title: Epithelioid sarcomas. Three cases.
abstract: The authors present two cases of epithelioid sarcoma of the hand and one of the foot with clinical interest. This recently described tumor (Enzinger, 1970), is relatively rare. It occurs in the hand, forearm, pretibial region and foot and affects principally young adults. It should be emphasized, and this is borne out in the literature, that this tumor may appear perfectly benign and often has a course of long duration. The difficult of clinical and especially of histologic diagnosis as well as the difficulty of determining the boundaries of extension of the tumor makes it necessary to carry out radical surgery (amputation or rarely block excision). Every author agrees that local excision is to be condemned, there being an 85% recurrence rate. Spread of the tumor is by way of the fascial planes and tendon sheaths. Lymphatic and pulmonary metastases occur particularly when there is vascular invasion.
authors.affiliation: Service d'Orthopédie Traumatologie A, Centre Hospitalier Régional et Universitaire, Caen.
authors.forename: J L
authors.initials: JL
authors.lastname: Condamine
authors.forename: B
authors.initials: B
authors.lastname: Louis
authors.forename: D
authors.initials: D
authors.lastname: Richter
authors.forename: J L
authors.initials: JL
authors.lastname: Roffe
authors.forename: J H
authors.initials: JH
authors.lastname: Aubriot
mesh_terms: D000328:Adult; D000671:Amputation, Surgical; D005205:Fascia / Q000473:pathology; D005260:Female; D005500:Follow-Up Studies; D005534:Foot Diseases / Q000473:pathology* / Q000601:surgery; D006225:Hand / Q000473:pathology* / Q000528:radiation effects / Q000601:surgery; D006801:Humans; D008175:Lung Neoplasms / Q000556:secondary; D008207:Lymphatic Metastasis / Q000473:pathology; D008297:Male; D009361:Neoplasm Invasiveness; D009364:Neoplasm Recurrence, Local / Q000473:pathology; D012509:Sarcoma / Q000473:pathology* / Q000532:radiotherapy / Q000556:secondary / Q000601:surgery; D012883:Skin Ulcer / Q000473:pathology; D012983:Soft Tissue Neoplasms / Q000473:pathology* / Q000532:radiotherapy / Q000601:surgery; D013710:Tendons / Q000473:pathology; D016896:Treatment Outcome