Hypertension secondary to progressive vascular neurofibromatosis.
A 4 year old girl with neurofibromatosis type 1 (NF1) was referred for hypertension. An aortogram showed narrowing of the left main renal artery. An angiogram three and a half years later showed coarctation of the abdominal aorta. She underwent aortoplasty but the stenosis recurred. Vascular involvement in NF1 may be progressive and requires long term follow up.
Kurien
A
A
Department of Nephrology, Birmingham Children's Hospital, Ladywood Middleway.
John
P R
PR
Milford
D V
DV
D001012:Aorta, Abdominal / Q000000981:diagnostic imaging; D001017:Aortic Coarctation / Q000000981:diagnostic imaging / Q000209:etiology; D002675:Child, Preschool; D018450:Disease Progression; D005260:Female; D005500:Follow-Up Studies; D006801:Humans; D006973:Hypertension / Q000209:etiology*; D006978:Hypertension, Renovascular / Q000209:etiology; D008134:Long-Term Care; D009456:Neurofibromatosis 1 / Q000150:complications*; D011859:Radiography