Cystic rectal duplication: a rare cause of neonatal intestinal obstruction.
A case of cystic rectal duplication revealed on day 2 of life by a low intestinal occluding syndrome is reported. Radiologic imaging (ultrasonography, cystography, rectography) showed a large, retrorectal liquid formation in the pelvis and abdomen, with pelvic compression of the terminal alimentary canal and lower urinary tract. Magnetic resonance imaging demonstrated a liquid formation with clearly defined edges and no medullary involvement, thus ruling out the possibility of a previous meningeal hernia. Biological markers were within normal limits. On day 4, a 9 x 6-cm cystic rectal duplication was removed, followed by a temporary colostomy. Pathologic examination demonstrated typical rectal architecture with ciliated cells. Radiologic and clinical findings at 2-month follow-up were reassuring. This case report is exceptional for the following reasons: (1) As a rule, rectal duplications are relatively rare (70 cases reported in the literature); (2) The means of disclosing a neonatal rectal duplication is unusual (4 cases reported in the literature); (3) The volume of the malformation was considerable; and (4) Heterotopic ciliated epithelium was present.
Mboyo
A
A
Department of Pediatric Surgery, Centre Hospitalier de Besançon, Hôpital Saint-Jacques, 2, place Saint-Jacques, 25030 Besançon Cedex, France.
Monek
O
O
Massicot
R
R
Martin
L
L
Destuynder
O
O
Lemouel
A
A
Aubert
D
D
D003560:Cysts / Q000150:complications* / Q000601:surgery; D006801:Humans; D007231:Infant, Newborn; D007410:Intestinal Diseases / Q000150:complications* / Q000601:surgery; D007415:Intestinal Obstruction / Q000209:etiology* / Q000601:surgery; D008297:Male; D012007:Rectum / Q000002:abnormalities* / Q000601:surgery