title: Cervical spondylotic amyotrophy associated with Hirayama's disease.
abstract: A 47-year-old man with Hirayama's disease who developed cervical spondylotic amyotrophy (CSA) is presented. The patient had noted weakness and atrophy of hand and forearm muscles bilaterally at the age of 16. At the age of 40, he developed proximal muscle atrophy and weakness bilaterally after 20 years of a non-progressive state. Myelography and computed tomography (CT)-myelography revealed that ventral cord compression at multiple levels of C4-7 vertebral bodies was increased when the neck was extended. The clinical diagnosis was CSA associated with Hirayama's disease. To our knowledge, this is the first such case to be reported.
authors.affiliation: Department of Neurology, Takamatsu Red Cross Hospital, Kagawa.
authors.forename: S
authors.initials: S
authors.lastname: Hashiguchi
authors.forename: N
authors.initials: N
authors.lastname: Ogasawara
authors.forename: A
authors.initials: A
authors.lastname: Watanabe
authors.forename: Y
authors.initials: Y
authors.lastname: Kawachi
authors.forename: N
authors.initials: N
authors.lastname: Miki
mesh_terms: D002574:Cervical Vertebrae / Q000000981:diagnostic imaging / Q000473:pathology*; D005542:Forearm / Q000473:pathology; D006225:Hand / Q000473:pathology; D006801:Humans; D008297:Male; D008875:Middle Aged; D009134:Muscular Atrophy, Spinal / Q000150:complications* / Q000000981:diagnostic imaging; D009192:Myelography; D013117:Spinal Cord Compression / Q000150:complications / Q000000981:diagnostic imaging / Q000473:pathology; D013128:Spinal Osteophytosis / Q000150:complications*; D014057:Tomography, X-Ray Computed