[A rare cause of chronic respiratory insufficiency: arthrogryposis in adults].
Arthrogryposis is a congenital disease leading to multiple joint ankylosis in utero observed as sequellae at birth. Deformation of the chest produces respiratory failure usually seen at birth. We report a case in an adult which required intermittent nocturnal positive pressure nasal ventilation.
Rivaud
E
E
Strecker
A
A
Mallart
A
A
Vallet
L
L
Lafitte
J J
JJ
D000328:Adult; D000367:Age Factors; D001176:Arthrogryposis / Q000150:complications*; D002908:Chronic Disease; D006801:Humans; D007385:Intermittent Positive-Pressure Ventilation; D007738:Kyphosis / Q000150:complications / Q000503:physiopathology; D008297:Male; D012131:Respiratory Insufficiency / Q000209:etiology* / Q000628:therapy