Isolated myoclonic alien hand as the sole presentation of pathologically established Creutzfeldt-Jakob disease: a report of two patients.
Creutzfeldt-Jakob disease may have many atypical presentations before the development of classic progressive dementia and startle myoclonus. In two patients with pathologically established disease association with a progressive alien hand syndrome was the sole initial manifestation of the disease.
MacGowan
D J
DJ
Department of Neurology, New York Hospital, Cornell Medical Center, USA.
Delanty
N
N
Petito
F
F
Edgar
M
M
Mastrianni
J
J
DeArmond
S J
SJ
D000368:Aged; D007562:Creutzfeldt-Jakob Syndrome / Q000503:physiopathology*; D017809:Fatal Outcome; D005260:Female; D006225:Hand / Q000503:physiopathology*; D006801:Humans; D009207:Myoclonus / Q000503:physiopathology*; D010468:Perceptual Disorders