[Scleroderma en coup de sabre with intracranial involvement. A case report].
Scleroderma en coup de sabre is a descriptive term denoting linear scleroderma of the frontoparietal area of the face and scalp. This form of scleroderma is infrequent, mainly in pediatric patients, but not infrequently associates neurologic symptoms, especially epilepsy. We describe a 15-year-old girl with scleroderma en coup de sabre and a long-standing history of epilepsy. Cranial magnetic resonance examination reaffirms the clinical impression that inflammation is not solely confined to the skin in this form of linear scleroderma.
Ortigado Matamala
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A
Servicio de Neurología Infantil, Hospital Infantil La Paz, Madrid.
Martínez Granero
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MA
Pascual Castroviejo
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I
D000293:Adolescent; D004569:Electroencephalography; D004827:Epilepsy / Q000175:diagnosis / Q000209:etiology*; D005260:Female; D006801:Humans; D012594:Scleroderma, Localized / Q000150:complications* / Q000175:diagnosis