[Mental deficiency preceded by transitory hypertonic cerebral motor disorder].
OBJECTIVE
To analyse clinical and outcome features of patients with mental retardation and transient hypertonia in early life which lead to the diagnosis of hypertonic cerebral palsy.


METHODS
We study six patients that presented with the above features in our neuropediatric out patients clinic. Clinical data related with the hypertonic signs and its evolution were collected. All the patients were assessed to find their present cognitive and development state.


RESULTS
Clinical and radiological signs of a possible prenatal neurological damage were found in all the patients. Structural anomalies were presented in neuroimaging in five cases. Agenesia or hypoplasia of corpus callosum was the most common finding. The pattern of progression of this cases were: 1. Improvement of hypertonia with almost normal tone by the age of two years. 2. Despite of the resolution of motor signs, persistence of different degrees of mental retardation.


CONCLUSIONS
Our reported patients presented a peculiar pattern of progression within the wide variability of the cerebral palsy group.
Artigas
J
J
Unitat de Neuropediatria, Area Pediàtrica Nen Jesús, Consorci Hospitalari del Parc Taulí, Sabadell, Barcelona, España.
Brun
C
C
Lorente
I
I
D061085:Agenesis of Corpus Callosum; D001480:Basal Ganglia Diseases / Q000150:complications; D002547:Cerebral Palsy / Q000150:complications* / Q000175:diagnosis / Q000209:etiology; D002675:Child, Preschool; D006801:Humans; D007223:Infant; D008607:Intellectual Disability / Q000150:complications*; D026741:Physical Therapy Modalities; D011596:Psychomotor Disorders / Q000628:therapy