title: Isolated myoclonic alien hand as the sole presentation of pathologically established Creutzfeldt-Jakob disease: a report of two patients.
abstract: Creutzfeldt-Jakob disease may have many atypical presentations before the development of classic progressive dementia and startle myoclonus. In two patients with pathologically established disease association with a progressive alien hand syndrome was the sole initial manifestation of the disease.
authors.affiliation: Department of Neurology, New York Hospital, Cornell Medical Center, USA.
authors.forename: D J
authors.initials: DJ
authors.lastname: MacGowan
authors.forename: N
authors.initials: N
authors.lastname: Delanty
authors.forename: F
authors.initials: F
authors.lastname: Petito
authors.forename: M
authors.initials: M
authors.lastname: Edgar
authors.forename: J
authors.initials: J
authors.lastname: Mastrianni
authors.forename: S J
authors.initials: SJ
authors.lastname: DeArmond
mesh_terms: D000368:Aged; D007562:Creutzfeldt-Jakob Syndrome / Q000503:physiopathology*; D017809:Fatal Outcome; D005260:Female; D006225:Hand / Q000503:physiopathology*; D006801:Humans; D009207:Myoclonus / Q000503:physiopathology*; D010468:Perceptual Disorders