[Imaging aspect of a case of fibrodysplasia ossificans progressiva].
Fibrodysplasia ossificans progressiva is a rare congenital disease that affects children under the age of five years. Soft tissue swelling of the cervical and dorsal regions with local pain, warmth and low grade fever are the early clinical manifestations, usually associated with hallux valgus and microdactily of the fingers and toes. Calcifications of the fascias and muscles cause muscular contractures leading to progressive disability and restrictive lung disease. In the early stage, CT shows edema of the soft tissues and later on, calcifications of muscular fascia. The association of these radiographic and CT findings is specific and should avoid muscular biopsies which are known to be an aggravating factor in this disease.
Haddad
S
S
Service de Radiologie, Hôtel-Dieu de France, Beyrouth, Liban.
Menassa
L
L
Nasnas
R
R
Abadjian
G
G
Slaba
S
S
Atallah
N
N
D002114:Calcinosis / Q000000981:diagnostic imaging; D002675:Child, Preschool; D004487:Edema / Q000000981:diagnostic imaging; D006801:Humans; D008279:Magnetic Resonance Imaging; D008297:Male; D009221:Myositis Ossificans / Q000175:diagnosis / Q000000981:diagnostic imaging*; D013997:Time Factors; D014057:Tomography, X-Ray Computed
Aspect en imagerie d'un cas de fibrodysplasie ossifiante progressive.