendal thigh flaps, reduction clitoroplasty and labia minora reconstruction. The third sister had sufficient vaginal depth and had release of an introitus skin web, clitoroplasty and labia minora reconstruction. All patients had a good result. The reconstructed vaginas are stable and sensate.
Velidedeoğlu
H V
HV
Department of Plastic and Reconstructive Surgery, Social Insurance Association Hospital of Ankara, Turkey.
Coşkunfirat
O K
OK
Bozdoğan
M N
MN
Sahin
U
U
Türkgüven
Y
Y
D000293:Adolescent; D000328:Adult; D013734:Androgen-Insensitivity Syndrome / Q000235:genetics / Q000473:pathology / Q000601:surgery*; D002987:Clitoris / Q000601:surgery; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D008297:Male; D009919:Orchiectomy; D013524:Surgical Flaps / Q000379:methods; D014621:Vagina / Q000601:surgery