[Melkersson-Rosenthal syndrome. Presentation of a clinical case and review of the literature].
Melkersson-Rosenthal syndrome is a rare form of hereditary angioedema characterised by a triad of symptoms of which incomplete (oligo- or monosymptomatic) forms have been described, frequently associated with dysreactive diseases or neoplasia. The authors describe the case of a 48-year-old man with an incomplete form which was successfully treated with steroids and, after a careful and detailed revision of the literature on the subject, they make a number of etiopathogenetic, histopathological, clinical and therapeutic comments.
Nifosì
G
G
Ospedale di Nizza Monferrató (Asti), Azienda USL, Asti.
Scassa
E
E
D006801:Humans; D008297:Male; D008556:Melkersson-Rosenthal Syndrome / Q000150:complications / Q000188:drug therapy / Q000276:immunology; D008875:Middle Aged