title: Intraabdominal desmoplastic small round cell tumour in an 11-year-old boy.
abstract: A case of desmoplastic small round cell tumour (DSRCT) is presented. This aggressive and rare neoplasm predominantly affects males and is almost exclusively intraabdominal in location. It is unique in that neural, mesenchymal and epithelial markers are co-expressed. Despite multi-modal therapy, the prognosis is extremely poor. The present report details the clinical features and typical pathological findings of DSRCT in an 11-year-old boy, who succumbed to the disease 16 months after diagnosis despite multiple chemotherapeutic regimes.
authors.affiliation: Department of Paediatrics, University of Malaya, Kuala Lumpur, Malaysia.
authors.forename: H
authors.initials: H
authors.lastname: Ariffin
authors.forename: W A
authors.initials: WA
authors.lastname: Ariffin
authors.forename: K T
authors.initials: KT
authors.lastname: Wong
authors.forename: T M
authors.initials: TM
authors.lastname: Ramanujam
authors.forename: H P
authors.initials: HP
authors.lastname: Lin
mesh_terms: D000008:Abdominal Neoplasms / Q000175:diagnosis / Q000473:pathology; D002648:Child; D017809:Fatal Outcome; D006801:Humans; D008297:Male