First report of distal obstructive uropathy and prune-belly syndrome in an infant with amniotic band syndrome.
We describe the first report of distal obstructive uropathy and prune-belly syndrome in an infant with amniotic band syndrome. Prenatal ultrasonographic examination in the third trimester revealed intermittent oligohydramnios, bilateral hydronephrosis, and megacystis. Postnatally, the infant was found to have a scalp defect, a skin pedicle, pseudosyndactyly and constriction rings on the hands, marked distention of the abdomen, a fibrous band attached to the proximal urethra causing urethral stricture, a swollen penile shaft, bilateral talipes equinovarus, and syndactyly of the feet. Multiple fibrous amniotic bands could be identified in the placenta. Our case shows that fetal distal obstructive uropathy can be associated with the congenital constriction band syndrome.
Chen
C P
CP
Department of Obstetrics and Gynecology, Mackay Memorial Hospital, Taipei, Taiwan, Republic of China.
Liu
F F
FF
Jan
S W
SW
Wang
K G
KG
Lan
C C
CC
D000328:Adult; D000652:Amniotic Band Syndrome / Q000150:complications* / Q000000981:diagnostic imaging / Q000473:pathology; D003025:Clubfoot / Q000473:pathology; D005260:Female; D005315:Fetal Diseases / Q000000981:diagnostic imaging; D005385:Fingers / Q000002:abnormalities; D006228:Hand Deformities, Congenital / Q000209:etiology; D006801:Humans; D006869:Hydronephrosis / Q000000981:diagnostic imaging; D007231:Infant, Newborn; D008297:Male; D016104:Oligohydramnios / Q000000981:diagnostic imaging; D010409:Penile Diseases / Q000209:etiology; D010920:Placenta / Q000473:pathology; D011247:Pregnancy; D011535:Prune Belly Syndrome / Q000209:etiology*; D012535:Scalp / Q000002:abnormalities; D012868:Skin Abnormalities; D013576:Syndactyly / Q000209:etiology; D014034:Toes / Q000002:abnormalities; D016216:Ultrasonography, Prenatal; D014525:Urethral Stricture / Q000209:etiology*; D001743:Urinary Bladder / Q000002:abnormalities / Q000000981:diagnostic imaging