Idiopathic hypertrophic pachymeningitis: spectrum of the disease.
Hypertrophic pachymeningitis is extremely rare. It is a fibrosing inflammatory process which involves the dura mater, including the tentorium. Numerous pathological entities produce thickening of the pachymeninges, so that idiopathic hypertrophic pachymeningitis is a diagnosis of exclusion. We describe four patients with idiopathic hypertrophic pachymeningitis who had varied clinical presentation. Imaging studies revealed diffuse thickening of the pachymeninges; in one patient there was extensive dural sinus thrombosis. Since no identifiable cause was found, the cases were labelled as idiopathic.
Goyal
M
M
Department of Neuroradiology, All India Institute of Medical Sciences, New Delhi, India.
Malik
A
A
Mishra
N K
NK
Gaikwad
S B
SB
D000328:Adult; D001921:Brain / Q000473:pathology; D003392:Cranial Sinuses / Q000473:pathology; D003937:Diagnosis, Differential; D004388:Dura Mater / Q000473:pathology; D005260:Female; D006801:Humans; D006984:Hypertrophy; D008279:Magnetic Resonance Imaging; D008297:Male; D008581:Meningitis / Q000175:diagnosis* / Q000473:pathology; D008875:Middle Aged; D009460:Neurologic Examination; D012851:Sinus Thrombosis, Intracranial / Q000175:diagnosis / Q000473:pathology; D014057:Tomography, X-Ray Computed