title: Familial exudative vitreoretinopathy: surgical intervention and visual acuity outcomes.
abstract: BACKGROUND
  Familial exudative vitreoretinopathy (FEVR) is a hereditary condition that may lead to vitreous hemorrhage and traction retinal detachment necessitating surgical intervention. In this paper we review the results of surgery on seven such patients (eight eyes).
  
  
  METHODS
  Seven patients (eight eyes) were followed up after surgery that had been performed because of vitreous hemorrhage and/or traction retinal detachment due to FEVR, in an effort to evaluate outcomes. Parameters that were noted were the current age, gender, age at the time of first surgery, length of follow-up and postoperative retinal status and visual acuity.
  
  
  RESULTS
  Seven patients (eight eyes) ranging in age from 6 months to 44 years with a mean of 24.7 and a median of 26 years were followed. There were three females and four males. The lowest age at which surgery was first performed was 6 months and the highest was 28 years, with a mean of 14.7 and a median of 17 years. Six of the 8 eyes were reattached following surgery, although some required multiple procedures.
  
  
  CONCLUSIONS
  Vitreoretinal surgery may be of benefit in helping to preserve some degree of vision in eyes of patients with FEVR who develop vitreous hemorrhage and/or retinal detachment.
authors.affiliation: Wills Eye Hospital, Philadelphia, PA 19107, USA.
authors.forename: A
authors.initials: A
authors.lastname: Shubert
authors.forename: W
authors.initials: W
authors.lastname: Tasman
mesh_terms: D000293:Adolescent; D000328:Adult; D002648:Child; D002675:Child, Preschool; D005122:Exudates and Transudates; D005260:Female; D005451:Fluorescein Angiography; D005500:Follow-Up Studies; D005654:Fundus Oculi; D006801:Humans; D007223:Infant; D008297:Male; D012163:Retinal Detachment / Q000209:etiology / Q000601:surgery; D016896:Treatment Outcome; D014792:Visual Acuity / Q000502:physiology*; D018630:Vitreoretinopathy, Proliferative / Q000150:complications / Q000503:physiopathology / Q000601:surgery*; D014823:Vitreous Hemorrhage / Q000209:etiology / Q000601:surgery