title: Association of Sjögren's syndrome with hereditary angioneurotic edema: report of a case.
abstract: A case of hereditary angioneurotic edema (HANE) associated with Sjögren's syndrome is presented. One of the members of a pedigree of HANE due to deficiency of C1 inhibitor (C1INH) had a positive titer for anti-SS-A and anti-SS-B antibodies in the serum, complaining of symptom of dry eyes and dry mouth. A lip biopsy revealed lymphocytic infiltration of minor salivary glands. The patient had renal tubular acidosis (RTA). Thus the patient was diagnosed as suffering from Sjögren's syndrome with RTA.
authors.affiliation: Faculty of Home Economics, Otsuma Women's University, Tokyo, Japan.
authors.forename: Y
authors.initials: Y
authors.lastname: Suzuki
authors.forename: F
authors.initials: F
authors.lastname: Hinoshita
authors.forename: K
authors.initials: K
authors.lastname: Yokoyama
authors.forename: H
authors.initials: H
authors.lastname: Katori
authors.forename: Y
authors.initials: Y
authors.lastname: Ubara
authors.forename: S
authors.initials: S
authors.lastname: Hara
authors.forename: Y
authors.initials: Y
authors.lastname: Ogura
authors.forename: A
authors.initials: A
authors.lastname: Yamada
mesh_terms: D000799:Angioedema / Q000235:genetics* / Q000276:immunology*; D003169:Complement Inactivator Proteins / Q000172:deficiency / Q000235:genetics; D005260:Female; D006801:Humans; D008180:Lupus Erythematosus, Systemic / Q000235:genetics / Q000276:immunology; D008875:Middle Aged; D010375:Pedigree; D012859:Sjogren's Syndrome / Q000235:genetics / Q000276:immunology*
chemical_list: D003169:Complement Inactivator Proteins