Ivemark syndrome. A case with successful surgical intervention.
A 19-day-old boy with Ivemark syndrome (splenic agenesis associated with complex cardiac malformations and visceral abnormality) underwent palliative surgery including Glenn and hemi-Fontan procedures. Five months later the child is alive and well. We believe that early palliative surgery is worthwhile in Ivemark syndrome with a single ventricle.
Tkebuchava
T
T
Department of Cardiovascular Surgery, University Hospital, Zürich, Switzerland.
von Segesser
L K
LK
Lachat
M
M
Genoni
M
M
Bauersfeld
U
U
Turina
M
M
D000015:Abnormalities, Multiple / Q000175:diagnosis / Q000503:physiopathology / Q000601:surgery*; D006348:Cardiac Surgical Procedures / Q000379:methods*; D005500:Follow-Up Studies; D006330:Heart Defects, Congenital / Q000175:diagnosis / Q000601:surgery*; D006801:Humans; D007231:Infant, Newborn; D008297:Male; D010166:Palliative Care; D013154:Spleen / Q000002:abnormalities*; D013577:Syndrome