Postosteotomy healing in Pyle's disease (familial metaphyseal dysplasia). A case report.
Pyle's disease is rare skeletal dysplasia in which a defect in metaphyseal remodeling leads to grossly widened metaphyses of long bones. Genu valgum, one of the few clinical findings in this disease, may warrant surgical intervention. Postoperative healing is documented only in Pyle's original patient. A case is presented in which bilateral osteotomies were performed through the proximal tibia for progressive genu valgum. The osteotomies healed within 12 weeks when treatment was performed with standard techniques. This information will allow osteotomies to be performed with confidence.
Lindberg
E J
EJ
Division of Orthopaedic Surgery, Harbor/UCLA Medical Center, Torrance, USA.
Watts
H G
HG
D000293:Adolescent; D001848:Bone Diseases, Developmental / Q000150:complications / Q000000981:diagnostic imaging / Q000601:surgery*; D006801:Humans; D016916:Joint Deformities, Acquired / Q000000981:diagnostic imaging / Q000209:etiology / Q000601:surgery*; D008297:Male; D010027:Osteotomy; D011859:Radiography; D013977:Tibia / Q000601:surgery*