Bentall operation for a child with Marfan syndrome: a case report.
Children with Marfan syndrome rarely undergo surgery for annuloaortic ectasia and aortic regurgitation in the first decade. A 7-year-old girl presented with congestive heart failure due to severe aortic regurgitation associated with annuloaortic ectasia (6 cm). She also had funnel chest. She underwent a Bentall operation and sternal turn-over with a satisfactory result. Since the aortic valve cusps had rolled edges, the aortic valve was not spared. Histology of the aortic valve cusps showed myxoid degeneration and fragmentation of elastic fibers.
Miura
M
M
Second Department of Surgery, Yamagata University, School of Medicine, Japan.
Shimazaki
Y
Y
Watanabe
T
T
Iijima
Y
Y
Kuraoka
S
S
Inui
K
K
Oshikirl
T
T
Uchida
T
T
Nakasato
M
M
D001011:Aorta / Q000002:abnormalities / Q000601:surgery*; D001021:Aortic Valve / Q000002:abnormalities / Q000601:surgery*; D001022:Aortic Valve Insufficiency / Q000150:complications / Q000175:diagnosis / Q000601:surgery*; D002648:Child; D005260:Female; D006801:Humans; D008382:Marfan Syndrome / Q000150:complications* / Q000175:diagnosis; D014057:Tomography, X-Ray Computed