Nerve cell lesions caused by 3-hydroxyglutaric acid: a possible mechanism for neurodegeneration in glutaric acidaemia I.
Flott-Rahmel
B
B
Department of Pediatrics, University of Münster, Germany.
Falter
C
C
Schluff
P
P
Fingerhut
R
R
Christensen
E
E
Jakobs
C
C
Musshoff
U
U
Fautek
J D
JD
Deufel
T
T
Ludolph
A
A
Ullrich
K
K
D000255:Adenosine Triphosphate / Q000378:metabolism; D000592:Amino Acid Metabolism, Inborn Errors / Q000378:metabolism*; D000818:Animals; D004594:Electrophysiology; D005977:Glutarates / Q000097:blood* / Q000633:toxicity*; D006624:Hippocampus / Q000166:cytology / Q000187:drug effects; D009410:Nerve Degeneration / Q000503:physiopathology*; D009422:Nervous System Diseases / Q000378:metabolism*; D009474:Neurons / Q000187:drug effects*; D009924:Organ Culture Techniques; D051381:Rats
C108959:3-hydroxyglutaric acid; D005977:Glutarates; C010971:glutaconic acid; D000255:Adenosine Triphosphate; C035736:glutaric acid