Severe pulmonary hypertension: a feature of Swyer-James syndrome?
Swyer-James syndrome, unilateral hyperlucent lung with air entrapment, generally occurs after severe infections during childhood. It is usually diagnosed by its characteristic chest radiographic image film or computed tomography, in patients who are almost asymptomatic. We report a case of Swyer-James syndrome, diagnosed from the study of severe pulmonary hypertension and with a fatal outcome.
Fernández Fabrellas
E
E
Dept of Penumology, Hospital Doctor Peset, Valencia, Spain.
Marín González
M
M
Almenar Bonet
L
L
Blanquer Olivas
R
R
D000328:Adult; D017809:Fatal Outcome; D005260:Female; D006061:Gonadal Dysgenesis, 46,XY / Q000150:complications* / Q000000981:diagnostic imaging; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology*; D008168:Lung / Q000002:abnormalities* / Q000000981:diagnostic imaging; D014057:Tomography, X-Ray Computed