Fatal rupture of an acquired aneurysm of the pulmonary artery: rare complication after surgical palliation of tricuspid atresia.
We report the case of a young woman who died from rupture of an aneurysmal dilatation of the left pulmonary artery. She suffered from tricuspid atresia type Ib and underwent a classic Glenn anastomosis at the age of 11 months; at 11 years a direct laterolateral anastomosis was constructed between the ascending aorta and the left pulmonary artery rather than a Fontan procedure for technical reasons. She subsequently developed severe pulmonary hypertension and an aneurysmal dilatation of the left pulmonary artery and was refused any further surgical correction.
Boubaker
A
A
Department of Pathology, University Hospital, Rue du Bugnon 25, CH-1011 Lausanne CHUV, Switzerland.
Payot
M
M
Genton
C Y
CY
D000328:Adult; D017542:Aneurysm, Ruptured / Q000209:etiology*; D017809:Fatal Outcome; D005260:Female; D006801:Humans; D006976:Hypertension, Pulmonary / Q000209:etiology; D010166:Palliative Care; D011651:Pulmonary Artery; D016079:Refusal to Treat; D012422:Rupture, Spontaneous; D013997:Time Factors; D018785:Tricuspid Atresia / Q000601:surgery*