Association of Sjögren's syndrome with hereditary angioneurotic edema: report of a case.
A case of hereditary angioneurotic edema (HANE) associated with Sjögren's syndrome is presented. One of the members of a pedigree of HANE due to deficiency of C1 inhibitor (C1INH) had a positive titer for anti-SS-A and anti-SS-B antibodies in the serum, complaining of symptom of dry eyes and dry mouth. A lip biopsy revealed lymphocytic infiltration of minor salivary glands. The patient had renal tubular acidosis (RTA). Thus the patient was diagnosed as suffering from Sjögren's syndrome with RTA.
Suzuki
Y
Y
Faculty of Home Economics, Otsuma Women's University, Tokyo, Japan.
Hinoshita
F
F
Yokoyama
K
K
Katori
H
H
Ubara
Y
Y
Hara
S
S
Ogura
Y
Y
Yamada
A
A
D000799:Angioedema / Q000235:genetics* / Q000276:immunology*; D003169:Complement Inactivator Proteins / Q000172:deficiency / Q000235:genetics; D005260:Female; D006801:Humans; D008180:Lupus Erythematosus, Systemic / Q000235:genetics / Q000276:immunology; D008875:Middle Aged; D010375:Pedigree; D012859:Sjogren's Syndrome / Q000235:genetics / Q000276:immunology*
D003169:Complement Inactivator Proteins