title: Polyunsaturated fatty acids reverse the lysosomal storage and accumulation of subunit 9 of mitochondrial F1F0-ATP synthase in cultured lymphoblasts from patients with Batten disease.
authors.affiliation: Department of Pathology and Pediatrics, University of Texas Southwestern Medical Center, Dallas, USA.
authors.forename: M J
authors.initials: MJ
authors.lastname: Bennett
authors.forename: R L
authors.initials: RL
authors.lastname: Boriack
authors.forename: R M
authors.initials: RM
authors.lastname: Boustany
mesh_terms: D002460:Cell Line; D004791:Enzyme Inhibitors / Q000494:pharmacology; D005231:Fatty Acids, Unsaturated / Q000494:pharmacology*; D005839:Gentamicins / Q000494:pharmacology; D006801:Humans; D007231:Infant, Newborn; D008214:Lymphocytes / Q000187:drug effects / Q000201:enzymology* / Q000378:metabolism; D008928:Mitochondria / Q000187:drug effects / Q000201:enzymology / Q000378:metabolism*; D009472:Neuronal Ceroid-Lipofuscinoses / Q000201:enzymology*; D006180:Proton-Translocating ATPases / Q000037:antagonists & inhibitors / Q000378:metabolism*
chemical_list: D004791:Enzyme Inhibitors; D005231:Fatty Acids, Unsaturated; D005839:Gentamicins; D006180:Proton-Translocating ATPases