title: Systemic mast cell disease associated with hairy cell leukaemia.
abstract: Systemic mast cell disease (SMCD) can be regarded as a tumorous proliferation of tissue mast cells involving various organs. The frequency with which SMCD is found in patients with haematological disorders suggests that the association is non-random. The association includes primarily, myeloid disorders such as myelodysplastic syndromes and acute or chronic myeloproliferative disorders. Lymphoproliferative disorders may also occur but more rarely, mostly non-Hodgkin's low grade B cell lymphomas. In this report a case is described in which SMCD occurred in a patient with hairy cell leukaemia.
authors.affiliation: Laboratory of Pathology, Centre Hospitalo-Universitaire and Centre de Pathologie de Dijon, France.
authors.forename: T
authors.initials: T
authors.lastname: Petrella
authors.forename: O
authors.initials: O
authors.lastname: Depret
authors.forename: L
authors.initials: L
authors.lastname: Arnould
authors.forename: M
authors.initials: M
authors.lastname: Maynadie
authors.forename: H
authors.initials: H
authors.lastname: Guy
authors.forename: S
authors.initials: S
authors.lastname: Dalac
authors.forename: D
authors.initials: D
authors.lastname: Caillot
authors.forename: O
authors.initials: O
authors.lastname: Casasnovas
authors.forename: J N
authors.initials: JN
authors.lastname: Lombard
mesh_terms: D006801:Humans; D007943:Leukemia, Hairy Cell / Q000150:complications*; D008297:Male; D008415:Mastocytosis / Q000150:complications*; D008875:Middle Aged