title: Otodental syndrome.
abstract: Otodental dysplasia, a form of ectodermal dysplasia, is characterized by abnormal dental crown morphology and sensorineural hearing loss. A variety of dental abnormalities are prominent features of this syndrome--most notably gigantic, bulbous posterior teeth. In this case, a sibling is identifies in a family with otodental syndrome that had been diagnosed earlier. A unique opportunity is provided to view the intact adult dentition and possible complications for dental treatment.
authors.affiliation: Goodfellow Air Force Base, Texas, USA.
authors.forename: A J
authors.initials: AJ
authors.lastname: Mesaros
authors.forename: J W
authors.initials: JW
authors.lastname: Basden
mesh_terms: D000293:Adolescent; D004476:Ectodermal Dysplasia / Q000235:genetics / Q000473:pathology*; D005192:Family Health; D006319:Hearing Loss, Sensorineural / Q000235:genetics; D006801:Humans; D008297:Male; D008963:Molar / Q000002:abnormalities*; D013577:Syndrome; D014071:Tooth Abnormalities / Q000235:genetics* / Q000473:pathology; D019228:Tooth Crown / Q000002:abnormalities*