Systemic mast cell disease associated with hairy cell leukaemia.
Systemic mast cell disease (SMCD) can be regarded as a tumorous proliferation of tissue mast cells involving various organs. The frequency with which SMCD is found in patients with haematological disorders suggests that the association is non-random. The association includes primarily, myeloid disorders such as myelodysplastic syndromes and acute or chronic myeloproliferative disorders. Lymphoproliferative disorders may also occur but more rarely, mostly non-Hodgkin's low grade B cell lymphomas. In this report a case is described in which SMCD occurred in a patient with hairy cell leukaemia.
Petrella
T
T
Laboratory of Pathology, Centre Hospitalo-Universitaire and Centre de Pathologie de Dijon, France.
Depret
O
O
Arnould
L
L
Maynadie
M
M
Guy
H
H
Dalac
S
S
Caillot
D
D
Casasnovas
O
O
Lombard
J N
JN
D006801:Humans; D007943:Leukemia, Hairy Cell / Q000150:complications*; D008297:Male; D008415:Mastocytosis / Q000150:complications*; D008875:Middle Aged