Surgical correction of incomplete cryptophthalmos in Fraser syndrome.
OBJECTIVE
To demonstrate favorable long-term visual outcome after ocular reconstruction in an infant with Fraser syndrome and with complete left cryptophthalmos.


METHODS
Reconstruction of incomplete right cryptophthalmos in our patient was accomplished in a stepwise manner, beginning in the third week of life, by dissecting the eyelids from the cornea, reconstructing the conjunctival fornices with buccal mucosa, and repairing the upper lid coloboma in a flap reconstruction using the inferior eyelid margin.


RESULTS
At age 3 years, the patient currently has good movement of the right eyelids when blinking, reasonable right tear function, and a visual acuity in the right eye between 20/200 and 20/360 on forced preferential looking.


CONCLUSIONS
In selected cases of incomplete cryptophthalmos, oculoplastic and corneal surgery may result in useful vision and in good eyelid movement when blinking.
Dibben
K
K
Cornea-Genetic Eye Medical Clinic, Los Angeles, CA 90048, USA.
Rabinowitz
Y S
YS
Shorr
N
N
Graham
J M
JM
D000015:Abnormalities, Multiple / Q000601:surgery; D002675:Child, Preschool; D019465:Craniofacial Abnormalities / Q000150:complications*; D005124:Eye Abnormalities / Q000150:complications / Q000601:surgery*; D005143:Eyelids / Q000002:abnormalities* / Q000601:surgery*; D006801:Humans; D008297:Male; D013524:Surgical Flaps / Q000379:methods; D013576:Syndactyly / Q000150:complications*; D013577:Syndrome; D014564:Urogenital Abnormalities; D014792:Visual Acuity