Congenital primitive neuroectodermal tumor of the hand: a case report.
A congenital peripheral primitive neuroectodermal tumor of the hand demonstrating aggressive behavior by rapid growth and ulceration, as well as early diffuse metastasis is presented. Management consisted of below-elbow amputation and chemotherapy. Despite the tumor's initial response, intracranial metastases occurred 7 months later. The patient died shortly thereafter, 15 months after presentation.
Daw
J L
JL
Division of Plastic and Reconstructive Surgery, Northwestern University Medical School, Chicago, IL, USA.
Wiedrich
T A
TA
Bauer
B S
BS
D005260:Female; D006225:Hand; D006801:Humans; D007223:Infant; D018242:Neuroectodermal Tumors, Primitive / Q000151:congenital* / Q000473:pathology / Q000601:surgery