[Ectodermal dysplasia: multiple manifestations of a hereditary disease].
Ectodermal dysplasia is a hereditary disease that can manifest itself in many ways. Four cases, including two cases involving heterozygote twins, are presented. The clinical signs of the disease, as observed are compared to the knowledge offered in the classic and modern literature. Special attention is given to the intraoral manifestations of the disease, and to the solutions that a multidisciplinary dental team could consider to improve the masticatory function and the facial esthetics of patients affected by this disease.
Ouellet
B
B
Hôpital Ste-Justine.
Agha-Amiri
M
M
Dubé-Baril
C
C
Mascrès
C
C
D000848:Anodontia / Q000209:etiology*; D002648:Child; D002675:Child, Preschool; D017742:Dental Care for Chronically Ill; D004200:Diseases in Twins / Q000235:genetics; D004476:Ectodermal Dysplasia / Q000150:complications* / Q000235:genetics; D005260:Female; D006801:Humans; D007039:Hypotrichosis / Q000209:etiology; D008297:Male; D009264:Nails, Malformed; D010375:Pedigree